AutoICD API

E25.0

Billable

Congenital adrenogenital disorders assoc w enzyme deficiency

Congenital adrenogenital disorders associated with enzyme deficiency

Status

Billable / Specific

Block

E20-E35

Parent Code

E25

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital adrenal hyperplasia
  • 21-Hydroxylase deficiency
  • Salt-losing congenital adrenal hyperplasia

Includes

Conditions included under this code

  • adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
  • Female adrenal pseudohermaphroditism
  • Female heterosexual precocious pseudopuberty
  • Male isosexual precocious pseudopuberty
  • Male macrogenitosomia praecox
  • Male sexual precocity with adrenal hyperplasia
  • Male virilization (female)

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Related Codes(2)
E25.8

Other adrenogenital disorders

BillableE25.9

Adrenogenital disorder, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

5A71.01Congenital adrenal hyperplasiaequivalentPrimary
Also Known As / Clinical Terms(283)

SNOMED CT

UMLS

Clinical Terms

  • Disorder of cholesterol metabolism
  • Adrenal pseudohermaphroditism
  • Congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency
  • Aldosterone deficiency due to 18-hydroxysteroid dehydrogenase deficiency
  • Congenital small adrenal gland
  • Gynandrism
  • Congenital lipoid hyperplasia of adrenal cortex with male pseudohermaphroditism
  • Simple virilizing adrenal hyperplasia
  • CAH - desmolase deficiency
  • Merms
  • Bile acid synthesis disorder
  • CMO I deficiency
  • 21-Hydroxylase Deficiency
  • Simple-virilising congenital adrenal hyperplasia
  • Bile acid synthetic defect
  • CAH - 3 beta-dehydrogenase deficiency
  • Male adrenal pseudohermaphroditism
  • Congenital adrenal hypoplasia, X-linked
  • Adrenal Hyperplasia
  • Inborn error of bile acid synthesis
  • Male pseudohermaphroditism
  • Deficiency of 17beta-hydroxysteroid dehydrogenase
  • Congenital lipoid adrenal hyperplasia due to STAR deficiency
  • adrenal congenital hyperplasia
  • congenital adrenal hyperplasia
  • 3 beta-HSD deficiency
  • Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
  • Male pseudohermaphroditism due to congenital adrenal hyperplasia
  • Female pseudohermaphroditism due to congenital adrenal hyperplasia
  • Foetal endocrine disorder
  • Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency classic form
  • CAH1
  • Deficiency of steroid 21-hydroxylase
  • Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency
  • Cholesterol desmolase deficiency
  • Fetal endocrine disorder
  • Deficiency of steroid 11-beta-hydroxylase
  • Late onset congenital adrenal hyperplasia
  • CAH - Congenital adrenal hypoplasia
  • Salt-losing congenital adrenal hyperplasia (disorder)
  • Wilkins disease
  • 3-Beta-hydroxy-delta-5-C27-steroid dehydrogenase deficiency
  • Corticosterone 18-monooxygenase deficiency
  • Congenital lipoid adrenal hyperplasia due to steroidogenic acute regulatory protein deficiency non classic form
  • Mild steroid 21-hydroxylase deficiency
  • Disorder of bile acid synthesis
  • Steroid 21-hydroxylase deficiency, simple virilising type
  • Adrenogenital disorder due to 11-beta-hydroxylase deficiency
  • Congenital adrenal hyperplasia due to 21-hydroxylase deficiency non-classic form
  • Steroid 21-monooxygenase deficiency, simple virilizing type
  • Deficiency of steroid 11-beta-monooxygenase
  • 21-hydroxylase deficiency, salt wasting type
  • CMO II deficiency
  • BASD - Bile acid synthetic defect
  • Congenital hypoplasia of adrenal gland
  • Congenital adrenal hyperplasia - desmolase deficiency
  • Congenital lipoid adrenal hyperplasia due to STAR deficiency non-classic form
  • hyperplasia adrenal congenital
  • CAH - Congenital adrenal hyperplasia
  • 46,XY disorder of sex development due to isolated 17,20-lyase deficiency
  • Congenital bile acid synthesis defect type 1
  • Aldosterone deficiency due to 18-hydroxylase defect
  • Defective synthesis of cholesterol desmolase
  • Hypertension due to congenital adrenal hyperplasia
  • Moderate steroid 21-hydroxylase deficiency
  • 17 alpha-Hydroxyprogesterone aldolase deficiency
  • Adrenal virilism
  • CAH - 18-hydroxylase deficiency
  • CAH - 11 beta-hydroxylase deficiency
  • Adrenogenital Syndrome
  • Congenital adrenal hypoplasia
