E25.0
BillableCongenital adrenogenital disorders assoc w enzyme deficiency
Congenital adrenogenital disorders associated with enzyme deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
Includes
Conditions included under this code
- adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
- Female adrenal pseudohermaphroditism
- Female heterosexual precocious pseudopuberty
- Male isosexual precocious pseudopuberty
- Male macrogenitosomia praecox
- Male sexual precocity with adrenal hyperplasia
- Male virilization (female)
Also Known As / Clinical Terms
SNOMED CT
- Female pseudohermaphroditism8800006
- Ferms8800006
- Gynandrism8800006
- Severe steroid 21-hydroxylase deficiency15991002
- Virilising syndrome of adrenal origin17318002
- Virilizing syndrome of adrenal origin17318002
- 20,22-Desmolase deficiency44231009
- Cholesterol desmolase deficiency44231009
- Cholesterol monooxygenase (side-chain cleaving) deficiency44231009
- Congenital lipoid hyperplasia of adrenal cortex with male pseudohermaphroditism44231009
- Defective synthesis of cholesterol desmolase44231009
- Mild steroid 21-hydroxylase deficiency45235005
- 18-Hydroxycorticosterone dehydrogenase deficiency47757001
- 18-Hydroxylase deficiency47757001
- Aldosterone deficiency due to 18-hydroxylase defect47757001
- Aldosterone deficiency due to 18-hydroxysteroid dehydrogenase deficiency47757001
- CAH - 18-hydroxylase deficiency47757001
- CMO I deficiency47757001
- CMO II deficiency47757001
- Corticosterone 18-monooxygenase deficiency47757001
- Corticosterone methyl oxidase type I deficiency47757001
- Corticosterone methyl oxidase type II deficiency47757001
- 17 alpha-Hydroxyprogesterone aldolase deficiency49013001
- Defective synthesis of 17-20 desmolase49013001
- Male pseudohermaphroditism due to testicular 17,20-desmolase deficiency49013001
- Steroid 17,20-lyase deficiency49013001
- Adrenogenital disorder due to 21-hydroxylase deficiency52604008
- Congenital adrenal hyperplasia, type 152604008
- Simple virilising adrenal hyperplasia52604008
- Simple virilizing adrenal hyperplasia52604008
- Simple-virilising congenital adrenal hyperplasia52604008
- Simple-virilizing congenital adrenal hyperplasia52604008
- Steroid 21-hydroxylase deficiency, simple virilising type52604008
- Steroid 21-hydroxylase deficiency, simple virilizing type52604008
- Steroid 21-monooxygenase deficiency, simple virilising type52604008
- Steroid 21-monooxygenase deficiency, simple virilizing type52604008
- 3 beta-HSD deficiency54470008
- 3 beta-Hydroxysteroid dehydrogenase deficiency54470008
- CAH - 3 beta-dehydrogenase deficiency54470008
- Congenital adrenal hyperplasia, type 454470008
- Moderate steroid 21-hydroxylase deficiency60045007
- Aldosterone deficiency60086000
- Hypoaldosteronism60086000
- 21-hydroxylase deficiency, salt wasting type71578002
- Congenital adrenal hyperplasia, type 271578002
- Steroid 21-monooxygenase deficiency, salt wasting type71578002
- CAH - Congenital adrenal hypoplasia93235007
- Congenital adrenal hypoplasia93235007
- Congenital hypoplasia of adrenal gland93235007
- Congenital small adrenal gland93235007
- Fetal virilism95622006
- Foetal virilism95622006
- Male pseudohermaphroditism111332007
- Merms111332007
- Disorder of cholesterol metabolism123963007
- Deficiency of 3alpha-hydroxysteroid dehydrogenase124135001
- Deficiency of 17beta-hydroxysteroid dehydrogenase124136000
- Deficiency of 3beta-hydroxysteroid dehydrogenase124136000
- 11-beta-hydroxylase deficiency124214007
- Adrenogenital disorder due to 11-beta-hydroxylase deficiency124214007
- CAH - 11 beta-hydroxylase deficiency124214007
- Congenital adrenal hyperplasia, type 3124214007
- Deficiency of steroid 11-beta-hydroxylase124214007
- Deficiency of steroid 11-beta-monooxygenase124214007
- Hypertensive congenital adrenal hyperplasia124214007
- Steroid 11-beta-monooxygenase deficiency124214007
- 21-hydroxylase deficiency124221007
- CAH - 21-hydroxylase deficiency124221007
- Deficiency of steroid 21-hydroxylase124221007
- Deficiency of steroid 21-monooxygenase124221007
- BASD - Bile acid synthetic defect235915002
- Bile acid synthesis disorder235915002
- Bile acid synthetic defect235915002
- Disorder of bile acid synthesis235915002
- Inborn error of bile acid synthesis235915002
- Synthetic defect of bile acids235915002
- Virilisation - adrenogenital237749004
- Virilisation-adrenogenital syndrome237749004
- Virilization - adrenogenital237749004
