G11.3
BillableCerebellar ataxia with defective DNA repair
Cerebellar ataxia with defective DNA repair
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Ataxia telangiectasia [Louis-Bar]
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •cerebral palsyG80
- •hereditary and idiopathic neuropathyG60
- •metabolic disordersE70-E88
- •Cockayne's syndromeQ87.19
- •other disorders of purine and pyrimidine metabolismE79
- •xeroderma pigmentosumQ82.1
Related Codes(8)
G11.0Congenital nonprogressive ataxia
G11.1Early-onset cerebellar ataxia
G11.2Late-onset cerebellar ataxia
G11.4Hereditary spastic paraplegia
G11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6Leukodystrophy with vanishing white matter disease
G11.8Other hereditary ataxias
G11.9Hereditary ataxia, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(24)
SNOMED CT
- Ataxia telangiectasia68504005
- Ataxia telangiectasia syndrome68504005
- Ataxia-telangiectasia syndrome68504005
- Louis-Bar syndrome68504005
- Ataxia telangiectasia variant763065008
- v-AT - ataxia telangiectasia variant763065008
- Chorea due to immunological disorder1259621007
- Chorea due to ataxia telangiectasia syndrome1259708007
- Dystonia due to ataxia telangiectasia syndrome1260334009
- Dystonia due to ataxia-telangiectasia syndrome1260334009
UMLS
Clinical Terms
- Chorea due to immunological disorder
- Ataxia telangiectasia syndrome
- Dystonia due to ataxia-telangiectasia syndrome
- Chorea due to ataxia telangiectasia syndrome
- Ataxia telangiectasia [Louis-Bar]
- Louis-Bar syndrome
- Ataxia-telangiectasia syndrome
- Dystonia due to ataxia telangiectasia syndrome
- Ataxia telangiectasia variant
- v-AT - ataxia telangiectasia variant
- Ataxia telangiectasia
Frequently Asked Questions
What is the ICD-10 code for cerebellar ataxia with defective dna repair?
The ICD-10-CM code for cerebellar ataxia with defective dna repair is G11.3. The full clinical description is "Cerebellar ataxia with defective DNA repair". G11.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G11.3 mean?
ICD-10-CM code G11.3 represents “Cerebellar ataxia with defective DNA repair”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G11.3 a billable code?
Yes, G11.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G11.3 in?
G11.3 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G11.3 map to?
G11.3 maps to 5 SNOMED CT concepts: 68504005, 763065008, 1259708007, 1259621007, 1260334009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G11.3?
G11.3 is linked to 2 UMLS Concept Unique Identifiers: C2875047, C0494451. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G11.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cerebellar ataxia with defective dna repair affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G11.3?
G11.3 maps to the ICD-11 code: 8A03.Z (Ataxic disorders, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.