Q82.2
BillableCongenital cutaneous mastocytosis
Congenital cutaneous mastocytosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital diffuse cutaneous mastocytosis
- Congenital maculopapular cutaneous mastocytosis
- Congenital urticaria pigmentosa
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •acrodermatitis enteropathicaE83.2
- •congenital erythropoietic porphyriaE80.0
- •pilonidal cyst or sinusL05
- •Sturge-Weber (-Dimitri) syndromeQ85.89
- •cutaneous mastocytosis NOSD47.01
- •diffuse cutaneous mastocytosis (with onset after newborn period)D47.01
- •malignant mastocytosisC96.2
- •systemic mastocytosisD47.02
- •urticaria pigmentosa (non-congenital) (with onset after newborn period)D47.01
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q82.0Hereditary lymphedema
Q82.1Xeroderma pigmentosum
Q82.3Incontinentia pigmenti
Q82.4Ectodermal dysplasia (anhidrotic)
Q82.5Congenital non-neoplastic nevus
Q82.6Congenital sacral dimple
Q82.8Other specified congenital malformations of skin
Q82.9Congenital malformation of skin, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(14)
SNOMED CT
UMLS
Clinical Terms
- Congenital cutaneous mastocytosis (disorder)
- Congenital maculopapular cutaneous mastocytosis
- Bullous diffuse cutaneous mastocytosis
- Congenital urticaria pigmentosa
- Congenital diffuse cutaneous mastocytosis
- Bullous eruption
Frequently Asked Questions
What is the ICD-10 code for congenital cutaneous mastocytosis?
The ICD-10-CM code for congenital cutaneous mastocytosis is Q82.2. The full clinical description is "Congenital cutaneous mastocytosis". Q82.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q82.2 mean?
ICD-10-CM code Q82.2 represents “Congenital cutaneous mastocytosis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q82.2 a billable code?
Yes, Q82.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q82.2 in?
Q82.2 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q82.2?
Q82.2 has Excludes1 notes indicating codes that cannot be used together with it, including: acrodermatitis enteropathica (E83.2); congenital erythropoietic porphyria (E80.0); pilonidal cyst or sinus (L05.-); and 6 more.
What SNOMED CT codes does Q82.2 map to?
Q82.2 maps to 3 SNOMED CT concepts: 1148891004, 271759003, 16833831000119106. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q82.2?
Q82.2 is linked to 4 UMLS Concept Unique Identifiers: C5779617, C4509433, C4509595, C4509434. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q82.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital cutaneous mastocytosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q82.2?
Q82.2 maps to the ICD-11 code: 2A21.Z (Mastocytosis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.