G11.8
BillableOther hereditary ataxias
Other hereditary ataxias
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •cerebral palsyG80
- •hereditary and idiopathic neuropathyG60
- •metabolic disordersE70-E88
Related Codes(8)
G11.0Congenital nonprogressive ataxia
G11.1Early-onset cerebellar ataxia
G11.2Late-onset cerebellar ataxia
G11.3Cerebellar ataxia with defective DNA repair
G11.4Hereditary spastic paraplegia
G11.5Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6Leukodystrophy with vanishing white matter disease
G11.9Hereditary ataxia, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(330)
SNOMED CT
- Delayed dentition5639000
- Delayed eruption of tooth5639000
- Delayed tooth eruption5639000
- Late tooth eruption5639000
- Sanger-Brown cerebellar ataxia37960002
- Early familial cerebellar degeneration syndrome45897005
- Jervis' syndrome45897005
- Bailey-Cushing syndrome60146005
- Cerebellar midline syndrome60146005
- Oculomotor nerve finding106153001
- Third cranial nerve finding106153001
- ALF - Acute liver failure197270009
- Acute hepatic failure197270009
- Acute liver failure197270009
- Slow to talk229721007
- Speech delay229721007
- Abnormal saccadic eye movement246767003
- Dysmetric ataxia246767003
- Truncal ataxia250067008
- Congenital non-progressive ataxia278509004
- Finding of intelligibility of articulation289193001
- Observation of clarity of speech289193001
- Observation of intelligibility of articulation289193001
- Observation of intelligibility of speech289193001
- Unintelligible articulation289194007
- Unintelligible speech289194007
- Clipped speech289195008
- Scamping speech289195008
- Slurred speech289195008
- Slurring289195008
- Episodic ataxia type 2420932006
- Episodic ataxia type 2 (EA2)420932006
- Episodic ataxia type 1421182009
- Episodic ataxia type 1 (EA1)421182009
- Episodic ataxia421455009
- Arts syndrome702441001
- Fatal X-linked ataxia with deafness and loss of vision702441001
- Lethal ataxia-deafness-optic atrophy702441001
- Asidan ataxia711158005
- Costa de Morte ataxia711158005
- Spinocerebellar ataxia 36711158005
- Spinocerebellar ataxia type 36711158005
- Autosomal recessive cerebelloparenchymal disorder type 3715369006
- Cerebelloparenchymal disorder III715369006
- SCAR2 (spinocerebellar ataxia autosomal recessive 2)715369006
- Richards-Rundle syndrome715415005
- Ataxia with pigmentary retinopathy715726000
- Cerebellar syndrome pigmentary maculopathy715726000
- Spinocerebellar ataxia type 7715726000
- Spinocerebellar ataxia type 1715748006
- Spinocerebellar ataxia type 2715751004
- Spinocerebellar ataxia type 6715752006
- Spinocerebellar ataxia type 8715753001
- Spinocerebellar ataxia type 10715754007
- Spinocerebellar ataxia type 4715755008
- Spinocerebellar ataxia type 28715824008
- Congenital nonprogressive spinocerebellar ataxia715825009
- Spinocerebellar ataxia type 29715825009
- Spinocerebellar ataxia type 31715826005
- Spinocerebellar ataxia type 15/16716724006
- Cayman ataxia717332007
- Cerebellar ataxia Cayman type717332007
- Episodic ataxia type 6718753002
- Episodic ataxia type 4718754008
- Periodic vestibulocerebellar ataxia718754008
- Episodic ataxia and vertigo with tinnitus and myokymia syndrome718755009
- Episodic ataxia type 3718755009
- Episodic ataxia type 5718756005
- Spinocerebellar ataxia type 26718769009
- Spinocerebellar ataxia type 25718770005
- Spinocerebellar ataxia type 20718771009
- Spinocerebellar ataxia type 23718772002
- Spinocerebellar ataxia type 21718774001
- Spinocerebellar ataxia type 11719207000
- Spinocerebellar ataxia type 12719208005
- Spinocerebellar ataxia type 13719209002
- Spinocerebellar ataxia type 14719210007
- Huntington disease-like 4719249005
- Spinocerebellar ataxia type 17719249005
- Spinocerebellar ataxia type 18719250005
- Spinocerebellar ataxia type 19719251009
- Spinocerebellar ataxia type 27719252002
- Spinocerebellar ataxia type 30719253007
- Spinocerebellar ataxia type 32719254001
- Erythrokeratodermia with ataxia719255000
- Spinocerebellar ataxia and erythrokeratodermia719255000
- Spinocerebellar ataxia type 34719255000
- Spinocerebellar ataxia type 35719300001
- Spinocerebellar ataxia type 37719301002
