D47.01
BillableCutaneous mastocytosis
Cutaneous mastocytosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(2)
Also Known As / Clinical Terms(141)
SNOMED CT
- Cutaneous mastocytosis, adult form34739009
- Urticaria pigmentosa, adult form34739009
- Cutaneous mastocytosis, infantile form76621000
- Urticaria pigmentosa, infantile form76621000
- Chronic deafness232325008
- Mast cell naevus239147000
- Mast cell nevus239147000
- Mastocytoma of skin239147000
- Bullous eruption271759003
- Cutaneous mastocytosis397012002
- Cutaneous mastocytoma397013007
- Solitary cutaneous mastocytoma397013007
- Solitary mastocytoma397013007
- Diffuse erythrodermic mastocytosis397014001
- Bullous cutaneous mastocytosis404170009
- Bullous urticaria pigmentosa404170009
- Mastocytoma404171008
- Familial mastocytosis404173006
- Cutaneous mastocytosis, short stature, hearing loss syndrome722453009
- Hennekam Beemer syndrome722453009
- Bullous diffuse cutaneous mastocytosis1148891004
- Pseudoxanthomatous nodular cutaneous mastocytosis1153344009
- Maculopapular cutaneous mastocytosis1332134000
UMLS
- Cutaneous MastocytosesC1136033
- Cutaneous MastocytosisC1136033
- Cutaneous mastocytosisC1136033
- Cutaneous mastocytosis (disorder)C1136033
- Cutaneous mastocytosis (morphologic abnormality)C1136033
- MASTCC1136033
- MASTOCYTOSIS, CUTANEOUSC1136033
- Mastocytoses, CutaneousC1136033
- Mastocytoses, SkinC1136033
- Mastocytosis, CutaneousC1136033
- Mastocytosis, SkinC1136033
- Skin MastocytosesC1136033
- Skin MastocytosisC1136033
- Cutaneous Mastocytoses, DiffuseC0024901
- Cutaneous Mastocytosis, DiffuseC0024901
- DCMC0024901
- Diffuse Cutaneous MastocytosisC0024901
- Diffuse cutaneous mastocytosisC0024901
- Diffuse cutaneous mastocytosis (morphologic abnormality)C0024901
- MASTOCYTOSIS, DIFFUSE CUTANEOUSC0024901
- Mastocytosis, Diffuse CutaneousC0024901
- Cutaneous Mastocytoses, MaculopapularC0042111
- Cutaneous Mastocytosis, MaculopapularC0042111
- MASTOCYTOSIS, MACULOPAPULAR CUTANEOUSC0042111
- Maculopapular Cutaneous MastocytosesC0042111
- Maculopapular Cutaneous MastocytosisC0042111
- Maculopapular cutaneous mastocytosisC0042111
- Maculopapular cutaneous mastocytosis (disorder)C0042111
- UP/MPCMC0042111
- URTICARIA PIGMENTOSAC0042111
- Urticaria PigmentosaC0042111
- Urticaria Pigmentosa/Maculopapular Cutaneous MastocytosisC0042111
- Urticaria pigmentosaC0042111
- pigmentosa urticariaC0042111
- urticaria pigmentosaC0042111
- Cutaneous Solitary MastocytomaC0343115
- Cutaneous mastocytomaC0343115
- Isolated Cutaneous MastocytomaC0343115
- Isolated Mastocytoma of the SkinC0343115
- Mastocytoma, SkinC0343115
- Skin MastocytomaC0343115
- Skin Solitary MastocytomaC0343115
- Solitary Mastocytoma of SkinC0343115
- Solitary Mastocytoma of the SkinC0343115
- Solitary cutaneous mastocytomaC0343115
- Solitary cutaneous mastocytoma (disorder)C0343115
- Solitary mastocytomaC0343115
- Solitary mastocytoma of skinC0343115
- Solitary mastocytoma of skin (morphologic abnormality)C0343115
- Paucicellular mastocytosisC0263402
- TMEP - telangiectasia macularis eruptiva perstansC0263402
- Telangiectasia macularis eruptiva perstansC0263402
- Telangiectasia macularis eruptiva perstans (disorder)C0263402
- Telangiectasia macularis eruptive perstansC0263402
- Telangiectatic cutaneous mastocytosisC0263402
Clinical Terms
- Diffuse cutaneous mastocytosis
- Mastocytosis, Skin
- Mastocytoma
- Mastocytoma of skin
