E76.1
BillableMucopolysaccharidosis, type II
Mucopolysaccharidosis, type II
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Hunter's syndrome
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Hunter syndrome, mild form5667009
- Hunter's syndrome, mild form5667009
- Mucopolysaccharidosis type II mild form5667009
- Deficiency of iduronate-2-sulfatase70737009
- Deficiency of iduronate-2-sulphatase70737009
- Hunter disease70737009
- Hunter syndrome70737009
- Hunter's syndrome70737009
- Iduronate 2-sulfatase deficiency70737009
- Iduronate 2-sulphatase deficiency70737009
- Iduronate sulfatase deficiency70737009
- Iduronate sulphatase deficiency70737009
- MPS 2 - Mucopolysaccharidosis 270737009
- MPSII - Mucopolysaccharidosis type II70737009
- Mucopolysaccharidosis type II70737009
- Mucopolysaccharidosis, MPS-II70737009
- Sulfo-iduronate sulfatase deficiency70737009
- Sulfoiduronidate sulfatase deficiency70737009
- Sulpho-iduronate sulphatase deficiency70737009
- Sulphoiduronidate sulphatase deficiency70737009
- Hunter syndrome, severe form73146005
- Hunter's syndrome, severe form73146005
- Mucopolysaccharidosis type II severe form73146005
- Cerebral degeneration in Hunter disease192795000
- Cerebral degeneration in Hunter's disease192795000
- Cerebral degeneration in mucopolysaccharidosis192796004
UMLS
- Deficiency of iduronate-2-sulfataseC0026705
- Deficiency of iduronate-2-sulphataseC0026705
- Gargoylism, Hunter SyndromeC0026705
- HUNTER SYNDROMEC0026705
- Hunter SyndromeC0026705
- Hunter Syndrome GargoylismC0026705
- Hunter diseaseC0026705
- Hunter syndromeC0026705
- Hunter's SyndromeC0026705
- Hunter's syndromeC0026705
- Hunters SyndromeC0026705
- IDS DEFICIENCYC0026705
- IDURONATE 2-SULFATASE DEFICIENCYC0026705
- Iduronate 2-sulfatase deficiencyC0026705
- Iduronate 2-sulphatase deficiencyC0026705
- Iduronate sulfatase deficiencyC0026705
- Iduronate sulphatase deficiencyC0026705
- MPS 2C0026705
- MPS 2 - Mucopolysaccharidosis 2C0026705
- MPS IIC0026705
- MPS2C0026705
- MPSII - Mucopolysaccharidosis type IIC0026705
- MUCOPOLYSACCHARIDOSIS, TYPE IIC0026705
- Mucopolysaccharidosis 2C0026705
- Mucopolysaccharidosis IIC0026705
- Mucopolysaccharidosis Type 2C0026705
- Mucopolysaccharidosis Type IIC0026705
- Mucopolysaccharidosis type IIC0026705
- Mucopolysaccharidosis type II (disorder)C0026705
- Mucopolysaccharidosis, MPS-IIC0026705
- Mucopolysaccharidosis, type IIC0026705
- SIDS DEFICIENCYC0026705
- SULFOIDURONATE SULFATASE DEFICIENCYC0026705
- Sulfo-iduronate sulfatase deficiencyC0026705
- Sulfoiduronidate sulfatase deficiencyC0026705
- Sulpho-iduronate sulphatase deficiencyC0026705
- Sulphoiduronidate sulphatase deficiencyC0026705
- Syndrome, HunterC0026705
- Syndrome, Hunter'sC0026705
- disease huntersC0026705
- diseases huntersC0026705
- hunter diseaseC0026705
- hunter syndromeC0026705
- hunter's syndromeC0026705
- hunters syndromeC0026705
- mucopolysaccharidosis iiC0026705
- mucopolysaccharidosis type IIC0026705
- mucopolysaccharidosis type iiC0026705
Frequently Asked Questions
What is the ICD-10 code for mucopolysaccharidosis, type ii?
The ICD-10-CM code for mucopolysaccharidosis, type ii is E76.1. The full clinical description is "Mucopolysaccharidosis, type II". E76.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.1 mean?
ICD-10-CM code E76.1 represents "Mucopolysaccharidosis, type II". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.1 a billable code?
Yes, E76.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.1 in?
E76.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.1?
E76.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.1 map to?
E76.1 maps to 5 SNOMED CT concepts: 192795000, 192796004, 70737009, 5667009, 73146005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.1?
E76.1 is linked to 1 UMLS Concept Unique Identifier: C0026705. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.