Q89.4
BillableConjoined twins
Conjoined twins
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Craniopagus
- Dicephaly
- Pygopagus
- Thoracopagus
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
Q89.0Congenital absence and malformations of spleen
Q89.1Congenital malformations of adrenal gland
Q89.2Congenital malformations of other endocrine glands
Q89.3Situs inversus
Q89.7Multiple congenital malformations, not elsewhere classified
Q89.8Other specified congenital malformations
Q89.9Congenital malformation, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(253)
SNOMED CT
- Thoracodidymus1769008
- Anadidymus6667002
- Thoracopagus epigastricus7722005
- Dicephalus dipus tribrachius7763004
- Syncephalus8569001
- Synencephalus8569001
- Synencephaly8569001
- Catadidymus8962004
- Katadidymus8962004
- Desmiognathus15969009
- Dicephalus parasiticus15969009
- Heterodidymus16095003
- Heterodymus16095003
- Ischiopagus19179000
- Ischiopagus twins19179000
- Cephalothoracopagus21530000
- Xiphopagus24297000
- Thoracodelphus24533004
- Thoradelphus24533004
- Thoracopagus parasiticus24679000
- Pygoamorphus30248008
- Epignathus31248004
- Deradelphus35595006
- Conjoined twins with two heads38439000
- Cranial duplication38439000
- Craniodidymus38439000
- Dicephalus38439000
- Dicephaly38439000
- Monocephalus39564008
- Dicephalus tripus tribrachius41132007
- Conjoined twins41337007
- Siamese twins41337007
- Cryptodidymus43387009
- Fetus in fetu43387009
- Foetus in foetu43387009
- Parasite of asymmetrical conjoined twins46100008
- Parasitic twin of asymmetrical conjoined twins46100008
- Dicephalus dipus dibrachius46698009
- Janiceps57918009
- Janus57918009
- Synthorax59777009
- Thoracopagus59777009
- Thorax-joined twins59777009
- Anakatadidymus64490002
- Dicephalus dipygus64490002
- Craniopagus parietalis66426000
- Asymmetrical conjoined twins70013003
- Asymmetrical disomata70013003
- Heteradelphus70013003
- Heteropagus70013003
- Heteropagus twins70013003
- Unequal conjoined twins70013003
- Buttock-joined twins70642007
- Pygopagus70642007
- Dipygus71464000
- Opodidymus74307005
- Opodymus74307005
- Cephalopagus74516008
- Craniopagus74516008
- Head-joined twins74516008
- Monomphalus75617000
- Omphalopagus75617000
- Omphalopagus twins75617000
- Diplopagus76089002
- Duplicitas symmetros76089002
- Equal conjoined twins76089002
- Symmetrical conjoined twins76089002
- Symmetrical disomata76089002
- Gastrothoracopagus78728005
- Thoracogastrodidymus78728005
- Ischiomelus81307004
- Thoracoparacephalus82007007
- Pygodidymus84589003
- Dicephalus dipus tetrabrachius85445006
- Craniopagus occipitalis85630009
- Thoracomelus86280002
- Dipygus parasiticus89409002
- Gastrothoracopagus dipygus89409002
- Fetal neoplasm127332000
- Foetal neoplasm127332000
- Craniopagus frontalis205771006
- Craniopagus parasiticus205774003
- Thoracopagus with separate hearts and pericardial sacs458040001
- Thoracopagus with separate hearts and common pericardial sac458041002
- Thoracopagus with conjoined atria458042009
- Thoracopagus with conjoined atriums458042009
- Thoracopagus with conjoined atria and ventricles458043004
- Thoracopagus with conjoined atriums and ventricles458043004
- Rachipagus458044005
- Parapagus458085000
- Dithoracic parapagus458086004
- Dicephalic parapagus458087008
- Polysomia723974008
- Polysomus723974008
- Fetal epignathus897278005
- Foetal epignathus897278005
- Fetal epignathus with conjoined twins897279002
- Foetal epignathus with conjoined twins897279002
- Thoracoomphalopagus1010611006
- Sternopagus1010667003
UMLS
- Buttock-joined twinsC0266711
- PygopagusC0266711
- Pygopagus (disorder)C0266711
- CephalopagusC0266692
- CraniopagusC0266692
- Craniopagus (disorder)C0266692
- Head-joined twinsC0266692
- Conjoined TwinC0041428
- Conjoined TwinsC0041428
- Conjoined twinsC0041428
- Conjoined twins (disorder)C0041428
- Siamese TwinC0041428
- Siamese TwinsC0041428
- Siamese twinsC0041428
- Twin, ConjoinedC0041428
- Twin, SiameseC0041428
- Twins, ConjoinedC0041428
- Twins, SiameseC0041428
- conjoin twinC0041428