- Spinocerebellar ataxia with altered vertical eye movement719301002
- Spinocerebellar ataxia type 5719302009
- Congenital atrophy of optic nerve722990003
- Congenital optic atrophy722990003
- ARCA1 - autosomal recessive cerebellar ataxia type 1725433003
- Autosomal recessive cerebellar ataxia Beauce type725433003
- CAMOS (cerebellar ataxia, mental retardation, optic atrophy, skin abnormalities) syndrome726031001
- CAMOS syndrome726031001
- Cerebellar ataxia, intellectual disability, optic atrophy, skin abnormalities syndrome726031001
- SCAR5 - spinocerebellar ataxia autosomal recessive 5726031001
- Spinocerebellar ataxia dysmorphism syndrome733033001
- Spinocerebellar ataxia type 40734020000
- Spinocerebellar ataxia type 38734021001
- Autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome763312008
- Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome763344007
- Poretti Boltshauser syndrome763344007
- Ataxia, delayed dentition, hypomyelination syndrome764095005
- Leukoencephalopathy, ataxia, hypodontia, hypomyelination syndrome764095005
- Spinocerebellar ataxia with axonal neuropathy type 1765091006
- Autosomal recessive cerebellar ataxia with saccadic intrusion syndrome766814006
- Ataxia pancytopenia syndrome768556005
- Myelocerebellar disorder768556005
- CLCN2 (chloride voltage-gated channel 2) related leucoencephalopathy768663003
- CLCN2 (chloride voltage-gated channel 2) related leukoencephalopathy768663003
- CLCN2-related leucoencephalopathy768663003
- CLCN2-related leukoencephalopathy768663003
- Leucoencephalopathy with ataxia768663003
- Leucoencephalopathy with mild cerebellar ataxia and white matter oedema768663003
- Leukoencephalopathy with ataxia768663003
- Leukoencephalopathy with mild cerebellar ataxia and white matter edema768663003
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WW domain containing oxidoreductase deficiency770898002
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX (WW domain containing oxidoreductase) deficiency770898002
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX deficiency770898002
- Autosomal recessive spinocerebellar ataxia type 12770898002
- Episodic ataxia type 8773495009
- Episodic ataxia with slurred speech773495009
- Ataxia, photosensitivity, short stature syndrome773769008
- Fenton Wilkinson Toselano syndrome773769008
- MIRAS - mitochondrial recessive ataxia syndrome782696001
- Recessive mitochondrial ataxia syndrome782696001
- Intellectual disability, hyperkinetic movement, truncal ataxia syndrome787174003
- Non-progressive cerebellar ataxia1119354003
- Progressive truncal ataxia1119356001
- Autosomal dominant cerebellar ataxia type 21156796002
- Congenital cerebellar ataxia due to RNA, U12 small nuclear mutation1177169004
- Congenital cerebellar ataxia due to RNU12 mutation1177169004
- Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome1187643003
- Autosomal recessive spinocerebellar ataxia type 211187643003
- Autosomal recessive spinocerebellar ataxia type 31204415006
- Autosomal recessive spinocerebellar ataxia, blindness, deafness syndrome1204415006
- Autosomal recessive spinocerebellar ataxia, blindness, hearing loss syndrome1204415006
- SCAR3 - spinocerebellar ataxia autosomal recessive type 31204415006
- Neuhauser Eichner Opitz syndrome1208339007
- Recurrent encephalopathy of childhood1208339007
- Spinocerebellar ataxia type 411208512000
- Spinocerebellar ataxia type 421208513005
- Spinocerebellar ataxia type 431208516002
- Severe intellectual disability, agenesis of corpus callosum, facial dysmorphism, cerebellar ataxia syndrome1208727002
- 4H leucodystrophy1208933000
- 4H leukodystrophy1208933000
- POLR-related leucodystrophy1208933000
- POLR-related leukodystrophy1208933000
- Lichtenstein Knorr syndrome1237413006
- Progressive autosomal recessive ataxia, deafness syndrome1237413006
- Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome1237413006
- SCAR19 - spinocerebellar ataxia, autosomal recessive 191237413006
- Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome1237514002
- Mitochondrial myopathy, cerebellar atrophy, pigmentary retinopathy syndrome1237514002
