D81.7
BillableMajor histocompatibility complex class II deficiency
Major histocompatibility complex class II deficiency
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Bare lymphocyte syndrome type 2191002000
- Bare lymphocyte syndrome type II191002000
- Immunodeficiency by defective expression of major histocompatibility complex class II191002000
- MHC (major histocompatibility complex) class II deficiency191002000
- Major histocompatibility complex class II deficiency191002000
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X associated protein mutation1351501003
- MHC (major histocompatibility complex) class II deficiency due to RFXAP mutation1351501003
- Major histocompatibility complex class II deficiency due to RFXAP mutation1351501003
- Immunodeficiency by defective expression of major histocompatibility complex class II due to class II major histocompatibility complex transactivator mutation1351502005
- MHC (major histocompatibility complex) class II deficiency due to CIITA mutation1351502005
- Major histocompatibility complex class II deficiency due to CIITA mutation1351502005
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X associated ankyrin containing protein mutation1351503000
- MHC (major histocompatibility complex) class II deficiency due to RFXANK mutation1351503000
- Major histocompatibility complex class II deficiency due to RFXANK mutation1351503000
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X5 mutation1351504006
- MHC (major histocompatibility complex) class II deficiency due to RFX5 mutation1351504006
- Major histocompatibility complex class II deficiency due to RFX5 mutation1351504006
UMLS
- BLS Type IIC2931418
- BLS type IIC2931418
- BLS, TYPE IIC2931418
- Bare Lymphocyte Syndrome Type 2C2931418
- Bare Lymphocyte Syndrome, Type IIC2931418
- Bare lymphocyte syndrome 2C2931418
- Bare lymphocyte syndrome type 2C2931418
- Bare lymphocyte syndrome type IIC2931418
- Immunodeficiency by Defective Expression of MHC Class IIC2931418
- Immunodeficiency by defective expression of major histocompatibility complex class IIC2931418
- Immunodeficiency by defective expression of major histocompatibility complex class II (disorder)C2931418
- MHC (major histocompatibility complex) class II deficiencyC2931418
- Major histocompatibility complex class II deficiencyC2931418
- SCID due to absence of class II HLA antigensC2931418
- SCID, HLA CLASS II-NEGATIVEC2931418
- SCID, HLA Class 2-NegativeC2931418
- SCID, HLA Class II-NegativeC2931418
- SCID, HLA class 2-negativeC2931418
- SCID, HLA class II-negativeC2931418
- SEVERE COMBINED IMMUNODEFICIENCY, HLA CLASS II-NEGATIVEC2931418
- Severe combined immunodeficiency, HLA class II-negativeC2931418
- Severe combined immunodeficiency, HLA class ii-negativeC2931418
Frequently Asked Questions
What is ICD-10 code D81.7?
ICD-10-CM code D81.7 represents "Major histocompatibility complex class II deficiency". It is a billable/specific code that can be used on a claim.
Is D81.7 a billable code?
Yes, D81.7 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.7 in?
D81.7 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.7?
D81.7 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D81.7 map to?
D81.7 maps to 5 SNOMED CT concepts: 191002000, 1351502005, 1351503000, 1351501003, 1351504006. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.7?
D81.7 is linked to 1 UMLS Concept Unique Identifier: C2931418. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.