AutoICD API

Q85.89

Billable

Other phakomatoses, not elsewhere classified

Other phakomatoses, not elsewhere classified

Status

Billable / Specific

Parent Code

Q85.8

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(3)
Q85.81

PTEN hamartoma tumor syndrome

BillableQ85.82

Other Cowden syndrome

BillableQ85.83

Von Hippel-Lindau syndrome

Billable
Also Known As / Clinical Terms(342)

SNOMED CT

UMLS

Clinical Terms

  • Sebaceous naevus
  • Peutz Jeghers Syndrome
  • Sturge Weber Krabbe Syndrome
  • Peutz-Jeghers polyps of small bowel
  • Port-wine stain with associated anomalies
  • Phakomatosis pigmentokeratotica
  • Schirmer's syndrome
  • Syndrome, Sturge-Weber-Dimitri
  • peutz jegher syndrome
  • weber syndrome
  • Syndrome, Sturge
  • Sturge-Weber-Krabbe syndrome
  • SCALP syndrome
  • Syndrome, Sturge-Weber
  • Peutz-Jeghers Syndrome
  • peutz jeghers syndromes
  • Smooth muscle naevus
  • Encephalofacial hemangiomatosis
  • PJS - Peutz-Jeghers syndrome
  • Polyps-and-Spots Syndrome
  • Polyposis, Peutz-Jeghers
  • Sturge-Kalischer-Weber Syndrome
  • sturges syndrome weber
  • Polyps and Spots Syndrome
  • Peutz Jeghers Polyposis
  • Meningofacial Angiomatosis-Cerebral Calcification Syndrome
  • Sebaceous nevus
  • Lentiginoses, Perioral
  • Sturge Weber Syndrome
  • Hamartomatous Intestinal Polyposis
  • Angiomatosis of meninges
  • Neuroretinoangiomatosis
  • Periorificial Lentiginosis Syndrome
  • Polyposis, hamartomatous intestinal
  • Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome
  • Phakomatosis, Sturge Weber
  • Meningo Oculo Facial Angiomatosis
  • Sturge-Weber Phakomatosis
  • Nevus sebaceous of Jadassohn
  • Angiomatosis, Meningo-Oculo-Facial
  • Sturge's Syndrome
  • PJS
  • Congenital arrector pili hamartoma
  • Phakomatosis caesiomarmorata
  • Peutz's Syndrome
  • Angiomatosis oculo-orbital-thalamo-encephalic syndrome
  • Centrofacial lentiginosis syndrome
  • Peutz-Jegher's Syndrome
  • Angiomatosis aculoorbital-thalamic syndrome
  • Periorificial Lentiginosis Syndromes
  • Abnormality of canalisation and retrogressive differentiation
  • Congenital leptomeningeal angiomatosis
  • Sturge Kalischer Weber Syndrome
  • Hereditary cutaneous vascular syndrome
  • Hamartoma of muscle
  • Nevus of pilar muscle
  • Generalized basaloid follicular hamartoma syndrome
  • Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome
  • Encephalotrigeminal Syndrome
  • Intestinal Polyposes, Hamartomatous
  • Syndrome, Peutz-Jegher's
  • Peutz-Jeghers polyposis
  • Intestinal polyposis-cutaneous pigmentation syndrome
  • Rhabdomyomatous mesenchymal hamartoma
  • Gingival enlargement due to Sturge-Weber syndrome
  • Spinal hamartoma
  • Polyp of small intestine
  • neurocutaneous syndrome
  • Encephalofacial haemangiomatosis
  • Sturge-Weber Disease
  • Sturge-Weber syndrome (disorder)
  • Encephalocutaneous angiomatosis
  • sturge weber disease
  • Jeghers-Peutz Syndrome
  • Sturge Disease
  • Phakomatosis spilorosea
  • Syndromes, Periorificial Lentiginosis
  • syndrome peutz-jeghers
  • Congenital rhabdomyomatous mesenchymal hamartoma
  • Vascular neurocutaneous syndrome
  • Diffuse smooth muscle hamartoma
  • Naevus sebaceous
  • SWS
  • Congenital smooth muscle hamartoma
  • Peutz-Jeghers syndrome (disorder)
  • Hemangiomatosis Syndrome, Encephalofacial
  • Basal cell nevus with comedones
  • Hamartomatous Intestinal Polyposes
  • Peutz-Jegher Syndrome