- Autosomal recessive cerebellar ataxia due to CWF19 like cell cycle control factor 1 deficiency1237625002
- Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency1237625002
- SCAR17 - spinocerebellar ataxia autosomal recessive type 171237625002
- DHX30-related neurodevelopmental delay, intellectual disability, ataxia, feeding difficulty syndrome1363573005
- DHX30-related neurodevelopmental disorder1363573005
- Neurodevelopmental delay, intellectual disability, ataxia, feeding difficulty syndrome1363573005
- Hereditary cerebellar atrophy431641000124107
Clinical Terms
- Myelocerebellar disorder
- Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
- Episodic ataxia type 1
- Autosomal recessive cerebellar ataxia Beauce type
- 4H leucodystrophy
- Autosomal recessive spinocerebellar ataxia type 21
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX (WW domain containing oxidoreductase) deficiency
- Congenital cerebellar ataxia due to RNU12 mutation
- Costa de Morte ataxia
- Episodic ataxia type 2
- Ataxia pancytopenia syndrome
- Observation of intelligibility of articulation
- Spinocerebellar ataxia type 13
- Cerebellar midline syndrome
- Cerebelloparenchymal disorder III
- Lethal ataxia-deafness-optic atrophy
- SCAR2 (spinocerebellar ataxia autosomal recessive 2)
- Asidan ataxia
- Ataxia, delayed dentition, hypomyelination syndrome
- Spinocerebellar ataxia type 6
- Congenital atrophy of optic nerve
- Fenton Wilkinson Toselano syndrome
- Mitochondrial myopathy, cerebellar atrophy, pigmentary retinopathy syndrome
- Spinocerebellar ataxia and erythrokeratodermia
- Speech delay
- Ataxia with pigmentary retinopathy
- Sanger-Brown cerebellar ataxia
- Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome
- Bailey-Cushing syndrome
- Spinocerebellar ataxia type 4
- Delayed dentition
- Episodic ataxia type 3
- Cerebellar ataxia, intellectual disability, optic atrophy, skin abnormalities syndrome
- Clipped speech
- Spinocerebellar ataxia type 23
- Recurrent encephalopathy of childhood
- Spinocerebellar ataxia with axonal neuropathy type 1
- Spinocerebellar ataxia type 42
- Jervis' syndrome
- Hereditary cerebellar atrophy
- Episodic ataxia type 1 (EA1)
- SCAR19 - spinocerebellar ataxia, autosomal recessive 19
- Poretti Boltshauser syndrome
- Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome
- Richards-Rundle syndrome
- Progressive truncal ataxia
- CAMOS (cerebellar ataxia, mental retardation, optic atrophy, skin abnormalities) syndrome
- Spinocerebellar ataxia type 40
- Dysmetric ataxia
- Slurred speech
- Spinocerebellar ataxia dysmorphism syndrome
- Autosomal recessive spinocerebellar ataxia type 12
- POLR-related leucodystrophy
- Huntington disease-like 4
- Acute hepatic failure
- Spinocerebellar ataxia type 20
- Leukoencephalopathy with mild cerebellar ataxia and white matter edema
- Early familial cerebellar degeneration syndrome
- Delayed eruption of tooth
- Fatal X-linked ataxia with deafness and loss of vision
- Spinocerebellar ataxia type 7
- Autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome
- POLR-related leukodystrophy
- Spinocerebellar ataxia with altered vertical eye movement
- ARCA1 - autosomal recessive cerebellar ataxia type 1
- Congenital non-progressive ataxia
- Spinocerebellar ataxia type 21
- Spinocerebellar ataxia type 31
- Spinocerebellar ataxia type 1
- Erythrokeratodermia with ataxia
- Autosomal recessive cerebellar ataxia with saccadic intrusion syndrome
- Cayman ataxia
- DHX30-related neurodevelopmental delay, intellectual disability, ataxia, feeding difficulty syndrome
- Spinocerebellar ataxia type 19
- Spinocerebellar ataxia type 15/16
- Acute liver failure
- Spinocerebellar ataxia type 41
- Autosomal recessive cerebelloparenchymal disorder type 3
- Intellectual disability, hyperkinetic movement, truncal ataxia syndrome
- Spinocerebellar ataxia type 8
- Progressive autosomal recessive ataxia, deafness syndrome
- Arts syndrome
- Autosomal recessive spinocerebellar ataxia, blindness, deafness syndrome
- Recessive mitochondrial ataxia syndrome
- Autosomal recessive spinocerebellar ataxia, blindness, hearing loss syndrome
- Ataxia, photosensitivity, short stature syndrome
- Finding of intelligibility of articulation
