5C56.3Z
Mucopolysaccharidosis, unspecified
Mucopolysaccharidosis, unspecified
ICD-10 Equivalents(5)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(14)
SNOMED CT ↗
- MPS - Mucopolysaccharidosis11380006
- Alpha-L-iduronidase deficiency75610003
- Restrictive cardiomyopathy due to mucopolysaccharidosis84725008
- Dilated cardiomyopathy due to mucopolysaccharidosis86995005
- Dilated cardiomyopathy due to metabolic disorder111285003
- Cerebral degeneration in mucopolysaccharidosis192796004
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Secondary restrictive cardiomyopathy415509000
- Cardiomyopathy due to storage disease860839005
- Dilated cardiomyopathy due to lysosomal storage disease880038008
Frequently Asked Questions
What is the ICD-11 code for mucopolysaccharidosis, unspecified?
The ICD-11 code for mucopolysaccharidosis, unspecified is 5C56.3Z. The full clinical description is "Mucopolysaccharidosis, unspecified".
What does ICD-11 code 5C56.3Z mean?
ICD-11 code 5C56.3Z represents “Mucopolysaccharidosis, unspecified”. It is classified under Chapter 5: Endocrine, Nutritional or Metabolic Diseases.
What chapter is 5C56.3Z in?
5C56.3Z is in Chapter 5: Endocrine, Nutritional or Metabolic Diseases (codes 5A00-5D46).
What is the ICD-10 equivalent of ICD-11 code 5C56.3Z?
5C56.3Z maps to 5 ICD-10 codes: E76 (Disorders of glycosaminoglycan metabolism), E76.2 (Other mucopolysaccharidoses), E76.3 (Mucopolysaccharidosis, unspecified), and 2 more. ICD-10 and ICD-11 do not always have one-to-one mappings — check the mapping type (equivalent, approximate, narrower, or broader) for each result.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What SNOMED CT codes does 5C56.3Z map to?
5C56.3Z maps to 10 SNOMED CT concepts: 75610003, 195027000, 860839005, 192796004, 880038008, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What UMLS concepts map to ICD-11 code 5C56.3Z?
5C56.3Z is linked to 4 UMLS Concept Unique Identifiers: C0342837, C0348491, C0348492, C0348503. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.