AutoICD API

E76

Non-billable

Disorders of glycosaminoglycan metabolism

Disorders of glycosaminoglycan metabolism

This is a header/category code. For billing purposes, use a more specific child code from the list below.

Status

Non-billable / Header

Block

E70-E88

Child Codes

6

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes 2

Conditions not included here, but the patient may have both

  • Ehlers-Danlos syndromes (Q79.6-)

Child Codes (6)

E76.0

Mucopolysaccharidosis, type I

E76.1

Mucopolysaccharidosis, type II

BillableE76.2

Other mucopolysaccharidoses

E76.3

Mucopolysaccharidosis, unspecified

BillableE76.8

Other disorders of glucosaminoglycan metabolism

BillableE76.9

Glucosaminoglycan metabolism disorder, unspecified

Billable

Also Known As / Clinical Terms

UMLS

Frequently Asked Questions

What is ICD-10 code E76?

ICD-10-CM code E76 represents "Disorders of glycosaminoglycan metabolism". It is a non-billable header code — use a more specific child code for billing purposes.

Is E76 a billable code?

No, E76 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 6 child codes under E76.

What chapter is E76 in?

E76 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E76?

E76 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What are the subcategories under E76?

E76 has 6 child codes, including: E76.0 (Mucopolysaccharidosis, type I), E76.1 (Mucopolysaccharidosis, type II), E76.2 (Other mucopolysaccharidoses), E76.3 (Mucopolysaccharidosis, unspecified), and 2 more.

What are the UMLS CUIs for E76?

E76 is linked to 1 UMLS Concept Unique Identifier: C0342837. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.