AutoICD API

D81

Non-billable

Combined immunodeficiencies

Combined immunodeficiencies

This is a header/category code. For billing purposes, use a more specific child code from the list below.

Status

Non-billable / Header

Block

D80-D89

Child Codes

10

Coding Notes

Includes

Conditions included under this code

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

  • autoimmune disease (systemic) NOS (M35.9)
  • functional disorders of polymorphonuclear neutrophils (D71)
  • human immunodeficiency virus [HIV] disease (B20)
  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Excludes 2

Conditions not included here, but the patient may have both

  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Child Codes (10)

D81.0

Severe combined immunodeficiency with reticular dysgenesis

BillableD81.1

Severe combined immunodeficiency w low T- and B-cell numbers

BillableD81.2

Severe combined immunodef w low or normal B-cell numbers

BillableD81.3

Adenosine deaminase [ADA] deficiency

D81.4

Nezelof's syndrome

BillableD81.5

Purine nucleoside phosphorylase [PNP] deficiency

BillableD81.6

Major histocompatibility complex class I deficiency

BillableD81.7

Major histocompatibility complex class II deficiency

BillableD81.8

Other combined immunodeficiencies

D81.9

Combined immunodeficiency, unspecified

Billable

Also Known As / Clinical Terms

UMLS

Frequently Asked Questions

What is ICD-10 code D81?

ICD-10-CM code D81 represents "Combined immunodeficiencies". It is a non-billable header code — use a more specific child code for billing purposes.

Is D81 a billable code?

No, D81 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 10 child codes under D81.

What chapter is D81 in?

D81 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D81?

D81 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.

What are the subcategories under D81?

D81 has 10 child codes, including: D81.0 (Severe combined immunodeficiency with reticular dysgenesis), D81.1 (Severe combined immunodeficiency w low T- and B-cell numbers), D81.2 (Severe combined immunodef w low or normal B-cell numbers), D81.3 (Adenosine deaminase [ADA] deficiency), and 6 more.

What are the UMLS CUIs for D81?

D81 is linked to 1 UMLS Concept Unique Identifier: C2711630. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.