E76.01
BillableHurler's syndrome
Hurler's syndrome
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Dysostosis multiplex syndrome65327002
- Gargoylism65327002
- Hurler disease MPS type 1H65327002
- Hurler's syndrome65327002
- Hurler-Pfaundler syndrome65327002
- L-iduronidase deficiency, Hurler type65327002
- Lipochondrodystrophy65327002
- MPS 1-H - Mucopolysaccharidosis type I-H65327002
- Mucopolysaccharidosis type I severe form65327002
- Mucopolysaccharidosis type I-H65327002
- Mucopolysaccharidosis, MPS-I-H65327002
- Alpha-L-iduronidase deficiency75610003
- L-iduronidase deficiency75610003
- MPS I75610003
- MPSI - Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis, MPS-I75610003
- Hurloid facies80174007
- Dysostosis multiplex254069004
- Dysostosis multiplex group279081001
UMLS
- Disease, Hurler'sC0086795
- Dysostosis multiplex syndromeC0086795
- GargoylismC0086795
- Gargoylism, Hurler SyndromeC0086795
- GargoylismsC0086795
- HURLER DISC0086795
- HURLER SYNDROMEC0086795
- HURLERS DISC0086795
- Hurler DiseaseC0086795
- Hurler SyndromeC0086795
- Hurler Syndrome GargoylismC0086795
- Hurler disease MPS type 1HC0086795
- Hurler syndromeC0086795
- Hurler's DiseaseC0086795
- Hurler's SyndromeC0086795
- Hurler's diseaseC0086795
- Hurler's syndromeC0086795
- Hurler-Pfaundler syndromeC0086795
- L-iduronidase deficiency, Hurler typeC0086795
- LipochondrodystrophyC0086795
- MPS 1-H - Mucopolysaccharidosis type I-HC0086795
- MPS I HC0086795
- MPS1-HC0086795
- MUCOPOLYSACCHARIDOSIS TYPE IHC0086795
- Mucopolysaccharidosis Type IHC0086795
- Mucopolysaccharidosis Type IhC0086795
- Mucopolysaccharidosis Type IhsC0086795
- Mucopolysaccharidosis type I severe formC0086795
- Mucopolysaccharidosis type I-HC0086795
- Mucopolysaccharidosis type I-H (disorder)C0086795
- Mucopolysaccharidosis, MPS-I-HC0086795
- Pfaundler-Hurler SyndromeC0086795
- Syndrome, Hurler'sC0086795
- Type Ih, MucopolysaccharidosisC0086795
- Type Ihs, MucopolysaccharidosisC0086795
- gargoylismC0086795
- hurlerC0086795
- hurler diseaseC0086795
- hurler syndromeC0086795
- hurler's diseaseC0086795
- hurler's syndromeC0086795
- hurlersC0086795
- hurlers diseaseC0086795
- hurlers syndromeC0086795
- lipochondrodystrophyC0086795
- thompson syndromeC0086795
Frequently Asked Questions
What is the ICD-10 code for hurler's syndrome?
The ICD-10-CM code for hurler's syndrome is E76.01. The full clinical description is "Hurler's syndrome". E76.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.01 mean?
ICD-10-CM code E76.01 represents "Hurler's syndrome". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.01 a billable code?
Yes, E76.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.01 in?
E76.01 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.01?
E76.01 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.01 map to?
E76.01 maps to 5 SNOMED CT concepts: 75610003, 254069004, 279081001, 65327002, 80174007. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.01?
E76.01 is linked to 1 UMLS Concept Unique Identifier: C0086795. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.