Severe combined immunodeficiency due to LCK deficiency
Severe combined immunodeficiency with low T- and B-cell numbers (disorder)
Severe combined immunodeficiency due to complete RAG1 and/or RAG2 deficiency
Combined immunodeficiency associated with maturation pathway defect
SCID (severe combined immunodeficiency) due to absent T cell receptor
Severe combined immunodeficiency due to absent interleukin-2 production
Combined immunodeficiency due to partial RAG1 deficiency
Autosomal dominant T-B- SCID (severe combined immunodeficiency) due to activated RAC2 defect
Autosomal dominant T-cell negative, B-cell negative severe combined immunodeficiency due to activated Rac family small GTPase 2 defect
Severe combined immunodeficiency due to CTPS1 deficiency
Omenn syndrome
Severe combined immunodeficiency due to absent interleukin-2 receptor
Severe combined immunodeficiency due to complete RAG1 (recombination activating gene 1) and/or RAG2 (recombination activating gene 2) deficiency
SCID (severe combined immunodeficiency) due to absent IL-2 (interleukin-2) production
Autosomal dominant T-cell negative, B-cell negative severe combined immunodeficiency due to activated RAC2 defect
SCID due to absent IL-2 receptor
Severe combined immunodeficiency due to absent peripheral T cell maturation
Severe combined immunodeficiency with low T- and B-cell numbers
Severe combined immunodeficiency due to absent T cell receptor
Severe combined immunodeficiency due to cytidine 5-prime triphosphate synthetase 1 deficiency
Disorder of eosinophil
Combined immunodeficiency due to partial recombination-activating gene 1 deficiency
SCID (severe combined immunodeficiency) due to absent peripheral T cell maturation
Severe combined immunodeficiency with hypereosinophilia
Severe combined immunodeficiency due to LCK (lymphocyte-specific protein-tyrosine kinase) deficiency
Severe combined immunodeficiency (SCID) due to absent IL-2 receptor
Hereditary eosinophilia
Severe combined immunodeficiency due to lymphocyte-specific protein-tyrosine kinase deficiency
Combined immunodeficiency with expansion of gamma delta T cell
Severe combined immunodeficiency due to complete recombination-activating gene 1 and/or recombination-activating gene 2 deficiency
SCID (severe combined immunodeficiency) due to complete RAG1/2 deficiency

Frequently Asked Questions

What is the ICD-10 code for severe combined immunodeficiency w low t- and b-cell numbers?

The ICD-10-CM code for severe combined immunodeficiency w low t- and b-cell numbers is D81.1. The full clinical description is "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers". D81.1 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D81.1 mean?

ICD-10-CM code D81.1 represents “Severe combined immunodeficiency [SCID] with low T- and B-cell numbers”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D81.1 a billable code?

Yes, D81.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D81.1 in?

D81.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D81.1?

D81.1 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.

What SNOMED CT codes does D81.1 map to?

D81.1 maps to 13 SNOMED CT concepts: 1351235001, 3439009, 725290000, 417967008, 191358004, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D81.1?

D81.1 is linked to 1 UMLS Concept Unique Identifier: C0451693. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D81.1 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like severe combined immunodeficiency w low t- and b-cell numbers affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D81.1?

D81.1 maps to the ICD-11 code: 4A01.10 (Severe combined immunodeficiencies).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.