- SCAR17 - spinocerebellar ataxia autosomal recessive type 17
- Severe intellectual disability, agenesis of corpus callosum, facial dysmorphism, cerebellar ataxia syndrome
- Spinocerebellar ataxia type 30
- Autosomal recessive spinocerebellar ataxia type 3
- Non-progressive cerebellar ataxia
- Observation of clarity of speech
- DHX30-related neurodevelopmental disorder
- Oculomotor nerve finding
- Spinocerebellar ataxia type 25
- Spinocerebellar ataxia type 5
- Spinocerebellar ataxia type 2
- Autosomal dominant cerebellar ataxia type 2
- Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
- Autosomal recessive cerebellar ataxia due to CWF19 like cell cycle control factor 1 deficiency
- CLCN2-related leukoencephalopathy
- Leukoencephalopathy with ataxia
- MIRAS - mitochondrial recessive ataxia syndrome
- Slurring
- Spinocerebellar ataxia type 12
- Episodic ataxia type 4
- Leucoencephalopathy with ataxia
- Spinocerebellar ataxia type 27
- SCAR5 - spinocerebellar ataxia autosomal recessive 5
- Spinocerebellar ataxia type 38
- Episodic ataxia type 6
- Spinocerebellar ataxia type 34
- Leucoencephalopathy with mild cerebellar ataxia and white matter oedema
- Congenital optic atrophy
- Lichtenstein Knorr syndrome
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WW domain containing oxidoreductase deficiency
- Spinocerebellar ataxia type 26
- Truncal ataxia
- Delayed tooth eruption
- Episodic ataxia type 8
- Spinocerebellar ataxia 36
- Episodic ataxia
- Episodic ataxia with slurred speech
- Scamping speech
- Episodic ataxia type 5
- Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency
- Spinocerebellar ataxia type 14
- CLCN2-related leucoencephalopathy
- Spinocerebellar ataxia type 37
- Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX deficiency
- Unintelligible speech
- Cerebellar ataxia Cayman type
- Neurodevelopmental delay, intellectual disability, ataxia, feeding difficulty syndrome
- CLCN2 (chloride voltage-gated channel 2) related leucoencephalopathy
- Spinocerebellar ataxia type 36
- CAMOS syndrome
- Spinocerebellar ataxia type 11
- 4H leukodystrophy
- Late tooth eruption
- Spinocerebellar ataxia type 35
- Unintelligible articulation
- Spinocerebellar ataxia type 32
- Abnormal saccadic eye movement
- Episodic ataxia type 2 (EA2)
- Observation of intelligibility of speech
- Spinocerebellar ataxia type 17
- SCAR3 - spinocerebellar ataxia autosomal recessive type 3
- CLCN2 (chloride voltage-gated channel 2) related leukoencephalopathy
- Third cranial nerve finding
- Cerebellar syndrome pigmentary maculopathy
- Spinocerebellar ataxia type 29
- Congenital cerebellar ataxia due to RNA, U12 small nuclear mutation
- Leukoencephalopathy, ataxia, hypodontia, hypomyelination syndrome
- Neuhauser Eichner Opitz syndrome
- Congenital nonprogressive spinocerebellar ataxia
- Episodic ataxia and vertigo with tinnitus and myokymia syndrome
- Slow to talk
- Spinocerebellar ataxia type 10
- Spinocerebellar ataxia type 28
- Periodic vestibulocerebellar ataxia
- Spinocerebellar ataxia type 43
- Spinocerebellar ataxia type 18
- ALF - Acute liver failure
Frequently Asked Questions
What is the ICD-10 code for other hereditary ataxias?
The ICD-10-CM code for other hereditary ataxias is G11.8. The full clinical description is "Other hereditary ataxias". G11.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G11.8 mean?
ICD-10-CM code G11.8 represents “Other hereditary ataxias”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G11.8 a billable code?
Yes, G11.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G11.8 in?
G11.8 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G11.8 map to?
G11.8 maps to 90 SNOMED CT concepts: 1208933000, 197270009, 725433003, 246767003, 1187643003, and 85 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G11.8?
G11.8 is linked to 1 UMLS Concept Unique Identifier: C0477348. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G11.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other hereditary ataxias affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G11.8?
G11.8 maps to the ICD-11 code: 8A03.Z (Ataxic disorders, unspecified).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.