D81.6
BillableMajor histocompatibility complex class I deficiency
Major histocompatibility complex class I deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Bare lymphocyte syndrome
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Bare lymphocyte syndrome type 1725136003
- Bare lymphocyte syndrome type I725136003
- Immunodeficiency by defective expression of HLA (human leucocyte antigen) class 1725136003
- Immunodeficiency by defective expression of HLA (human leukocyte antigen) class 1725136003
- Immunodeficiency by defective expression of human leucocyte antigen class 1725136003
- Immunodeficiency by defective expression of human leucocyte antigen class I725136003
- Immunodeficiency by defective expression of human leukocyte antigen class 1725136003
- Immunodeficiency by defective expression of human leukocyte antigen class I725136003
- Immunodeficiency by defective expression of major histocompatibility complex class I725136003
- MHC (major histocompatibility complex) class I deficiency725136003
- Major histocompatibility complex class I deficiency725136003
- Immunodeficiency by defective expression of human leucocyte antigen class 1 due to beta-2-microglobulin mutation1351351007
- Immunodeficiency by defective expression of human leukocyte antigen class 1 due to beta-2-microglobulin mutation1351351007
- Immunodeficiency by defective expression of major histocompatibility complex class I due to beta-2-microglobulin mutation1351351007
- MHC (major histocompatibility complex) class I deficiency due to B2M mutation1351351007
- Major histocompatibility complex class I deficiency due to B2M mutation1351351007
- Immunodeficiency by defective expression of human leucocyte antigen class 1 due to transporter 1, ATP binding cassette subfamily B member mutation1351354004
- Immunodeficiency by defective expression of human leukocyte antigen class 1 due to transporter 1, ATP binding cassette subfamily B member mutation1351354004
- Immunodeficiency by defective expression of major histocompatibility complex class I due to transporter 1, ATP binding cassette subfamily B member mutation1351354004
- MHC (major histocompatibility complex) class I deficiency due to TAP1 mutation1351354004
- Major histocompatibility complex class I deficiency due to TAP1 mutation1351354004
- Immunodeficiency by defective expression of human leucocyte antigen class 1 due to transporter 2, ATP binding cassette subfamily B member mutation1351355003
- Immunodeficiency by defective expression of human leukocyte antigen class 1 due to transporter 2, ATP binding cassette subfamily B member mutation1351355003
- Immunodeficiency by defective expression of major histocompatibility complex class I due to transporter 2, ATP binding cassette subfamily B member mutation1351355003
- MHC (major histocompatibility complex) class I deficiency due to TAP2 mutation1351355003
- Major histocompatibility complex class I deficiency due to TAP2 mutation1351355003
- Immunodeficiency by defective expression of human leucocyte antigen class 1 due to TAP binding protein mutation1351356002
- Immunodeficiency by defective expression of human leukocyte antigen class 1 due to TAP binding protein mutation1351356002
- Immunodeficiency by defective expression of major histocompatibility complex class I due to TAP binding protein mutation1351356002
- MHC (major histocompatibility complex) class I deficiency due to TAPBP mutation1351356002
- Major histocompatibility complex class I deficiency due to TAPBP mutation1351356002
UMLS
- BARE LYMPHOCYTE SYNDROME, TYPE IC1858266
- BLS, TYPE IC1858266
- BLS, Type IC1858266
- Bare Lymphocyte Syndrome Type 1C1858266
- Bare Lymphocyte Syndrome, Type IC1858266
- Bare lymphocyte syndrome type 1C1858266
- Bare lymphocyte syndrome type IC1858266
- HLA CLASS I DEFICIENCY, 1C1858266
- HLA Class I DeficiencyC1858266
- HLA class I deficiencyC1858266
- Immunodeficiency by Defective Expression of MHC Class IC1858266
- Immunodeficiency by defective expression of HLA (human leucocyte antigen) class 1C1858266
- Immunodeficiency by defective expression of HLA (human leukocyte antigen) class 1C1858266
- Immunodeficiency by defective expression of human leucocyte antigen class 1C1858266
- Immunodeficiency by defective expression of human leucocyte antigen class IC1858266
- Immunodeficiency by defective expression of human leukocyte antigen class 1C1858266
- Immunodeficiency by defective expression of human leukocyte antigen class IC1858266
- Immunodeficiency by defective expression of major histocompatibility complex class IC1858266
- Immunodeficiency by defective expression of major histocompatibility complex class I (disorder)C1858266
- MHC (major histocompatibility complex) class I deficiencyC1858266
- MHC CLASS I DEFICIENCY 1C1858266
- MHC1D1C1858266
- Major histocompatibility complex class I deficiencyC1858266
- Bare Lymphocyte SyndromeC0242583
- Bare Lymphocyte SyndromesC0242583
- Bare lymphocyte syndromeC0242583
- Lymphocyte Syndrome, BareC0242583
- Lymphocyte Syndromes, BareC0242583
- Severe combined immunodeficiency due to absent class II human leukocyte antigensC0242583
- Syndrome, Bare LymphocyteC0242583
- Syndromes, Bare LymphocyteC0242583
- bare lymphocyte syndromeC0242583
Frequently Asked Questions
What is the ICD-10 code for major histocompatibility complex class i deficiency?
The ICD-10-CM code for major histocompatibility complex class i deficiency is D81.6. The full clinical description is "Major histocompatibility complex class I deficiency". D81.6 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D81.6 mean?
ICD-10-CM code D81.6 represents "Major histocompatibility complex class I deficiency". It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D81.6 a billable code?
Yes, D81.6 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.6 in?
D81.6 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.6?
D81.6 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D81.6 map to?
D81.6 maps to 5 SNOMED CT concepts: 725136003, 1351356002, 1351351007, 1351354004, 1351355003. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.6?
D81.6 is linked to 2 UMLS Concept Unique Identifiers: C1858266, C0242583. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.