AutoICD API

G11.4

Billable

Hereditary spastic paraplegia

Hereditary spastic paraplegia

Status

Billable / Specific

Block

G10-G14

Parent Code

G11

ICD-11 Mapping

1 equivalent

Coding Notes

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
G11.0

Congenital nonprogressive ataxia

BillableG11.1

Early-onset cerebellar ataxia

G11.2

Late-onset cerebellar ataxia

BillableG11.3

Cerebellar ataxia with defective DNA repair

BillableG11.5

Hypomyelination - hypogonadotropic hypogonadism - hypodontia

BillableG11.6

Leukodystrophy with vanishing white matter disease

BillableG11.8

Other hereditary ataxias

BillableG11.9

Hereditary ataxia, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

8B44.0ZHereditary spastic paraplegia, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(449)

SNOMED CT

UMLS

Clinical Terms

  • Autosomal dominant spastic paraplegia type 19
  • X-linked pure hereditary spastic paraplegia
  • Autosomal recessive spastic ataxia of Charlevoix-Saguenay
  • Autosomal recessive spastic paraplegia type 77
  • Severe intellectual disability and progressive spastic paraplegia
  • Kjellin syndrome
  • Maternally-inherited spastic paraplegia
  • Silver disease
  • Paraplegia, Spastic, Hereditary
  • Autosomal dominant hereditary spastic paraplegia
  • Autosomal recessive spastic paraplegia type 9B
  • Spinocerebellar degeneration co-occurrent with macular corneal dystrophy
  • Autosomal recessive spastic paraplegia type 28
  • Spastic paraplegia with Paget disease of bone syndrome
  • Ataxia of bilateral lower limbs
  • Autosomal dominant spastic paraplegia type 42
  • Autosomal recessive spastic ataxia type 5
  • Autosomal recessive spastic ataxia type 4
  • PMA - Progressive muscular atrophy
  • Dystonia 9
  • Autosomal dominant spastic paraplegia type 37
  • Autosomal recessive spastic paraplegia type 48
  • Spastic paraparesis, amyotrophy, cataracts, gastroesophageal reflux syndrome
  • Spastic paraplegia type 7
  • SPAX1 - autosomal dominant spastic ataxia type 1
  • Spastic ataxia, dysarthria due to glutaminase deficiency
  • Autosomal dominant spastic paraplegia type 9B
  • X-linked hereditary spastic paraplegia
  • Spastic paraplegia, optic atrophy, neuropathy syndrome
  • Autosomal recessive spastic paraplegia type 26
  • Autosomal recessive spastic paraplegia type 62
  • Spastic paraparesis co-occurrent with deafness
  • Dystonia due to hereditary spastic paraplegia
  • IAHSP - infantile onset ascending hereditary spastic paralysis
  • Paraplegias, Hereditary Spastic
  • Kyphoscoliosis, lateral tongue atrophy, hereditary spastic paraplegia syndrome
  • SPAX3 - autosomal recessive spastic ataxia type 3
  • Wells Jankovic syndrome
  • Autosomal dominant spastic paraplegia type 13
  • Autosomal recessive spastic ataxia with leukoencephalopathy
  • Chronic deafness
  • Autosomal recessive hereditary spastic paraplegia
  • Motor neuron disease due to hereditary spastic paraplegia
  • Ataxia of bilateral lower extremities
  • Paroxysmal choreoathetosis
  • Autosomal recessive spastic paraplegia type 32
  • Hereditary spastic paraparesis type 15
  • Autosomal recessive spastic paraplegia type 11
  • Ataxia of both lower limbs
  • Autosomal recessive spastic paraplegia type 78
  • Distal spinal muscular atrophy
  • Nakamura Osame syndrome
  • Second cranial nerve finding
  • Autosomal dominant spastic paraplegia type 8
  • Strumpell disease
  • Autosomal recessive spastic paraplegia type 63
  • Spastic Paraplegia, Hereditary
  • Progressive muscular atrophy
  • Autosomal dominant familial spastic paraplegia type 3
  • AFG3L2 (AFG3 like matrix AAA peptidase subunit 2) related spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Hereditary sensory and autonomic neuropathy with spastic paraplegia
  • Disorder of glutamine metabolism
  • Parkinsonism due to heredodegenerative disorder
  • Autosomal dominant spastic paraplegia type 12
  • Parkinsonism due to hereditary spastic paraplegia
  • Bahemuka Brown syndrome
  • Autosomal dominant spastic paraplegia type 38
  • Autosomal recessive spastic paraplegia type 23
  • SPPRS (spastic paraplegia, psychomotor retardation, seizures) syndrome
  • Autosomal recessive spastic paraplegia type 59
