D81.1
BillableSevere combined immunodeficiency w low T- and B-cell numbers
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Combined immunodeficiency associated with maturation pathway defect3439009
- SCID (severe combined immunodeficiency) due to absent peripheral T cell maturation3439009
- Severe combined immunodeficiency due to absent peripheral T cell maturation3439009
- SCID (severe combined immunodeficiency) due to absent IL-2 (interleukin-2) production45390000
- Severe combined immunodeficiency due to absent interleukin-2 production45390000
- SCID (severe combined immunodeficiency) due to absent T cell receptor49555001
- Severe combined immunodeficiency due to absent T cell receptor49555001
- SCID due to absent IL-2 receptor111587007
- Severe combined immunodeficiency (SCID) due to absent IL-2 receptor111587007
- Severe combined immunodeficiency due to absent interleukin-2 receptor111587007
- Severe combined immunodeficiency with low T- and B-cell numbers190997006
- Hereditary eosinophilia191358004
- Disorder of eosinophil417967008
- Omenn syndrome722067005
- Severe combined immunodeficiency with hypereosinophilia722067005
- Combined immunodeficiency due to partial RAG1 deficiency725290000
- Combined immunodeficiency due to partial recombination-activating gene 1 deficiency725290000
- Combined immunodeficiency with expansion of gamma delta T cell725290000
- Severe combined immunodeficiency due to CTPS1 deficiency763623001
- Severe combined immunodeficiency due to cytidine 5-prime triphosphate synthetase 1 deficiency763623001
- SCID (severe combined immunodeficiency) due to complete RAG1/2 deficiency765188009
- Severe combined immunodeficiency due to complete RAG1 (recombination activating gene 1) and/or RAG2 (recombination activating gene 2) deficiency765188009
- Severe combined immunodeficiency due to complete RAG1 and/or RAG2 deficiency765188009
- Severe combined immunodeficiency due to complete recombination-activating gene 1 and/or recombination-activating gene 2 deficiency765188009
- Severe combined immunodeficiency due to LCK (lymphocyte-specific protein-tyrosine kinase) deficiency783617001
- Severe combined immunodeficiency due to LCK deficiency783617001
- Severe combined immunodeficiency due to lymphocyte-specific protein-tyrosine kinase deficiency783617001
- Autosomal dominant T-B- SCID (severe combined immunodeficiency) due to activated RAC2 defect1351235001
- Autosomal dominant T-cell negative, B-cell negative severe combined immunodeficiency due to activated RAC2 defect1351235001
- Autosomal dominant T-cell negative, B-cell negative severe combined immunodeficiency due to activated Rac family small GTPase 2 defect1351235001
UMLS
Frequently Asked Questions
What is ICD-10 code D81.1?
ICD-10-CM code D81.1 represents "Severe combined immunodeficiency [SCID] with low T- and B-cell numbers". It is a billable/specific code that can be used on a claim.
Is D81.1 a billable code?
Yes, D81.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.1 in?
D81.1 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.1?
D81.1 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D81.1 map to?
D81.1 maps to 13 SNOMED CT concepts: 1351235001, 3439009, 725290000, 417967008, 191358004, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.1?
D81.1 is linked to 1 UMLS Concept Unique Identifier: C0451693. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.