E76.3
BillableMucopolysaccharidosis, unspecified
Mucopolysaccharidosis, unspecified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(48)
SNOMED CT
- MPS - Mucopolysaccharidosis11380006
- Mucopolysaccharidosis11380006
- Alpha-L-iduronidase deficiency75610003
- L-iduronidase deficiency75610003
- MPS I75610003
- MPSI - Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis, MPS-I75610003
- Restrictive cardiomyopathy due to mucopolysaccharidosis84725008
- Dilated cardiomyopathy due to mucopolysaccharidosis86995005
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Cerebral degeneration in mucopolysaccharidosis192796004
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Secondary restrictive cardiomyopathy415509000
- Cardiomyopathy due to storage disease860839005
- Dilated cardiomyopathy due to lysosomal storage disease880038008
UMLS
Clinical Terms
- Cerebral degeneration in mucopolysaccharidosis
- Mucopolysaccharidosis type I
- Secondary restrictive cardiomyopathy
- Mucopolysaccharidosis NOS
- Dilated cardiomyopathy due to metabolic disorder
- MPS - Mucopolysaccharidosis
- Mucopolysaccharidoses
- Dilated cardiomyopathy due to lysosomal storage disease
- Mucopolysaccharidosis, MPS-I
- Alpha-L-iduronidase deficiency
- MPS I
- Cardiomyopathy due to mucopolysaccharidosis
- Dilated cardiomyopathy secondary to metabolic disorder
- Mucopolysaccharidosis cardiomyopathy
- Cardiomyopathy due to storage disease
- Dilated cardiomyopathy due to mucopolysaccharidosis
- Metabolic cardiomyopathy
- Mucopolysaccharidosis (disorder)
- MPSI - Mucopolysaccharidosis type I
- L-iduronidase deficiency
- Restrictive cardiomyopathy due to mucopolysaccharidosis
Frequently Asked Questions
What is the ICD-10 code for mucopolysaccharidosis, unspecified?
The ICD-10-CM code for mucopolysaccharidosis, unspecified is E76.3. The full clinical description is "Mucopolysaccharidosis, unspecified". E76.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.3 mean?
ICD-10-CM code E76.3 represents “Mucopolysaccharidosis, unspecified”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.3 a billable code?
Yes, E76.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.3 in?
E76.3 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.3?
E76.3 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.3 map to?
E76.3 maps to 10 SNOMED CT concepts: 75610003, 195027000, 860839005, 192796004, 880038008, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.3?
E76.3 is linked to 1 UMLS Concept Unique Identifier: C0026703. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E76.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like mucopolysaccharidosis, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E76.3?
E76.3 maps to the ICD-11 code: 5C56.3Z (Mucopolysaccharidosis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.