E76
Non-billableDisorders of glycosaminoglycan metabolism
Disorders of glycosaminoglycan metabolism
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Child Codes (6)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(4)
Frequently Asked Questions
What is the ICD-10 code for disorders of glycosaminoglycan metabolism?
The ICD-10-CM code for disorders of glycosaminoglycan metabolism is E76. The full clinical description is "Disorders of glycosaminoglycan metabolism". E76 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code E76 mean?
ICD-10-CM code E76 represents “Disorders of glycosaminoglycan metabolism”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is E76 a billable code?
No, E76 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 6 child codes under E76.
What chapter is E76 in?
E76 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76?
E76 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What are the subcategories under E76?
E76 has 6 child codes, including: E76.0 (Mucopolysaccharidosis, type I), E76.1 (Mucopolysaccharidosis, type II), E76.2 (Other mucopolysaccharidoses), E76.3 (Mucopolysaccharidosis, unspecified), and 2 more.
What are the UMLS CUIs for E76?
E76 is linked to 1 UMLS Concept Unique Identifier: C0342837. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E76 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like disorders of glycosaminoglycan metabolism affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E76?
E76 maps to the ICD-11 code: 5C56.3Z (Mucopolysaccharidosis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.