AutoICD API

E76.1

Billable

Mucopolysaccharidosis, type II

Mucopolysaccharidosis, type II

Status

Billable / Specific

Block

E70-E88

Parent Code

E76

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Hunter's syndrome

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(5)
E76.0

Mucopolysaccharidosis, type I

E76.2

Other mucopolysaccharidoses

E76.3

Mucopolysaccharidosis, unspecified

BillableE76.8

Other disorders of glucosaminoglycan metabolism

BillableE76.9

Glucosaminoglycan metabolism disorder, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

5C56.31Mucopolysaccharidosis type 2equivalentPrimary
Also Known As / Clinical Terms(117)

SNOMED CT

UMLS

Clinical Terms

  • Cerebral degeneration in mucopolysaccharidosis
  • Cerebral degeneration in Hunter's disease
  • Hunters Syndrome
  • IDS DEFICIENCY
  • Hunter syndrome
  • Mucopolysaccharidosis type II severe form
  • Sulfoiduronidate sulfatase deficiency
  • Mucopolysaccharidosis II
  • Mucopolysaccharidosis type II (disorder)
  • diseases hunters
  • hunter disease
  • Mucopolysaccharidosis type II mild form
  • Syndrome, Hunter
  • Hunter Syndrome Gargoylism
  • MPS II
  • SIDS DEFICIENCY
  • Syndrome, Hunter's
  • hunter's syndrome
  • Sulfo-iduronate sulfatase deficiency
  • Gargoylism, Hunter Syndrome
  • Mucopolysaccharidosis Type II
  • IDURONATE 2-SULFATASE DEFICIENCY
  • Cerebral degeneration in Hunter disease
  • MPS 2
  • SULFOIDURONATE SULFATASE DEFICIENCY
  • Deficiency of iduronate-2-sulphatase
  • disease hunters
  • MPS 2 - Mucopolysaccharidosis 2
  • Mucopolysaccharidosis 2
  • Sulpho-iduronate sulphatase deficiency
  • MPS2
  • Mucopolysaccharidosis Type 2
  • Iduronate sulfatase deficiency
  • Deficiency of iduronate-2-sulfatase
  • Hunter syndrome, severe form
  • MPSII - Mucopolysaccharidosis type II
  • Iduronate sulphatase deficiency
  • Sulphoiduronidate sulphatase deficiency
  • Mucopolysaccharidosis, MPS-II
  • Iduronate 2-sulphatase deficiency
  • Hunter's syndrome, mild form
  • Hunter syndrome, mild form
  • Hunter's syndrome, severe form
Frequently Asked Questions
What is the ICD-10 code for mucopolysaccharidosis, type ii?

The ICD-10-CM code for mucopolysaccharidosis, type ii is E76.1. The full clinical description is "Mucopolysaccharidosis, type II". E76.1 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E76.1 mean?

ICD-10-CM code E76.1 represents “Mucopolysaccharidosis, type II”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E76.1 a billable code?

Yes, E76.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E76.1 in?

E76.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E76.1?

E76.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E76.1 map to?

E76.1 maps to 5 SNOMED CT concepts: 192795000, 192796004, 70737009, 5667009, 73146005. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E76.1?

E76.1 is linked to 1 UMLS Concept Unique Identifier: C0026705. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E76.1 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like mucopolysaccharidosis, type ii affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E76.1?

E76.1 maps to the ICD-11 code: 5C56.31 (Mucopolysaccharidosis type 2).

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try FreeView API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.