AutoICD API

Q89.1

Billable

Congenital malformations of adrenal gland

Congenital malformations of adrenal gland

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(7)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(137)

SNOMED CT

Clinical Terms

  • Congenital enlarged adrenal gland
  • Congenital abnormal shape of adrenal gland
  • CAH - Congenital adrenal hypoplasia
  • MIRAGE (myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy) syndrome
  • Abnormal pituitary luteinising hormone
  • Aplasia of adrenal gland
  • Hypoplasia of adrenal medulla
  • Complex GKD (complex glycerol kinase deficiency)
  • Extracapsular adrenal tissue
  • Congenital small adrenal gland
  • Xp21 deletion syndrome
  • Congenital hypertrophy of adrenal gland
  • SERKAL (sex reversion, kidney, adrenal and lung dysgenesis) syndrome
  • Congenital adrenal gland anomaly NOS
  • Abnormal pituitary luteinizing hormone
  • Congenital abnormal fusion of adrenal glands
  • Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital phenotypes, enteropathy syndrome
  • Accessory adrenal gland
  • Xp21 microdeletion syndrome
  • Adrenal aplasia
  • Abnormal luteotrophic hormone
  • Congenital cyst of adrenal gland
  • Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome
  • Glycerol kinase deficiency
  • Congenital misshapen adrenal gland
  • Measurement procedure result absent
  • Adrenal cyst
  • Familial hyperglycerolaemia
  • Xp21 contiguous gene deletion syndrome
  • Accessory adrenal cortex
  • Congenital anomaly of adrenal gland
  • Familial adrenal hypoplasia with absent pituitary luteinising hormone
  • Ectopic adrenal cortex
  • Hyperglycerolemia
  • Sex reversion, kidney, adrenal and lung dysgenesis syndrome
  • Complex glycerol kinase deficiency
  • Congenital malposition of adrenal gland
  • Familial adrenal hypoplasia with absent pituitary luteinizing hormone
  • Congenital hypoplasia of adrenal gland
  • Ectopic adrenal gland
  • Congenital malpositioned adrenal gland
  • Hypertrophy of adrenal gland
  • IMAGe syndrome
  • MIRAGE syndrome
  • Supernumerary adrenal gland
  • Familial adrenal hypoplasia miniature type
  • Congenital fused adrenal glands
  • Disorder of glycerol metabolism
  • Congenital malformation of adrenal gland
  • Enlarged adrenal gland
  • Short stature co-occurrent and due to endocrine disorder
  • Deficiency of glycerol kinase
  • GKD - Glycerol kinase deficiency
  • SERKAL syndrome
  • Myelodysplasia, infection, restriction of growth, adrenal hypoplasia, genital anomalies, enteropathy syndrome
  • GK1 deficiency
  • Adrenal rest
  • Familial hyperglycerolemia
  • Aberrant adrenal gland
  • Adrenal hypertrophy
  • Congenital absence of adrenal gland
  • Cyst of adrenal gland
  • Hyperglycerolaemia
  • Congenital anomaly of adrenal gland (disorder)
  • Abnormal pituitary interstitial cell stimulating hormone
  • Congenital adrenal hypoplasia
  • Congenital anomalies of adrenal gland
Frequently Asked Questions
What is the ICD-10 code for congenital malformations of adrenal gland?

The ICD-10-CM code for congenital malformations of adrenal gland is Q89.1. The full clinical description is "Congenital malformations of adrenal gland". Q89.1 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q89.1 mean?

ICD-10-CM code Q89.1 represents “Congenital malformations of adrenal gland”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q89.1 a billable code?

Yes, Q89.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q89.1 in?

Q89.1 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q89.1?

Q89.1 has Excludes1 notes indicating codes that cannot be used together with it, including: adrenogenital disorders (E25.-); congenital adrenal hyperplasia (E25.0).

What SNOMED CT codes does Q89.1 map to?

Q89.1 maps to 28 SNOMED CT concepts: 49494003, 386776005, 7322007, 68352004, 702615004, and 23 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q89.1?

Q89.1 is linked to 1 UMLS Concept Unique Identifier: C0158797. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q89.1 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformations of adrenal gland affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q89.1?

Q89.1 maps to the ICD-11 code: LC8Z (Structural developmental anomalies of the adrenal glands, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.