Cutaneous syndrome with ichthyosis
Autosomal recessive cerebellar ataxia with oculomotor apraxia type 1
SCAR16 - spinocerebellar ataxia autosomal recessive type 16
Hereditary Cerebellar Ataxia
Cerebellar ataxia and ectodermal dysplasia
Progressive cerebellar ataxia
Conorenal syndrome
Dystonia 9
Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to RUBCN deficiency
Autosomal recessive spinocerebellar ataxia type 9
Marie Cerebellar Ataxia
Autosomal recessive cerebellar ataxia due to STUB1 deficiency
Autosomal recessive ataxia with oculomotor apraxia type 1
Ataxia due to mitochondrial mutations
Narcolepsy
Usher syndrome
Chronic deafness
Primary progressive cerebellar degeneration
Ichthyosis, cerebellar degeneration and hepatosplenomegaly
Paroxysmal choreoathetosis
Gemignani syndrome
Saldino-Mainzer dysplasia
Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to TUD deficiency
Primary cerebellar degeneration
Autosomal recessive cerebellar ataxia-epilepsy-intellectual disability syndrome due to RUBCN (RUN and cysteine rich domain containing beclin 1 interacting protein) deficiency
Cerebellar ataxia associated with another disorder
Ataxia with deafness and intellectual disability syndrome
Hereditary cerebellar atrophy
Neurodevelopmental delay, hypotonia, cerebellar ataxia, cardiac conduction defects syndrome
ARCA2 - autosomal recessive cerebellar ataxia type 2
Retinitis pigmentosa-deafness-ataxia syndrome
Salih ataxia
Cerebellar Ataxia, Marie's
Hereditary ataxia NOS
Autosomal recessive spinocerebellar ataxia type 15
familial cerebellar ataxia
Cerebellar Ataxia, Marie
SCA47 - spinocerebellar ataxia type 47
Hereditary cerebellar degeneration (disorder)
CAPOS (cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss) syndrome
Chorea due to hereditary ataxia
Cerebellar ataxia with oculomotor apraxia type 4
Spinocerebellar ataxia autosomal recessive type 16
X-linked progressive cerebellar ataxia
Hereditary cerebellar degeneration
Paroxysmal sleep
PUM1-associated developmental disability, ataxia, seizure syndrome
EAST (epilepsy, ataxia, sensorineural deafness, and tubulopathy) syndrome
SESAME syndrome
Episodic ataxia type 7
Hereditary cerebellar disease
Marie's cerebellar ataxia (disorder)
Optic atrophy, ataxia, peripheral neuropathy, global developmental delay syndrome
Cerebellar ataxia, brain abnormalities, cardiac conduction defects syndrome
Non-progressive cerebellar ataxia
Cerebral ataxia
AOA2 - ataxia oculomotor apraxia type 2
AOA4 - ataxia, oculomotor apraxia type 4
Cerebellar ataxia
Paroxysmal dystonia
PADDAS syndrome
Spinocerebellar ataxia, amyotrophy, deafness syndrome
Marie's cerebellar ataxia
Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
Ataxia oculomotor apraxia type 1
Narcoleptic syndrome
Autosomal recessive ataxia due to coenzyme Q10 deficiency
Myoclonus, cerebellar ataxia, deafness syndrome
AOA1 (ataxia oculomotor apraxia type 1)
Infantile cerebellar and retinal degeneration
Usher's syndrome
Neurodevelopmental delay, hypotonia, cerebellar atrophy, cardiac conduction defects syndrome
Spinocerebellar ataxia with axonal neuropathy type 2
Ataxia with tapetoretinal degeneration syndrome
Autosomal recessive cerebellar ataxia due to STUB1 (STIP1 homology and U-box containing protein 1) deficiency
Hereditary cerebellar syndrome
Cerebellar ataxia with hypogonadism and choroidal dystrophy syndrome
Cerebellar ataxia co-occurrent with ectodermal dysplasia
Retinal pigment epithelial dystrophy
Autosomal recessive ataxia due to ubiquinone deficiency
Renal dysplasia, retinal pigmentary dystrophy, cerebellar ataxia, skeletal dysplasia syndrome
Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
Reardon Baraitser syndrome
Episodic ataxia
Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
Hereditary choroidal atrophy
Autosomal recessive cerebellar ataxia due to STIP1 homology and U-box containing protein 1 deficiency
Autosomal recessive cerebellar ataxia with oculomotor apraxia type 2
Spinocerebellar disease
Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
Boucher Neuhäuser syndrome
Posthemiplegic ataxia
marie's ataxia
Choreoathetosis
Pumilio RNA binding family member 1-associated developmental disability, ataxia, seizure syndrome
SCAR23 - spinocerebellar ataxia autosomal recessive type 23
Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
Fragile X associated tremor ataxia syndrome
Hereditary cerebellar ataxia NOS
Holmes' disease
Spinocerebellar ataxia autosomal recessive type 23
Primary hypersomnia
SCAR15 - autosomal recessive spinocerebellar ataxia type 15
SCAR1 - spinocerebellar ataxia autosomal recessive 1
Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to RUN and cysteine rich domain containing beclin 1 interacting protein deficiency
Hereditary choroidal dystrophy
SESAME (seizures, sensorineural deafness, ataxia, mental retardation, electrolyte imbalance) syndrome
Paroxysmal dyskinesia
Gelineau's syndrome
Hallgren's syndrome
Retinitis pigmentosa-deafness syndrome
Congenital cataract with ataxia and deafness syndrome

Frequently Asked Questions

What is the ICD-10 code for hereditary ataxia, unspecified?

The ICD-10-CM code for hereditary ataxia, unspecified is G11.9. The full clinical description is "Hereditary ataxia, unspecified". G11.9 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code G11.9 mean?

ICD-10-CM code G11.9 represents “Hereditary ataxia, unspecified”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.

Is G11.9 a billable code?

Yes, G11.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is G11.9 in?

G11.9 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).

What SNOMED CT codes does G11.9 map to?

G11.9 maps to 54 SNOMED CT concepts: 715366004, 725408001, 1217230002, 725394006, 722967008, and 49 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for G11.9?

G11.9 is linked to 5 UMLS Concept Unique Identifiers: C0270749, C5779602, C0270752, C2875048, C2875049. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does G11.9 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary ataxia, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of G11.9?

G11.9 maps to the ICD-11 code: 8A03.Z (Ataxic disorders, unspecified).

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try Free View API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.