E76.0
Non-billableMucopolysaccharidosis, type I
Mucopolysaccharidosis, type I
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Child Codes (3)
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(21)
UMLS
- Alpha-L-iduronidase deficiencyC0023786
- IDUA deficiencyC0023786
- L-iduronidase deficiencyC0023786
- LipochondrodystrophiesC0023786
- LipochondrodystrophyC0023786
- MPS 1C0023786
- MPS IC0023786
- MPSI - Mucopolysaccharidosis type IC0023786
- Mucopolysaccharidosis 1C0023786
- Mucopolysaccharidosis IC0023786
- Mucopolysaccharidosis Type IC0023786
- Mucopolysaccharidosis type IC0023786
- Mucopolysaccharidosis type I (disorder)C0023786
- Mucopolysaccharidosis, MPS-IC0023786
- Mucopolysaccharidosis, type IC0023786
- i mucopolysaccharidosisC0023786
- iduronidase deficiency diseaseC0023786
- mps iC0023786
- mucopolysaccharidosis iC0023786
- mucopolysaccharidosis type IC0023786
- mucopolysaccharidosis type iC0023786
Frequently Asked Questions
What is the ICD-10 code for mucopolysaccharidosis, type i?
The ICD-10-CM code for mucopolysaccharidosis, type i is E76.0. The full clinical description is "Mucopolysaccharidosis, type I". E76.0 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code E76.0 mean?
ICD-10-CM code E76.0 represents “Mucopolysaccharidosis, type I”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is E76.0 a billable code?
No, E76.0 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 3 child codes under E76.0.
What chapter is E76.0 in?
E76.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.0?
E76.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What are the subcategories under E76.0?
E76.0 has 3 child codes, including: E76.01 (Hurler's syndrome), E76.02 (Hurler-Scheie syndrome), E76.03 (Scheie's syndrome).
What are the UMLS CUIs for E76.0?
E76.0 is linked to 1 UMLS Concept Unique Identifier: C0023786. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E76.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like mucopolysaccharidosis, type i affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E76.0?
E76.0 maps to the ICD-11 code: 5C56.30 (Mucopolysaccharidosis type 1).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.