PIGN-CDG - phosphatidylinositol glycan anchor biosynthesis class N congenital disorder of glycosylation
Native American myopathy
Sagittal synostosis
Congenital generalized hypercontractile muscle stiffness syndrome
ADNP-related multiple congenital anomalies, intellectual disability, autism spectrum disorder
Autositic twin of asymmetrical conjoined twins
Congenital complete absence of upper limb
Congenital disorder of glycosylation due to PIGN (phosphatidylinositol glycan anchor biosynthesis class N) deficiency
Familial dwarfism AND stiff joints
Lethal multiple pterygium syndrome
Multiple congenital anomalies
Multiple pterygium syndrome
EEC - Ectodermal dysplasia with ectrodactyly and cleft lip or palate
Monocephalus
CK syndrome
MCAHS (multiple congenital anomalies, hypotonia, seizures syndrome) type 2
Foetus with hereditary disease
Multiple malformation syndrome with unusual brain and/or neuromuscular findings
Anomalies congenital multiple
Akinesia
Ethmocephaly
Multiple Abnormalities
Male emopamil-binding protein disorder with neurological defect
Scaphocephaly
Multiple congenital anomalies NOS
Abnormalities, Multiple
Multiple congenital deformities NOS
Complex craniosynostosis
Tondury-Duhamel anomalad
multiple congenital anomaly
Helsmoortel-van der Aa syndrome
Omocephalus
Pentalogy of Cantrell
Multiple congenital abnormalities
Parieto-occipital craniosynostosis
SETD2-related microcephaly, severe intellectual disability, multiple congenital anomalies syndrome
Congenital myopathy, cleft palate. malignant hyperthermia syndrome
Kleeblattschadel deformity
Ochoa syndrome
Synotia
Fetal hereditary disease
Synotus
Ectrodactyly-ectodermal dysplasia-clefting syndrome
Cloverleaf skull syndrome
Interparietal craniosynostosis
Cantu syndrome
Amelia of upper limb
SET domain containing 2, histone lysine methyltransferase-related microcephaly, severe intellectual disability, multiple congenital anomalies syndrome
Activity dependent neuroprotector homeobox related multiple congenital anomalies, intellectual disability, autism spectrum disorder
Timothy syndrome
ABNORM MULTIPLE
Transverse deficiency of arm, shoulder level
Clover leaf skull deformity
EEC syndrome
Autosite of asymmetrical conjoined twins
Duhamel syndrome
Acephalobrachius
Hereditary disorder of fetus
Lambdoid craniosynostosis
Cantu's syndrome
Timothy syndrome type 2
Sagittal craniosynostosis
anomalies multiple
Hydrolethalus syndrome
abnormalities congenital multiple
Multiple congenital anomalies, hypotonia, seizures syndrome
Ethmocephalus
Duhamel's syndrome
Monocephalus tripus dibrachius
Malformations multiple
Congenital generalised hypercontractile muscle stiffness syndrome
SETD2 (SET domain containing 2, histone lysine methyltransferase) related microcephaly, severe intellectual disability, multiple congenital anomalies syndrome
Cloverleaf skull with multiple congenital anomalies syndrome
Multiple congenital anomalies, hypotonia, seizures syndrome type 2
MULTIPLE ABNORM
Male EBP (emopamil-binding protein) disorder with neurological defect
Ectodermal dysplasia with ectrodactyly and cleft lip or palate
Moore-Federman syndrome
Fetus with hereditary disease
Rudiger's syndrome
MEND (male emopamil-binding protein disorder with neurological defect) syndrome
Long QT syndrome type 8
Anomaly congenital multiple (NOS)
X-linked intellectual disability, microcephaly, cortical malformation, thin habitus syndrome

Frequently Asked Questions

What is the ICD-10 code for multiple congenital malformations, not elsewhere classified?

The ICD-10-CM code for multiple congenital malformations, not elsewhere classified is Q89.7. The full clinical description is "Multiple congenital malformations, not elsewhere classified". Q89.7 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q89.7 mean?

ICD-10-CM code Q89.7 represents “Multiple congenital malformations, not elsewhere classified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q89.7 a billable code?

Yes, Q89.7 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q89.7 in?

Q89.7 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q89.7?

Q89.7 has Excludes1 notes indicating codes that cannot be used together with it, including: congenital malformation syndromes affecting multiple systems (Q87.-).

What SNOMED CT codes does Q89.7 map to?

Q89.7 maps to 35 SNOMED CT concepts: 766824003, 205835001, 33994004, 205306000, 90313000, and 30 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q89.7?

Q89.7 is linked to 2 UMLS Concept Unique Identifiers: C0000772, C0495643. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q89.7 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like multiple congenital malformations, not elsewhere classified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q89.7?

Q89.7 maps to the ICD-11 code: LD2Z (Multiple developmental anomalies or syndromes, unspecified).

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try Free View API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.