AutoICD API

E76.03

Billable

Scheie's syndrome

Scheie's syndrome

Status

Billable / Specific

Block

E70-E88

Parent Code

E76.0

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
E76.01

Hurler's syndrome

BillableE76.02

Hurler-Scheie syndrome

Billable
Also Known As / Clinical Terms(70)

SNOMED CT

UMLS

Clinical Terms

  • Mucopolysaccharidosis type I
  • Scheie Syndrome
  • Mucopolysaccharidosis, MPS-I-S
  • Mucopolysaccharidosis, MPS-I
  • Mucopolysaccharidosis I-S
  • Alpha-L-iduronidase deficiency
  • Mucopolysaccharidosis V
  • Syndrome, Scheie's
  • scheies syndrome
  • MPS I
  • Mucopolysaccharidosis type I-S (disorder)
  • MPS I S
  • Mucopolysaccharidosis type I mild form
  • MUCOPOLYSACCHARIDOSIS TYPE IS
  • MPS 5
  • MPS V, FORMERLY
  • Mucopolysaccharidosis type I-S
  • L-iduronidase deficiency, Scheie type
  • MPSI - Mucopolysaccharidosis type I
  • Scheie disease MPS type 1S
  • L-iduronidase deficiency
  • MPS1-S
  • Mucopolysaccharidosis IS
  • MUCOPOLYSACCHARIDOSIS TYPE V, FORMERLY
  • MPS 1-S - Mucopolysaccharidosis type I-S
  • Mucopolysaccharidosis I S
  • Mucopolysaccharidosis 5
  • MPS5, FORMERLY
Frequently Asked Questions
What is the ICD-10 code for scheie's syndrome?

The ICD-10-CM code for scheie's syndrome is E76.03. The full clinical description is "Scheie's syndrome". E76.03 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E76.03 mean?

ICD-10-CM code E76.03 represents “Scheie's syndrome”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E76.03 a billable code?

Yes, E76.03 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E76.03 in?

E76.03 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E76.03?

E76.03 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E76.03 map to?

E76.03 maps to 2 SNOMED CT concepts: 75610003, 73123008. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E76.03?

E76.03 is linked to 1 UMLS Concept Unique Identifier: C0026708. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E76.03 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like scheie's syndrome affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E76.03?

There is no direct ICD-11 mapping available for E76.03 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try FreeView API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.