E76.0
Non-billableMucopolysaccharidosis, type I
Mucopolysaccharidosis, type I
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Child Codes (3)
Also Known As / Clinical Terms
UMLS
- Alpha-L-iduronidase deficiencyC0023786
- IDUA deficiencyC0023786
- L-iduronidase deficiencyC0023786
- LipochondrodystrophiesC0023786
- LipochondrodystrophyC0023786
- MPS 1C0023786
- MPS IC0023786
- MPSI - Mucopolysaccharidosis type IC0023786
- Mucopolysaccharidosis 1C0023786
- Mucopolysaccharidosis IC0023786
- Mucopolysaccharidosis Type IC0023786
- Mucopolysaccharidosis type IC0023786
- Mucopolysaccharidosis type I (disorder)C0023786
- Mucopolysaccharidosis, MPS-IC0023786
- Mucopolysaccharidosis, type IC0023786
- i mucopolysaccharidosisC0023786
- iduronidase deficiency diseaseC0023786
- mps iC0023786
- mucopolysaccharidosis iC0023786
- mucopolysaccharidosis type IC0023786
- mucopolysaccharidosis type iC0023786
Frequently Asked Questions
What is ICD-10 code E76.0?
ICD-10-CM code E76.0 represents "Mucopolysaccharidosis, type I". It is a non-billable header code — use a more specific child code for billing purposes.
Is E76.0 a billable code?
No, E76.0 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under E76.0.
What chapter is E76.0 in?
E76.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.0?
E76.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What are the subcategories under E76.0?
E76.0 has 3 child codes, including: E76.01 (Hurler's syndrome), E76.02 (Hurler-Scheie syndrome), E76.03 (Scheie's syndrome).
What are the UMLS CUIs for E76.0?
E76.0 is linked to 1 UMLS Concept Unique Identifier: C0023786. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.