E00
Non-billableCongenital iodine-deficiency syndrome
Congenital iodine-deficiency syndrome
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Use Additional Code
Additional codes that should follow this code
Child Codes (4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(10)
UMLS
- Congenital Iodine Deficiency HypothyroidismC3165526
- Congenital Iodine Deficiency SyndromeC3165526
- Congenital iodine deficiency syndromeC3165526
- Congenital iodine deficiency syndrome (disorder)C3165526
- Congenital iodine-deficiency hypothyroidism NOSC3165526
- Congenital iodine-deficiency syndromeC3165526
- Congenital iodine-deficiency syndrome, unspecifiedC3165526
- Endemic cretinism NOSC3165526
- Fetal iodine deficiency syndromeC3165526
- Foetal iodine deficiency syndromeC3165526
Frequently Asked Questions
What is the ICD-10 code for congenital iodine-deficiency syndrome?
The ICD-10-CM code for congenital iodine-deficiency syndrome is E00. The full clinical description is "Congenital iodine-deficiency syndrome". E00 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code E00 mean?
ICD-10-CM code E00 represents “Congenital iodine-deficiency syndrome”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is E00 a billable code?
No, E00 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 4 child codes under E00.
What chapter is E00 in?
E00 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E00?
E00 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); subclinical iodine-deficiency hypothyroidism (E02).
What are the subcategories under E00?
E00 has 4 child codes, including: E00.0 (Congenital iodine-deficiency syndrome, neurological type), E00.1 (Congenital iodine-deficiency syndrome, myxedematous type), E00.2 (Congenital iodine-deficiency syndrome, mixed type), E00.9 (Congenital iodine-deficiency syndrome, unspecified).
Are additional codes required with E00?
Yes, when using E00, also report: code (F70-F79) to identify associated intellectual disabilities..
What are the UMLS CUIs for E00?
E00 is linked to 1 UMLS Concept Unique Identifier: C3165526. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E00 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital iodine-deficiency syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E00?
E00 maps to the ICD-11 code: 5A00.04 (Congenital hypothyroidism due to iodine deficiency).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.