E76.3
BillableMucopolysaccharidosis, unspecified
Mucopolysaccharidosis, unspecified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- MPS - Mucopolysaccharidosis11380006
- Mucopolysaccharidosis11380006
- Alpha-L-iduronidase deficiency75610003
- L-iduronidase deficiency75610003
- MPS I75610003
- MPSI - Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis, MPS-I75610003
- Restrictive cardiomyopathy due to mucopolysaccharidosis84725008
- Dilated cardiomyopathy due to mucopolysaccharidosis86995005
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Cerebral degeneration in mucopolysaccharidosis192796004
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Secondary restrictive cardiomyopathy415509000
- Cardiomyopathy due to storage disease860839005
- Dilated cardiomyopathy due to lysosomal storage disease880038008
Frequently Asked Questions
What is ICD-10 code E76.3?
ICD-10-CM code E76.3 represents "Mucopolysaccharidosis, unspecified". It is a billable/specific code that can be used on a claim.
Is E76.3 a billable code?
Yes, E76.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.3 in?
E76.3 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.3?
E76.3 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.3 map to?
E76.3 maps to 10 SNOMED CT concepts: 75610003, 195027000, 860839005, 192796004, 880038008, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.3?
E76.3 is linked to 1 UMLS Concept Unique Identifier: C0026703. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.