Q89.1
BillableCongenital malformations of adrenal gland
Congenital malformations of adrenal gland
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
Q89.0Congenital absence and malformations of spleen
Q89.2Congenital malformations of other endocrine glands
Q89.3Situs inversus
Q89.4Conjoined twins
Q89.7Multiple congenital malformations, not elsewhere classified
Q89.8Other specified congenital malformations
Q89.9Congenital malformation, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(137)
SNOMED CT
- Accessory adrenal cortex7322007
- Aberrant adrenal gland49494003
- Ectopic adrenal gland49494003
- Congenital anomaly of adrenal gland60637003
- Congenital malformation of adrenal gland60637003
- Accessory adrenal gland68352004
- Supernumerary adrenal gland68352004
- Congenital absence of adrenal gland83190008
- Adrenal rest91285009
- Ectopic adrenal cortex91285009
- Congenital abnormal fusion of adrenal glands92833001
- Congenital fused adrenal glands92833001
- Congenital abnormal shape of adrenal gland92886003
- Congenital misshapen adrenal gland92886003
- Congenital enlarged adrenal gland93068008
- Congenital hypertrophy of adrenal gland93068008
- CAH - Congenital adrenal hypoplasia93235007
- Congenital adrenal hypoplasia93235007
- Congenital hypoplasia of adrenal gland93235007
- Congenital small adrenal gland93235007
- Congenital malposition of adrenal gland93304003
- Congenital malpositioned adrenal gland93304003
- Extracapsular adrenal tissue93452009
- Deficiency of glycerol kinase124322002
- Familial hyperglycerolaemia124322002
- Familial hyperglycerolemia124322002
- GK1 deficiency124322002
- GKD - Glycerol kinase deficiency124322002
- Glycerol kinase deficiency124322002
- Hyperglycerolaemia124322002
- Hyperglycerolemia124322002
- Congenital cyst of adrenal gland205744006
- Enlarged adrenal gland237782001
- Adrenal cyst237784000
- Cyst of adrenal gland237784000
- Disorder of glycerol metabolism237977000
- Abnormal luteotrophic hormone386776005
- Abnormal pituitary interstitial cell stimulating hormone386776005
- Abnormal pituitary luteinising hormone386776005
- Abnormal pituitary luteinizing hormone386776005
- Measurement procedure result absent442228008
- IMAGe syndrome702384004
- Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome702384004
- Adrenal aplasia702615004
- Aplasia of adrenal gland702615004
- SERKAL (sex reversion, kidney, adrenal and lung dysgenesis) syndrome723720008
- SERKAL syndrome723720008
- Sex reversion, kidney, adrenal and lung dysgenesis syndrome723720008
- Familial adrenal hypoplasia miniature type782917007
- Familial adrenal hypoplasia with absent pituitary luteinising hormone782917007
- Familial adrenal hypoplasia with absent pituitary luteinizing hormone782917007
- Hypoplasia of adrenal medulla1144876005
- Adrenal hypertrophy1217058003
- Hypertrophy of adrenal gland1217058003
- MIRAGE (myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy) syndrome1234831009
- MIRAGE syndrome1234831009
- Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy syndrome1234831009
- Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital phenotypes, enteropathy syndrome1234831009
- Complex GKD (complex glycerol kinase deficiency)1295529002
- Complex glycerol kinase deficiency1295529002
- Xp21 contiguous gene deletion syndrome1295529002
- Xp21 deletion syndrome1295529002
- Xp21 microdeletion syndrome1295529002
- Short stature co-occurrent and due to endocrine disorder368331000119100
UMLS
Clinical Terms
- Congenital enlarged adrenal gland
- Congenital abnormal shape of adrenal gland
- CAH - Congenital adrenal hypoplasia
- MIRAGE (myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy) syndrome
- Abnormal pituitary luteinising hormone
- Aplasia of adrenal gland
- Hypoplasia of adrenal medulla
- Complex GKD (complex glycerol kinase deficiency)
- Extracapsular adrenal tissue
- Congenital small adrenal gland
- Xp21 deletion syndrome
- Congenital hypertrophy of adrenal gland
- SERKAL (sex reversion, kidney, adrenal and lung dysgenesis) syndrome
- Congenital adrenal gland anomaly NOS
- Abnormal pituitary luteinizing hormone
- Congenital abnormal fusion of adrenal glands
- Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital phenotypes, enteropathy syndrome
- Accessory adrenal gland
- Xp21 microdeletion syndrome
- Adrenal aplasia
- Abnormal luteotrophic hormone
- Congenital cyst of adrenal gland
- Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome
- Glycerol kinase deficiency
- Congenital misshapen adrenal gland
- Measurement procedure result absent
- Adrenal cyst
- Familial hyperglycerolaemia
- Xp21 contiguous gene deletion syndrome
- Accessory adrenal cortex
- Congenital anomaly of adrenal gland
- Familial adrenal hypoplasia with absent pituitary luteinising hormone
- Ectopic adrenal cortex
- Hyperglycerolemia
- Sex reversion, kidney, adrenal and lung dysgenesis syndrome
- Complex glycerol kinase deficiency
- Congenital malposition of adrenal gland
- Familial adrenal hypoplasia with absent pituitary luteinizing hormone
- Congenital hypoplasia of adrenal gland
- Ectopic adrenal gland
- Congenital malpositioned adrenal gland
- Hypertrophy of adrenal gland
- IMAGe syndrome
- MIRAGE syndrome
- Supernumerary adrenal gland
- Familial adrenal hypoplasia miniature type
- Congenital fused adrenal glands
- Disorder of glycerol metabolism
- Congenital malformation of adrenal gland
- Enlarged adrenal gland
- Short stature co-occurrent and due to endocrine disorder
- Deficiency of glycerol kinase
- GKD - Glycerol kinase deficiency
- SERKAL syndrome
- Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy syndrome
- GK1 deficiency
- Adrenal rest
- Familial hyperglycerolemia
- Aberrant adrenal gland
- Adrenal hypertrophy
- Congenital absence of adrenal gland
- Cyst of adrenal gland
- Hyperglycerolaemia
- Congenital anomaly of adrenal gland (disorder)
- Abnormal pituitary interstitial cell stimulating hormone
- Congenital adrenal hypoplasia
- Congenital anomalies of adrenal gland
Frequently Asked Questions
What is the ICD-10 code for congenital malformations of adrenal gland?
The ICD-10-CM code for congenital malformations of adrenal gland is Q89.1. The full clinical description is "Congenital malformations of adrenal gland". Q89.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q89.1 mean?
ICD-10-CM code Q89.1 represents “Congenital malformations of adrenal gland”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q89.1 a billable code?
Yes, Q89.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q89.1 in?
Q89.1 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q89.1?
Q89.1 has Excludes1 notes indicating codes that cannot be used together with it, including: adrenogenital disorders (E25.-); congenital adrenal hyperplasia (E25.0).
What SNOMED CT codes does Q89.1 map to?
Q89.1 maps to 28 SNOMED CT concepts: 49494003, 386776005, 7322007, 68352004, 702615004, and 23 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q89.1?
Q89.1 is linked to 1 UMLS Concept Unique Identifier: C0158797. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q89.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformations of adrenal gland affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q89.1?
Q89.1 maps to the ICD-11 code: LC8Z (Structural developmental anomalies of the adrenal glands, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.