D81.9
BillableCombined immunodeficiency, unspecified
Combined immunodeficiency, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Severe combined immunodeficiency disorder [SCID] NOS
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Combined T-cell and B-cell immunodeficiency31323000
- SCID - severe combined immunodeficiency31323000
- Severe combined immunodeficiency31323000
- Severe combined immunodeficiency disease31323000
- Hepatic sinusoidal obstruction syndrome65617004
- Hepatic veno-occlusive disease65617004
- Veno-occlusive disease of the liver65617004
- Severe combined immunodeficiency with low T- and B-cell numbers190997006
- Severe combined immunodeficiency with maternofetal engraftment234570002
- Severe combined immunodeficiency with maternofoetal engraftment234570002
- Benign combined immunodeficiency234572005
- Autosomal recessive SCID (severe combined immunodeficiency disease)362993009
- Autosomal recessive severe combined immunodeficiency disease362993009
- Combined immunodeficiency disease442459007
- Cernunnos-XLF deficiency720853005
- NHEJ1 (non-homologous end joining factor) syndrome720853005
- Severe combined immunodeficiency due to Cernunnos protein deficiency720853005
- Severe combined immunodeficiency, microcephaly, growth retardation, sensitivity to ionising radiation syndrome720853005
- Severe combined immunodeficiency, microcephaly, growth retardation, sensitivity to ionizing radiation syndrome720853005
- Congenital atrophy of optic nerve722990003
- Congenital optic atrophy722990003
- Obstruction of visceral vein723877000
- Hepatic veno-occlusive disease with immunodeficiency syndrome724361001
- VODI (veno-occlusive disease, immunodeficiency) syndrome724361001
- VODI syndrome724361001
- Combined immunodeficiency with faciooculoskeletal anomalies syndrome770625006
- Roifman Chitayat syndrome770625006
- Combined immunodeficiency due to RAG 1/2 (recombination activating gene 1/2) deficiency783743009
- Combined immunodeficiency due to RAG 1/2 deficiency783743009
- Combined immunodeficiency with granulomatosis783743009
- Achondroplasia, severe combined immunodeficiency syndrome789777007
- Achondroplasia-Swiss type agammaglobulinaemia syndrome789777007
- Achondroplasia-Swiss type agammaglobulinemia syndrome789777007
- Immunodeficiency, short limb dwarfism syndrome789777007
- Short-limb skeletal dysplasia with severe combined immunodeficiency789777007
- Autoimmune haemolytic anaemia, autoimmune thrombocytopenia, primary immunodeficiency syndrome1222681008
- Autoimmune hemolytic anemia, autoimmune thrombocytopenia, primary immunodeficiency syndrome1222681008
- Evans syndrome associated with primary immunodeficiency1222681008
- TPPII (tripeptidyl-peptidase II) deficiency1222681008
- TPPII-related immunodeficiency, autoimmunity and neurodevelopmental delay with impaired glycolysis and lysosomal expansion disease1222681008
- TRIANGLE (TPPII-related immunodeficiency, autoimmunity, neurodevelopmental delay, impaired glycolysis, lysosomal expansion) disease1222681008
- Tripeptidyl-peptidase II deficiency1222681008
UMLS
- Combined immunity deficiencyC2711630
- Combined immunodeficienciesC2711630
- Combined immunodeficiencyC2711630
- Combined immunodeficiency diseaseC2711630
- Combined immunodeficiency disease (disorder)C2711630
- Combined immunodeficiency syndromeC2711630
- Combined immunodeficiency, unspecifiedC2711630
- Congenital Combined ImmunodeficiencyC2711630
- combined immunity deficiencyC2711630
- combined immunodeficiencyC2711630
- combined immunodeficiency syndromeC2711630
- Severe combined immunodeficiency disorder [SCID] NOSC2873846
Frequently Asked Questions
What is ICD-10 code D81.9?
ICD-10-CM code D81.9 represents "Combined immunodeficiency, unspecified". It is a billable/specific code that can be used on a claim.
Is D81.9 a billable code?
Yes, D81.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.9 in?
D81.9 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.9?
D81.9 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D81.9 map to?
D81.9 maps to 15 SNOMED CT concepts: 789777007, 1222681008, 362993009, 234572005, 720853005, and 10 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.9?
D81.9 is linked to 2 UMLS Concept Unique Identifiers: C2711630, C2873846. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.