- Virilization-adrenogenital syndrome237749004
- Pseudohermaphrodite, female with adrenocortical disorder237750004
- CAH - Congenital adrenal hyperplasia237751000
- Congenital adrenal cortical hyperplasia237751000
- Congenital adrenal hyperplasia237751000
- Congenital adrenogenital syndrome237751000
- Salt-losing congenital adrenal hyperplasia237753002
- Late onset congenital adrenal hyperplasia237754008
- CAH - desmolase deficiency237755009
- Congenital adrenal hyperplasia (CAH)- desmolase deficiency237755009
- Congenital adrenal hyperplasia - desmolase deficiency237755009
- Congenital adrenal hypoplasia, X-linked237764004
- Disorder of cholesterol catabolism238032002
- 3-Beta-hydroxy-delta-5-C27-steroid dehydrogenase deficiency238033007
- Congenital bile acid synthesis defect type 1238033007
- Adrenal virilism271077003
- Apert-Gallais syndrome271077003
- Wilkins disease271077003
- Fetal endocrine disorder363128000
- Foetal endocrine disorder363128000
- Hyperandrogenism due to non-classic 21-hydroxylase deficiency698854006
- Hyperandrogenism due to non-classic type of 21-hydroxylase deficiency698854006
- Congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency715733000
- Congenital lipoid adrenal hyperplasia due to STAR deficiency717260007
- Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency717260007
- Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency717261006
- Congenital lipoid adrenal hyperplasia due to STAR deficiency classic form840473004
- Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency classic form840473004
- Congenital lipoid adrenal hyperplasia due to STAR deficiency non-classic form840474005
- Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency non classic form840474005
- Congenital adrenal hyperplasia due to 21-hydroxylase deficiency non-classic form840509001
- Hypertension due to congenital adrenal hyperplasia1204139007
- Female adrenal pseudohermaphroditism1217071000
- Female pseudohermaphroditism due to congenital adrenal hyperplasia1217071000
- Adrenal pseudohermaphroditism1217074008
- Pseudohermaphroditism due to congenital adrenal hyperplasia1217074008
- Male adrenal pseudohermaphroditism1217078006
- Male pseudohermaphroditism due to congenital adrenal hyperplasia1217078006
- 46,XY disorder of sex development due to isolated 17,20-lyase deficiency1231281009
- Salt-losing congenital adrenal hyperplasia with virilism250591000119109
UMLS
- 21-Hydroxylase DeficiencyC0852654
- 21-Hydroxylase deficiencyC0852654
- 21-hydroxylase deficiencyC0852654
- CAH1C0852654
- ADRENAL HYPERPLASIA CONGENC0001627
- Adrenal HyperplasiaC0001627
- Adrenal Hyperplasia, CongenitalC0001627
- Adrenal Hyperplasias, CongenitalC0001627
- Adrenogenital SyndromeC0001627
- CAH - Congenital adrenal hyperplasiaC0001627
- CONGEN ADRENAL HYPERPLASIAC0001627
- Congenital Adrenal Gland HyperplasiaC0001627
- Congenital Adrenal HyperplasiaC0001627
- Congenital Adrenal HyperplasiasC0001627
- Congenital adrenal hyperplasiaC0001627
- Congenital adrenal hyperplasia (disorder)C0001627
- Congenital adrenogenital syndromeC0001627
- HYPERPLASIA CONGEN ADRENALC0001627
- Hyperplasia, Congenital AdrenalC0001627
- Hyperplasias, Congenital AdrenalC0001627
- adrenal congenital hyperplasiaC0001627
- congenital adrenal hyperplasiaC0001627
- hyperplasia adrenal congenitalC0001627
- hyperplasia congenital adrenalC0001627
- Congenital adrenogenital disorders assoc w enzyme deficiencyC0494311
- Congenital adrenogenital disorders associated with enzyme deficiencyC0494311
- Salt-losing congenital adrenal hyperplasiaC0342464
- Salt-losing congenital adrenal hyperplasia (disorder)C0342464
Frequently Asked Questions
What is ICD-10 code E25.0?
ICD-10-CM code E25.0 represents "Congenital adrenogenital disorders associated with enzyme deficiency". It is a billable/specific code that can be used on a claim.
Is E25.0 a billable code?
Yes, E25.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E25.0 in?
E25.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E25.0?
E25.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); galactorrhea (N64.3); gynecomastia (N62); and 2 more.
What SNOMED CT codes does E25.0 map to?
E25.0 maps to 45 SNOMED CT concepts: 124214007, 49013001, 47757001, 44231009, 124221007, and 40 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E25.0?
E25.0 is linked to 4 UMLS Concept Unique Identifiers: C0852654, C0001627, C0494311, C0342464. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.