  • Autosomal recessive spastic paraplegia type 27
  • Autosomal recessive spastic paraplegia type 74
  • Hereditary Spastic Paraplegias
  • Pure progressive muscular atrophy
  • spastic paraplegia hereditary
  • Autosomal dominant spastic ataxia type 7
  • Miotic pupil
  • Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
  • Spastic Paraplegia Hypertrophic Motor Sensory Neuropathy
  • Autosomal recessive spastic paraplegia type 71
  • SPOAN (spastic paraplegia, optic atrophy, neuropathy) syndrome
  • Pupil constriction
  • Autosomal recessive spastic paraplegia type 61
  • ARSAL - autosomal recessive spastic ataxia with leucoencephalopathy
  • AFG3L2-related spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Familial spastic paraplegia syndrome
  • SPAX 4 - autosomal recessive spastic ataxia type 4
  • Spastic paraplegia, facial cutaneous lesion syndrome
  • Autosomal dominant spastic paraplegia type 36
  • Macrocephaly with spastic paraplegia and dysmorphism syndrome
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal recessive spastic paraplegia type 24
  • Spastic paraplegia type 2
  • Autosomal recessive spastic paraplegia type 46
  • Spastic paraparesis, cataracts, speech delay syndrome
  • Autosomal dominant spastic paraplegia type 41
  • Autosomal recessive spastic ataxia with leucoencephalopathy
  • Spastic congenital paraplegia
  • Ataxia of left and right lower limbs
  • Autosomal dominant spastic paraplegia type 17
  • Autosomal recessive spastic paraplegia type 70
  • Palmoplantar keratoderma, spastic paralysis syndrome
  • Spastic paraparesis
  • Spastic ataxia with congenital miosis
  • Autosomal recessive spastic paraplegia type 58
  • Autosomal recessive spastic paraplegia type 44
  • Hypertrophic Motor Sensory Neuropathy Spastic Paraplegia
  • Autosomal recessive spastic paraplegia type 14
  • Autosomal recessive spastic ataxia type 3
  • Hypertrophic Motor-Sensory Neuropathy-Spastic Paraplegia
  • Autosomal recessive spastic paraplegia type 55
  • Autosomal recessive spastic paraplegia type 76
  • Spastic paraplegia due to NTE (neuropathy target esterase) mutation
  • Spastic paraplegia due to neuropathy target esterase mutation
  • Autosomal dominant spastic paraplegia type 73
  • Autosomal recessive spastic paraplegia type 54
  • MT-ATP6-related mitochondrial spastic paraplegia
  • Powell Venencie Gordon syndrome
  • Complicated hereditary spastic paraplegia
  • Autosomal recessive spastic paraplegia type 64
  • SINO syndrome
  • Autosomal dominant spastic paraplegia type 3
  • Autosomal recessive spastic paraplegia type 67
  • Miosis
  • Autosomal recessive spastic paraplegia type 66
  • Autosomal recessive spastic paraplegia type 69
  • Spastic paraplegia, intellectual disability and thin corpus callosum
  • X-linked spastic paraplegia type 34
  • Autosomal recessive spastic paraplegia type 15
  • Spastic paraplegia due to partial TFG deficiency
  • X-linked complex hereditary spastic paraplegia
  • Spastic paraparesis and deafness
  • Mast syndrome
  • Spastic paraparesis, vitiligo, premature greying, characteristic facies syndrome
  • Duchenne-Aran muscular atrophy
  • Cataracts, motor neuropathy, short stature, skeletal anomalies syndrome
  • SPG78 - autosomal recessive spastic paraplegia type 78
  • Autosomal recessive spastic paraplegia disc herniation syndrome
  • Autosomal recessive spastic paraplegia type 39
  • Autosomal dominant spastic paraplegia type 9A
  • Autosomal dominant spastic paraplegia type 6
  • Autosomal dominant spastic paraplegia type 10
  • Spastic gait type 2
  • Autosomal recessive spastic paraplegia type 5A
  • Autosomal dominant spastic paraplegia type 31
  • Disturbance of glutamine metabolism
  • Small pupil
  • Autosomal recessive spastic paraplegia type 18
  • Antinolo Nieto Borrego syndrome
  • Autosomal dominant complex hereditary spastic paraplegia
  • Paroxysmal dystonia
  • Punctate palmoplantar keratoderma
  • Spastic paraplegia, retinal degeneration syndrome
  • AP4 deficiency syndrome
  • Pure hereditary spastic paraplegia
  • Autosomal recessive spastic paraplegia type 25
  • Autosomal recessive cerebellar ataxia with late-onset spasticity
  • Autosomal recessive spastic paraplegia type 35
  • Bedouin spastic ataxia syndrome