  • Basal cell naevus with comedones
  • Congenital erector pili hamartoma
  • Polyposes, Hamartomatous Intestinal
  • Sturge-Weber syndrome
  • Sturge Syndrome
  • Syndrome, Sturge's
  • Nevus sebaceous
  • Phakomatosis pigmentovascularis
  • Perioral Lentiginosis
  • Hereditary neurocutaneous vascular malformations
  • Hamartoma of pilosebaceous apparatus
  • Hamartoma of intestine
  • Basaloid follicular hamartoma
  • Schimmelpeming Feuerstein Mims syndrome
  • Sturge-Weber-Dimitri Syndrome
  • Syndrome, Polyps-and-Spots
  • Epidermal naevus syndrome
  • Haemangioma of intracranial structure
  • Perlman syndrome
  • STURGE DIS
  • Syndrome, Sturge-Kalischer-Weber
  • syndrome webers
  • Perioral Lentiginoses
  • Lentiginosis, Perioral
  • Milles' syndrome
  • Organoid nevus
  • Centrofacial lentiginosis
  • Sturge Weber Dimitri Syndrome
  • Encephalofacial Hemangiomatosis Syndrome
  • Polyps-and-Spots Syndromes
  • Naevus sebaceous of Jadassohn
  • Encephalotrigeminal angiomatosis
  • Meningo-oculo-facial angiomatosis
  • Syndrome, Peutz-Jeghers
  • Naevus of pilar muscle
  • Abnormality of canalization and retrogressive differentiation
  • Sturge-Weber sequence
  • sturge syndrome weber
  • Peutz Jegher's Syndrome
  • Hemangioma of intracranial structure
  • Sturge-Weber(-Dimitri) syndrome
  • Syndrome, Periorificial Lentiginosis
  • Generalised basaloid follicular hamartoma syndrome
  • Phakomatosis cesiomarmorata
  • Hereditary neurocutaneous angiomata
  • Polyposis, intestinal, II
  • Intestinal Polyposis, Hamartomatous
  • Syndrome, Encephalofacial Hemangiomatosis
  • Phakomatosis, Sturge-Weber
  • Syndrome, Sturge-Weber-Krabbe
  • Syndromes, Polyps-and-Spots
  • Port-wine stain with oculocutaneous melanosis
  • webers syndrome
  • Hamartoma of small intestine
  • Organoid naevus
  • sturges weber syndrome
  • Angiomatosis Oculoorbital-Thalamic Syndrome
  • Phakomatosis cesioflammea
  • Epidermal nevus syndrome
  • Smooth muscle nevus
Frequently Asked Questions
What is the ICD-10 code for other phakomatoses, not elsewhere classified?

The ICD-10-CM code for other phakomatoses, not elsewhere classified is Q85.89. The full clinical description is "Other phakomatoses, not elsewhere classified". Q85.89 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q85.89 mean?

ICD-10-CM code Q85.89 represents “Other phakomatoses, not elsewhere classified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q85.89 a billable code?

Yes, Q85.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q85.89 in?

Q85.89 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q85.89?

Q85.89 has Excludes1 notes indicating codes that cannot be used together with it, including: ataxia telangiectasia [Louis-Bar] (G11.3); familial dysautonomia [Riley-Day] (G90.1); Meckel-Gruber syndrome (Q61.9).

What SNOMED CT codes does Q85.89 map to?

Q85.89 maps to 34 SNOMED CT concepts: 253188000, 19886006, 445135003, 254705003, 18822004, and 29 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q85.89?

Q85.89 is linked to 3 UMLS Concept Unique Identifiers: C0038505, C0031269, C0869082. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q85.89 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other phakomatoses, not elsewhere classified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q85.89?

There is no direct ICD-11 mapping available for Q85.89 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.