  • Steroid 21-monooxygenase deficiency, salt wasting type
  • 11-beta-hydroxylase deficiency
  • Steroid 17,20-lyase deficiency
  • Simple-virilizing congenital adrenal hyperplasia
  • Apert-Gallais syndrome
  • Aldosterone deficiency
  • Salt-losing congenital adrenal hyperplasia
  • Virilization-adrenogenital syndrome
  • Deficiency of 3alpha-hydroxysteroid dehydrogenase
  • Hypoaldosteronism
  • CAH - 21-hydroxylase deficiency
  • Adrenogenital disorder due to 21-hydroxylase deficiency
  • Disorder of cholesterol catabolism
  • Salt-losing congenital adrenal hyperplasia with virilism
  • CONGEN ADRENAL HYPERPLASIA
  • Congenital adrenal hyperplasia, type 1
  • Fetal virilism
  • Hyperplasia, Congenital Adrenal
  • Congenital lipoid adrenal hyperplasia due to STAR deficiency classic form
  • Female pseudohermaphroditism
  • Hyperandrogenism due to non-classic type of 21-hydroxylase deficiency
  • Simple virilising adrenal hyperplasia
  • Corticosterone methyl oxidase type I deficiency
  • Pseudohermaphrodite, female with adrenocortical disorder
  • Synthetic defect of bile acids
  • Virilization - adrenogenital
  • Hypertensive congenital adrenal hyperplasia
  • Corticosterone methyl oxidase type II deficiency
  • Cholesterol monooxygenase (side-chain cleaving) deficiency
  • HYPERPLASIA CONGEN ADRENAL
  • 18-Hydroxycorticosterone dehydrogenase deficiency
  • Congenital adrenogenital syndrome
  • Foetal virilism
  • 3 beta-Hydroxysteroid dehydrogenase deficiency
  • 18-Hydroxylase deficiency
  • Congenital Adrenal Hyperplasias
  • Steroid 11-beta-monooxygenase deficiency
  • Adrenal Hyperplasia, Congenital
  • Congenital Adrenal Gland Hyperplasia
  • Severe steroid 21-hydroxylase deficiency
  • Congenital adrenal hyperplasia, type 2
  • hyperplasia congenital adrenal
  • Virilizing syndrome of adrenal origin
  • Adrenal Hyperplasias, Congenital
  • Defective synthesis of 17-20 desmolase
  • Congenital adrenal hyperplasia (CAH)- desmolase deficiency
  • Virilisation-adrenogenital syndrome
  • Deficiency of steroid 21-monooxygenase
  • Congenital adrenal hyperplasia (disorder)
  • Hyperandrogenism due to non-classic 21-hydroxylase deficiency
  • Female adrenal pseudohermaphroditism
  • Steroid 21-monooxygenase deficiency, simple virilising type
  • Congenital adrenal cortical hyperplasia
  • Ferms
  • ADRENAL HYPERPLASIA CONGEN
  • Congenital adrenal hyperplasia, type 4
  • Male pseudohermaphroditism due to testicular 17,20-desmolase deficiency
  • Virilising syndrome of adrenal origin
  • Steroid 21-hydroxylase deficiency, simple virilizing type
  • Virilisation - adrenogenital
  • 20,22-Desmolase deficiency
  • Congenital adrenal hyperplasia, type 3
  • Pseudohermaphroditism due to congenital adrenal hyperplasia
  • Hyperplasias, Congenital Adrenal
  • Deficiency of 3beta-hydroxysteroid dehydrogenase
Frequently Asked Questions
What is the ICD-10 code for congenital adrenogenital disorders assoc w enzyme deficiency?

The ICD-10-CM code for congenital adrenogenital disorders assoc w enzyme deficiency is E25.0. The full clinical description is "Congenital adrenogenital disorders associated with enzyme deficiency". E25.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E25.0 mean?

ICD-10-CM code E25.0 represents “Congenital adrenogenital disorders associated with enzyme deficiency”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E25.0 a billable code?

Yes, E25.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E25.0 in?

E25.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E25.0?

E25.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); galactorrhea (N64.3); gynecomastia (N62); and 2 more.

What SNOMED CT codes does E25.0 map to?

E25.0 maps to 45 SNOMED CT concepts: 124214007, 49013001, 47757001, 44231009, 124221007, and 40 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E25.0?

E25.0 is linked to 4 UMLS Concept Unique Identifiers: C0852654, C0001627, C0494311, C0342464. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E25.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital adrenogenital disorders assoc w enzyme deficiency affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E25.0?

E25.0 maps to the ICD-11 code: 5A71.01 (Congenital adrenal hyperplasia).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.