D81.0
BillableSevere combined immunodeficiency with reticular dysgenesis
Severe combined immunodeficiency [SCID] with reticular dysgenesis
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(9)
D81.1Severe combined immunodeficiency w low T- and B-cell numbers
D81.2Severe combined immunodef w low or normal B-cell numbers
D81.3Adenosine deaminase [ADA] deficiency
D81.4Nezelof's syndrome
D81.5Purine nucleoside phosphorylase [PNP] deficiency
D81.6Major histocompatibility complex class I deficiency
D81.7Major histocompatibility complex class II deficiency
D81.8Other combined immunodeficiencies
D81.9Combined immunodeficiency, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(11)
SNOMED CT
- Combined immunodeficiency associated with maturation pathway defect3439009
- SCID (severe combined immunodeficiency) due to absent peripheral T cell maturation3439009
- Severe combined immunodeficiency due to absent peripheral T cell maturation3439009
- Severe combined immunodeficiency with reticular dysgenesis190996002
UMLS
Clinical Terms
- Severe combined immunodeficiency due to absent peripheral T cell maturation
- Severe combined immunodeficiency with reticular dysgenesis (disorder)
- SCID (severe combined immunodeficiency) due to absent peripheral T cell maturation
- Combined immunodeficiency associated with maturation pathway defect
Frequently Asked Questions
What is the ICD-10 code for severe combined immunodeficiency with reticular dysgenesis?
The ICD-10-CM code for severe combined immunodeficiency with reticular dysgenesis is D81.0. The full clinical description is "Severe combined immunodeficiency [SCID] with reticular dysgenesis". D81.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D81.0 mean?
ICD-10-CM code D81.0 represents “Severe combined immunodeficiency [SCID] with reticular dysgenesis”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D81.0 a billable code?
Yes, D81.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.0 in?
D81.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.0?
D81.0 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D81.0 map to?
D81.0 maps to 2 SNOMED CT concepts: 3439009, 190996002. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.0?
D81.0 is linked to 1 UMLS Concept Unique Identifier: C0494256. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D81.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like severe combined immunodeficiency with reticular dysgenesis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D81.0?
D81.0 maps to the ICD-11 code: 4A01.10 (Severe combined immunodeficiencies).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.