  • Spastic Paraplegias, Hereditary
  • Spastic paraplegia, nephritis, deafness syndrome
  • X-linked spastic paraplegia type 2
  • Strumpell-Lorrain disease
  • Spastic paraplegia, glaucoma, intellectual disability syndrome
  • Autosomal spastic paraplegia type 72
  • Autosomal recessive cerebellar ataxia due to GBA2 (glucosylceramidase beta 2) deficiency
  • Autosomal spastic paraplegia type 30
  • Spastic paraplegia, severe developmental delay, epilepsy syndrome
  • Spastic paraparesis, amyotrophy, cataracts, gastro-oesophageal reflux syndrome
  • Spastic paraplegia, optic atrophy, neuropathy and spastic paraplegia, optic atrophy neuropathy-related disorder
  • X-linked spastic paraplegia type 16
  • Early-onset progressive encephalopathy, spastic ataxia, distal spinal muscular atrophy syndrome
  • Mousa-Al Din-Al Nassar syndrome
  • Spastic paraparesis, vitiligo, premature graying, characteristic facies syndrome
  • Fitzsimmons Walson Mellor syndrome
  • Autosomal recessive spastic ataxia type 2
  • GM2 synthase deficiency
  • Infantile ascending hereditary spastic paralysis
  • HSP - Hereditary spastic paraplegia
  • Autosomal recessive spastic paraplegia type 53
  • Autosomal recessive spastic paraplegia type 45
  • MT-ATP6 mitochondrial disease
  • ARSACS - autosomal recessive spastic ataxia of Charlevoix-Saguenay
  • SPOAN and SPOAN-related disorder
  • Autosomal recessive spastic paraplegia type 57
  • Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
  • Congenital miosis
  • ARSAL - autosomal recessive spastic ataxia with leukoencephalopathy
  • Spastic paraparesis type 2
  • Autosomal dominant spastic ataxia type 1
  • Fatty acyl-CoA reductase 1 superactivity
  • Choreoathetosis
  • Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial disease
  • Paraplegia, Hereditary Spastic
  • Autosomal dominant spastic paraplegia type 29
  • Spastic Paraplegia-Hypertrophic Motor-Sensory Neuropathy
  • Constricted pupil
  • Hereditary spastic paraplegia (disorder)
  • Spastic ataxia and corneal dystrophy
  • Early-onset spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Autosomal recessive spastic paraplegia type 21
  • Lison syndrome
  • Autosomal recessive spastic paraplegia type 43
  • Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial spastic paraplegia
  • Infantile-onset ascending hereditary spastic paralysis
  • Autosomal dominant spastic paraplegia type 4
  • Autosomal recessive spastic paraplegia type 56
  • Spastic paraplegia, intellectual disability, nystagmus, obesity syndrome
  • Paroxysmal dyskinesia
  • Bilateral lower limb ataxia
  • HSAN (hereditary sensory and autonomic neuropathy) with spastic paraplegia
  • Spastic paraplegia with precocious puberty syndrome
  • Optic nerve finding
  • Autosomal recessive spastic paraplegia type 75
  • Spastic ataxia of Charlevoix-Saguenay
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Fryns macrocephaly
  • Autosomal recessive spastic paraplegia type 60
  • Autosomal recessive complex spastic paraplegia due to Kennedy pathway dysfunction
  • Macular corneal dystrophy
Frequently Asked Questions
What is the ICD-10 code for hereditary spastic paraplegia?

The ICD-10-CM code for hereditary spastic paraplegia is G11.4. The full clinical description is "Hereditary spastic paraplegia". G11.4 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code G11.4 mean?

ICD-10-CM code G11.4 represents “Hereditary spastic paraplegia”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.

Is G11.4 a billable code?

Yes, G11.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is G11.4 in?

G11.4 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).

What SNOMED CT codes does G11.4 map to?

G11.4 maps to 128 SNOMED CT concepts: 771469002, 778011005, 702445005, 784343003, 763402002, and 123 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for G11.4?

G11.4 is linked to 1 UMLS Concept Unique Identifier: C0037773. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does G11.4 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary spastic paraplegia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of G11.4?

G11.4 maps to the ICD-11 code: 8B44.0Z (Hereditary spastic paraplegia, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.