Q00.0
BillableAnencephaly
Anencephaly
Status
Billable / Specific
Parent Code
Q00Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Acephaly
- Acrania
- Amyelencephaly
- Hemianencephaly
- Hemicephaly
Excludes 2
Conditions not included here, but the patient may have both
- inborn errors of metabolism (E70-E88)
Also Known As / Clinical Terms
SNOMED CT
- Congenital absence of cerebrum11701009
- Hemicephalia11701009
- Hemicephalus11701009
- Hemicephaly11701009
- Holoacardius acephalus35577008
- Absence of head AND hands63340009
- Acephalocheiria63340009
- Acephalochiria63340009
- Amyelencephalus75076004
- Amyelencephaly75076004
- Hemianencephaly85641006
- Anencephalus89369001
- Anencephaly89369001
- Congenital absence of brain89369001
- Acephalia91848009
- Acephalus91848009
- Acephaly91848009
- Congenital absence of head91848009
- Acrania203923004
- Acardia205834002
- Acephalobrachius205835001
- Incomplete anencephaly359824007
- Holoanencephaly417658006
- Brain aplasia, congenital702611008
- Congenital brain aplasia702611008
- Anencephaly without rachischisis717939009
- Acheiria of left hand16090091000119100
- Congenital absence of left hand16090091000119100
- Acheiria of right hand1078261000119107
- Congenital absence of right hand1078261000119107
UMLS
- AcephalyC0685896
- AcephaliaC0685896
- AcephalusC0685896
- Acephaly (disorder)C0685896
- Congenital absence of headC0685896
- acephaliC0685896
- acephalusC0685896
- acephalyC0685896
- ABSENCE OF BRAIN CONGENC0002902
- ANPHC0002902
- Absence of Brain, CongenitalC0002902
- AnencephaliaC0002902
- AnencephaliasC0002902
- AnencephalusC0002902
- Anencephalus (disorder)C0002902
- AnencephalyC0002902
- Brain Congenital AbsenceC0002902
- CONGEN ABSENCE OF BRAINC0002902
- Congenital Absence of BrainC0002902
- Congenital absence of brainC0002902
- Embryonic anencephalyC0002902
- Fetal anencephalyC0002902
- Fetal anencephaly (disorder)C0002902
- Foetal anencephalyC0002902
- anencephaliaC0002902
- anencephalusC0002902
- anencephalyC0002902
- brain aplasiaC0002902
- AcraniaC0702169
- Acrania (disorder)C0702169
- AcraniasC0702169
- acraniaC0702169
- acraniusC0702169
- AmyelencephalusC0266672
- Amyelencephalus (disorder)C0266672
- AmyelencephalyC0266672
- Brain aplasia, congenitalC0266672
- Congenital brain aplasiaC0266672
- Congenital brain aplasia (disorder)C0266672
- Anencephalies, PartialC0302356
- Anencephaly, HemicranialC0302356
- Anencephaly, IncompleteC0302356
- Anencephaly, PartialC0302356
- HemianencephalyC0302356
- Hemianencephaly (disorder)C0302356
- HemicraniaC0302356
- Hemicranial AnencephalyC0302356
- Incomplete AnencephalyC0302356
- Incomplete anencephalyC0302356
- Incomplete anencephaly (disorder)C0302356
- Partial AnencephaliesC0302356
- Partial AnencephalyC0302356
- hemianencephalyC0302356
- hemicraniaC0302356
- Congenital absence of cerebrumC0266452
- HemicephaliaC0266452
- HemicephalusC0266452
- HemicephalyC0266452
- Hemicephaly (disorder)C0266452
- hemicephaliaC0266452
- hemicephalusC0266452
- hemicephalyC0266452
Frequently Asked Questions
What is the ICD-10 code for anencephaly?
The ICD-10-CM code for anencephaly is Q00.0. The full clinical description is "Anencephaly". Q00.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q00.0 mean?
ICD-10-CM code Q00.0 represents "Anencephaly". It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q00.0 a billable code?
Yes, Q00.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q00.0 in?
Q00.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q00.0 map to?
Q00.0 maps to 16 SNOMED CT concepts: 63340009, 205834002, 91848009, 205835001, 16090091000119100, and 11 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q00.0?
Q00.0 is linked to 6 UMLS Concept Unique Identifiers: C0685896, C0002902, C0702169, C0266672, C0302356, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.