Q00
Non-billableAnencephaly and similar malformations
Anencephaly and similar malformations
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Child Codes (3)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(1)
Frequently Asked Questions
What is the ICD-10 code for anencephaly and similar malformations?
The ICD-10-CM code for anencephaly and similar malformations is Q00. The full clinical description is "Anencephaly and similar malformations". Q00 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code Q00 mean?
ICD-10-CM code Q00 represents “Anencephaly and similar malformations”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a non-billable header code. Use a more specific child code for billing purposes.
Is Q00 a billable code?
No, Q00 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under Q00.
What chapter is Q00 in?
Q00 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What are the subcategories under Q00?
Q00 has 3 child codes, including: Q00.0 (Anencephaly), Q00.1 (Craniorachischisis), Q00.2 (Iniencephaly).
What are the UMLS CUIs for Q00?
Q00 is linked to 1 UMLS Concept Unique Identifier: C0158530. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q00 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like anencephaly and similar malformations affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q00?
Q00 maps to the ICD-11 code: LA00.Z (Anencephaly or similar anomalies, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.