- conjoined twinC0041428
- conjoined twinsC0041428
- conjoining twinsC0041428
- siamese twinC0041428
- siamese twinsC0041428
- twins conjoinedC0041428
- twins siameseC0041428
- Conjoined twins with two headsC0266674
- Cranial duplicationC0266674
- Cranial duplication (disorder)C0266674
- CraniodidymusC0266674
- DicephalusC0266674
- DicephalyC0266674
- SynthoraxC0266704
- ThoracopagusC0266704
- Thoracopagus (disorder)C0266704
- Thorax-joined twinsC0266704
- thoracopagusC0266704
- thoracopagus twinsC0266704
Clinical Terms
- Siamese Twins
- Craniopagus
- conjoining twins
- Anadidymus
- Cephalopagus
- twins conjoined
- Thoracodidymus
- Craniopagus parietalis
- Monocephalus
- Thoracopagus with conjoined atria and ventricles
- Janus
- Fetal epignathus with conjoined twins
- Parapagus
- Ischiopagus twins
- Heteropagus
- Thoracopagus parasiticus
- Twins, Siamese
- Dicephalus dipus tribrachius
- Foetal epignathus with conjoined twins
- Conjoined twins with two heads
- Polysomus
- Thoracoparacephalus
- Thoradelphus
- Fetus in fetu
- Gastrothoracopagus dipygus
- Foetal neoplasm
- Gastrothoracopagus
- Janiceps
- conjoined twin
- Deradelphus
- Monomphalus
- Head-joined twins
- Thoracopagus with conjoined atriums
- Craniopagus parasiticus
- Desmiognathus
- Dipygus
- Heterodidymus
- Thoracopagus with conjoined atria
- Dipygus parasiticus
- Equal conjoined twins
- Dicephalus dipus dibrachius
- Opodymus
- Pygoamorphus
- Twins, Conjoined
- Thoracogastrodidymus
- Thoracopagus with conjoined atriums and ventricles
- Asymmetrical disomata
- Heteradelphus
- Ischiomelus
- Thoracopagus with separate hearts and common pericardial sac
- Heterodymus
- Thoracopagus with separate hearts and pericardial sacs
- Omphalopagus
- Dicephalus dipus tetrabrachius
- Dithoracic parapagus
- Fetal neoplasm
- Dicephalus parasiticus
- Duplicitas symmetros
- Diplopagus
- Cephalothoracopagus
- Craniopagus frontalis
- thoracopagus twins
- Epignathus
- Synencephaly
- Foetal epignathus
- Thoracodelphus
- Thorax-joined twins
- Sternopagus
- siamese twin
- Asymmetrical conjoined twins
- Pygopagus (disorder)
- Symmetrical disomata
- Craniopagus (disorder)
- Thoracopagus (disorder)
- twins siamese
- Anakatadidymus
- Cryptodidymus
- Thoracopagus epigastricus
- Craniodidymus
- Twin, Siamese
- Parasite of asymmetrical conjoined twins
- Foetus in foetu
- Ischiopagus
- Symmetrical conjoined twins
- Thoracopagus
- Fetal epignathus
- Opodidymus
- Parasitic twin of asymmetrical conjoined twins
- Conjoined twins (disorder)
- Unequal conjoined twins
- Twin, Conjoined
- Cranial duplication (disorder)
- Dicephalic parapagus
- Rachipagus
- conjoin twin
- Thoracoomphalopagus
- Omphalopagus twins
- Dicephalus
- Synthorax
- Pygodidymus
- Polysomia
- Synencephalus
- Syncephalus
- Craniopagus occipitalis
- Xiphopagus
- Pygopagus
- Thoracomelus
- Cranial duplication
- Heteropagus twins
- Dicephaly
- Catadidymus
- Buttock-joined twins
- Dicephalus dipygus
- Katadidymus
- Dicephalus tripus tribrachius
Frequently Asked Questions
What is the ICD-10 code for conjoined twins?
The ICD-10-CM code for conjoined twins is Q89.4. The full clinical description is "Conjoined twins". Q89.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q89.4 mean?
ICD-10-CM code Q89.4 represents “Conjoined twins”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q89.4 a billable code?
Yes, Q89.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q89.4 in?
Q89.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q89.4 map to?
Q89.4 maps to 58 SNOMED CT concepts: 6667002, 64490002, 70013003, 70642007, 8962004, and 53 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q89.4?
Q89.4 is linked to 5 UMLS Concept Unique Identifiers: C0266711, C0266692, C0041428, C0266674, C0266704. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q89.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like conjoined twins affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q89.4?
Q89.4 maps to the ICD-11 code: LD2G (Conjoined twins).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.