Q89.3
BillableSitus inversus
Situs inversus
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Dextrocardia with situs inversus
- Mirror-image atrial arrangement with situs inversus
- Situs inversus or transversus abdominalis
- Situs inversus or transversus thoracis
- Transposition of abdominal viscera
- Transposition of thoracic viscera
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
Q89.0Congenital absence and malformations of spleen
Q89.1Congenital malformations of adrenal gland
Q89.2Congenital malformations of other endocrine glands
Q89.4Conjoined twins
Q89.7Multiple congenital malformations, not elsewhere classified
Q89.8Other specified congenital malformations
Q89.9Congenital malformation, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(124)
SNOMED CT
- Abnormal position of heart10818008
- Congenital abnormality of cardiac position10818008
- Congenital malposition of heart10818008
- Congenital malpositioned heart10818008
- Isomerism sequence24614000
- Laterality sequence24614000
- Dextrocardia27637000
- Heart in right chest27637000
- Right sided heart27637000
- Bronchiectasis, chronic sinusitis AND dextrocardia syndrome42402006
- Kartagener syndrome42402006
- Kartageners syndrome42402006
- Siewert syndrome42402006
- Situs inversus43876007
- Situs inversus viscerum43876007
- Visceral inversion43876007
- Abdominal transposition68716001
- Situs inversus abdominalis68716001
- Transposition of abdominal organs68716001
- Transposition of abdominal viscera68716001
- Situs inversus thoracis70978004
- Transposition of thoracic organs70978004
- Transposition of thoracic viscera70978004
- Dextrocardia/situs inversus finding85090007
- Dysmotile cilia syndrome86204009
- ICS - Immotile cilia syndrome86204009
- Immotile cilia syndrome86204009
- PCD - Primary ciliary dyskinesia86204009
- Polynesian bronchiectasis86204009
- Primary ciliary dyskinesia86204009
- Complete situs inversus with dextrocardia205768003
- Isolated laevocardia205769006
- Isolated levocardia205769006
- Laevocardia205769006
- Levocardia205769006
- Situs inversus with laevocardia205769006
- Situs inversus with levocardia205769006
- Agnathia, holoprosencephaly, situs inversus syndrome722283003
- Atrial situs inversus871616009
UMLS
- Abdominal situs inversusC0037221
- Complete transpositionC0037221
- Complete transposition (morphologic abnormality)C0037221
- Inversus, SitusC0037221
- Situs InversusC0037221
- Situs Inversus ViscerumC0037221
- Situs inversusC0037221
- Situs inversus visceralisC0037221
- Situs inversus viscerumC0037221
- Situs inversus viscerum (disorder)C0037221
- Situs transversusC0037221
- Visceral inversionC0037221
- inversus situsC0037221
- situs inversusC0037221
- situs transversusC0037221
- situs viscerum inversusC0037221
- Abdominal transpositionC0266644
- Situs abdominalis inversusC0266644
- Situs inversus abdominalisC0266644
- Situs inversus abdominalis (disorder)C0266644
- Situs inversus or transversus abdominalisC0266644
- Transposition of abdominal organsC0266644
- Transposition of abdominal visceraC0266644
- Dextrocardia with situs inversusC1395317
- Mirror-image atrial arrangement with situs inversusC2910351
- Situs Inversus ThoracisC0266645
- Situs inversus or transversus thoracisC0266645
- Situs inversus thoracisC0266645
- Situs inversus thoracis (disorder)C0266645
- Transposition of thoracic organsC0266645
- Transposition of thoracic visceraC0266645
Clinical Terms
- Heart in right chest
- Levocardia
- Complete transposition
- Transposition of abdominal viscera
- Transposition of thoracic viscera
- Situs inversus viscerum
- Isomerism sequence
- Kartageners syndrome
- situs viscerum inversus
- Congenital abnormality of cardiac position
- Congenital malpositioned heart
- Immotile cilia syndrome
- Situs inversus with laevocardia
- Abdominal situs inversus
- Dextrocardia with situs inversus
- Primary ciliary dyskinesia
- Complete transposition (morphologic abnormality)
- Polynesian bronchiectasis
- Situs inversus with levocardia
- Mirror-image atrial arrangement with situs inversus
- Kartagener syndrome
- Dextrocardia
- Isolated laevocardia
- Congenital malposition of heart
- Isolated levocardia
- Siewert syndrome
- Situs inversus viscerum (disorder)
- ICS - Immotile cilia syndrome
- Transposition of thoracic organs
- Abnormal position of heart
- Situs inversus thoracis
- Agnathia, holoprosencephaly, situs inversus syndrome
- Situs inversus visceralis
- Right sided heart
- Bronchiectasis, chronic sinusitis AND dextrocardia syndrome
- Situs transversus
- Situs abdominalis inversus
- Laterality sequence
- PCD - Primary ciliary dyskinesia
- Situs inversus abdominalis
- Visceral inversion
- Situs inversus abdominalis (disorder)
- Dextrocardia/situs inversus finding
- Complete situs inversus with dextrocardia
- Dysmotile cilia syndrome
- Situs inversus or transversus abdominalis
- Abdominal transposition
- Inversus, Situs
- Situs inversus thoracis (disorder)
- Situs inversus or transversus thoracis
- inversus situs
- Atrial situs inversus
- Laevocardia
- Transposition of abdominal organs
Frequently Asked Questions
What is the ICD-10 code for situs inversus?
The ICD-10-CM code for situs inversus is Q89.3. The full clinical description is "Situs inversus". Q89.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q89.3 mean?
ICD-10-CM code Q89.3 represents “Situs inversus”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q89.3 a billable code?
Yes, Q89.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q89.3 in?
Q89.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q89.3?
Q89.3 has Excludes1 notes indicating codes that cannot be used together with it, including: dextrocardia NOS (Q24.0).
What SNOMED CT codes does Q89.3 map to?
Q89.3 maps to 13 SNOMED CT concepts: 68716001, 10818008, 722283003, 871616009, 42402006, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q89.3?
Q89.3 is linked to 5 UMLS Concept Unique Identifiers: C0037221, C0266644, C1395317, C2910351, C0266645. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q89.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like situs inversus affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q89.3?
Q89.3 maps to the ICD-11 code: LA82 (Total mirror imagery).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.