E76.01
BillableHurler's syndrome
Hurler's syndrome
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Also Known As / Clinical Terms(108)
SNOMED CT
- Dysostosis multiplex syndrome65327002
- Gargoylism65327002
- Hurler disease MPS type 1H65327002
- Hurler's syndrome65327002
- Hurler-Pfaundler syndrome65327002
- L-iduronidase deficiency, Hurler type65327002
- Lipochondrodystrophy65327002
- MPS 1-H - Mucopolysaccharidosis type I-H65327002
- Mucopolysaccharidosis type I severe form65327002
- Mucopolysaccharidosis type I-H65327002
- Mucopolysaccharidosis, MPS-I-H65327002
- Alpha-L-iduronidase deficiency75610003
- L-iduronidase deficiency75610003
- MPS I75610003
- MPSI - Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis type I75610003
- Mucopolysaccharidosis, MPS-I75610003
- Hurloid facies80174007
- Dysostosis multiplex254069004
- Dysostosis multiplex group279081001
UMLS
- Disease, Hurler'sC0086795
- Dysostosis multiplex syndromeC0086795
- GargoylismC0086795
- Gargoylism, Hurler SyndromeC0086795
- GargoylismsC0086795
- HURLER DISC0086795
- HURLER SYNDROMEC0086795
- HURLERS DISC0086795
- Hurler DiseaseC0086795
- Hurler SyndromeC0086795
- Hurler Syndrome GargoylismC0086795
- Hurler disease MPS type 1HC0086795
- Hurler syndromeC0086795
- Hurler's DiseaseC0086795
- Hurler's SyndromeC0086795
- Hurler's diseaseC0086795
- Hurler's syndromeC0086795
- Hurler-Pfaundler syndromeC0086795
- L-iduronidase deficiency, Hurler typeC0086795
- LipochondrodystrophyC0086795
- MPS 1-H - Mucopolysaccharidosis type I-HC0086795
- MPS I HC0086795
- MPS1-HC0086795
- MUCOPOLYSACCHARIDOSIS TYPE IHC0086795
- Mucopolysaccharidosis Type IHC0086795
- Mucopolysaccharidosis Type IhC0086795
- Mucopolysaccharidosis Type IhsC0086795
- Mucopolysaccharidosis type I severe formC0086795
- Mucopolysaccharidosis type I-HC0086795
- Mucopolysaccharidosis type I-H (disorder)C0086795
- Mucopolysaccharidosis, MPS-I-HC0086795
- Pfaundler-Hurler SyndromeC0086795
- Syndrome, Hurler'sC0086795
- Type Ih, MucopolysaccharidosisC0086795
- Type Ihs, MucopolysaccharidosisC0086795
- gargoylismC0086795
- hurlerC0086795
- hurler diseaseC0086795
- hurler syndromeC0086795
- hurler's diseaseC0086795
- hurler's syndromeC0086795
- hurlersC0086795
- hurlers diseaseC0086795
- hurlers syndromeC0086795
- lipochondrodystrophyC0086795
- thompson syndromeC0086795
Clinical Terms
- MPS 1-H - Mucopolysaccharidosis type I-H
- Mucopolysaccharidosis type I
- Mucopolysaccharidosis type I-H
- Hurler Syndrome
- hurler
- Dysostosis multiplex group
- Hurler-Pfaundler syndrome
- Gargoylism
- Mucopolysaccharidosis, MPS-I
- Type Ihs, Mucopolysaccharidosis
- Mucopolysaccharidosis type I severe form
- Alpha-L-iduronidase deficiency
- L-iduronidase deficiency, Hurler type
- hurlers
- Mucopolysaccharidosis, MPS-I-H
- MPS I
- Disease, Hurler's
- MPS I H
- Hurloid facies
- Lipochondrodystrophy
- Mucopolysaccharidosis type I-H (disorder)
- Mucopolysaccharidosis Type Ih
- Dysostosis multiplex
- MPS1-H
- Hurler's Disease
- Pfaundler-Hurler Syndrome
- hurler disease
- Dysostosis multiplex syndrome
- Mucopolysaccharidosis Type Ihs
- hurlers syndrome
- Syndrome, Hurler's
- HURLERS DIS
- MPSI - Mucopolysaccharidosis type I
- Type Ih, Mucopolysaccharidosis
- Hurler Syndrome Gargoylism
- Hurler disease MPS type 1H
- L-iduronidase deficiency
- hurlers disease
- HURLER DIS
- thompson syndrome
- Gargoylisms
- Gargoylism, Hurler Syndrome
Frequently Asked Questions
What is the ICD-10 code for hurler's syndrome?
The ICD-10-CM code for hurler's syndrome is E76.01. The full clinical description is "Hurler's syndrome". E76.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.01 mean?
ICD-10-CM code E76.01 represents “Hurler's syndrome”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.01 a billable code?
Yes, E76.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.01 in?
E76.01 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.01?
E76.01 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.01 map to?
E76.01 maps to 5 SNOMED CT concepts: 75610003, 254069004, 279081001, 65327002, 80174007. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.01?
E76.01 is linked to 1 UMLS Concept Unique Identifier: C0086795. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E76.01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hurler's syndrome affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E76.01?
There is no direct ICD-11 mapping available for E76.01 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.