- Cutaneous mastocytosis (morphologic abnormality)
- MASTOCYTOSIS, MACULOPAPULAR CUTANEOUS
- Mastocytosis, Diffuse Cutaneous
- Diffuse erythrodermic mastocytosis
- Maculopapular cutaneous mastocytosis
- TMEP - telangiectasia macularis eruptiva perstans
- Maculopapular cutaneous mastocytosis (disorder)
- Solitary Mastocytoma of the Skin
- Cutaneous Mastocytoses, Diffuse
- Hennekam Beemer syndrome
- Telangiectasia macularis eruptiva perstans
- UP/MPCM
- Mastocytoma, Skin
- Bullous eruption
- Bullous cutaneous mastocytosis
- Maculopapular Cutaneous Mastocytoses
- MASTC
- Solitary mastocytoma of skin
- Bullous diffuse cutaneous mastocytosis
- Bullous urticaria pigmentosa
- Pseudoxanthomatous nodular cutaneous mastocytosis
- Cutaneous mastocytosis, short stature, hearing loss syndrome
- Isolated Cutaneous Mastocytoma
- Solitary mastocytoma of skin (morphologic abnormality)
- Cutaneous Mastocytosis, Maculopapular
- Telangiectasia macularis eruptive perstans
- MASTOCYTOSIS, CUTANEOUS
- urticaria pigmentosa
- Telangiectasia macularis eruptiva perstans (disorder)
- Mast cell naevus
- Mast cell nevus
- Urticaria Pigmentosa/Maculopapular Cutaneous Mastocytosis
- Chronic deafness
- Cutaneous mastocytosis, infantile form
- Skin Mastocytoma
- Solitary cutaneous mastocytoma (disorder)
- pigmentosa urticaria
- Solitary mastocytoma
- Familial mastocytosis
- Diffuse cutaneous mastocytosis (morphologic abnormality)
- Skin Mastocytoses
- Telangiectatic cutaneous mastocytosis
- Paucicellular mastocytosis
- Urticaria pigmentosa, infantile form
- Cutaneous Mastocytoses
- Solitary cutaneous mastocytoma
- Cutaneous mastocytoma
- Cutaneous mastocytosis, adult form
- DCM
- Cutaneous Solitary Mastocytoma
- Isolated Mastocytoma of the Skin
- Mastocytoses, Skin
- Skin Mastocytosis
- Urticaria pigmentosa, adult form
- Cutaneous Mastocytosis, Diffuse
- Mastocytoses, Cutaneous
- Cutaneous Mastocytoses, Maculopapular
- Skin Solitary Mastocytoma
- Cutaneous mastocytosis (disorder)
Frequently Asked Questions
What is the ICD-10 code for cutaneous mastocytosis?
The ICD-10-CM code for cutaneous mastocytosis is D47.01. The full clinical description is "Cutaneous mastocytosis". D47.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D47.01 mean?
ICD-10-CM code D47.01 represents “Cutaneous mastocytosis”. It is classified under Chapter 2: Neoplasms and is a billable/specific code that can be used on a claim.
Is D47.01 a billable code?
Yes, D47.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D47.01 in?
D47.01 is in Chapter 2: Neoplasms (codes C00-D49).
What codes cannot be used with D47.01?
D47.01 has Excludes1 notes indicating codes that cannot be used together with it, including: neoplasms of unspecified behavior (D49.-); congenital cutaneous mastocytosis (Q82.2); histiocytic neoplasms of uncertain behavior (D47.Z9); and 4 more.
What SNOMED CT codes does D47.01 map to?
D47.01 maps to 15 SNOMED CT concepts: 404170009, 1148891004, 271759003, 232325008, 397013007, and 10 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D47.01?
D47.01 is linked to 5 UMLS Concept Unique Identifiers: C1136033, C0024901, C0042111, C0343115, C0263402. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D47.01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cutaneous mastocytosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D47.01?
There is no direct ICD-11 mapping available for D47.01 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.