G11.5
BillableHypomyelination - hypogonadotropic hypogonadism - hypodontia
Hypomyelination - hypogonadotropic hypogonadism - hypodontia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- 4H syndrome
- Pol III-related leukodystrophy
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •cerebral palsyG80
- •hereditary and idiopathic neuropathyG60
- •metabolic disordersE70-E88
Related Codes(8)
G11.0Congenital nonprogressive ataxia
G11.1Early-onset cerebellar ataxia
G11.2Late-onset cerebellar ataxia
G11.3Cerebellar ataxia with defective DNA repair
G11.4Hereditary spastic paraplegia
G11.6Leukodystrophy with vanishing white matter disease
G11.8Other hereditary ataxias
G11.9Hereditary ataxia, unspecified
Also Known As / Clinical Terms(61)
SNOMED CT
UMLS
- 4H LEUKODYSTROPHY 1C2676243
- 4H SYNDROMEC2676243
- 4H syndromeC2676243
- ADDHC2676243
- ATAXIA, DELAYED DENTITION, AND HYPOMYELINATIONC2676243
- Ataxia, Delayed Dentition, and HypomyelinationC2676243
- Ataxia, delayed dentition, and hypomyelinationC2676243
- HLD7C2676243
- Hypomyelinating Leukodystrophy-7C2676243
- Hypomyelination - hypogonadotropic hypogonadism - hypodontiaC2676243
- Hypomyelination, hypodontia, hypogonadotropic hypogonadismC2676243
- Hypomyelination, hypogonadotropic hypogonadism, hypodontia syndromeC2676243
- Hypomyelination, hypogonadotropic hypogonadism, hypodontia syndrome (disorder)C2676243
- LEUKODYSTROPHY, HYPOMYELINATING, 7, WITH OR WITHOUT OLIGODONTIA AND/OR HYPOGONADOTROPIC HYPOGONADISMC2676243
- LEUKODYSTROPHY, HYPOMYELINATING, WITH HYPODONTIA AND HYPOGONADOTROPIC HYPOGONADISMC2676243
- LEUKOENCEPHALOPATHY, HYPOMYELINATING, WITH ATAXIA AND DELAYED DENTITIONC2676243
- Leukodystrophy, Hypomyelinating, 7C2676243
- Leukodystrophy, Hypomyelinating, with Hypodontia and Hypogonadotropic HypogonadismC2676243
- Leukodystrophy, hypomyelinating, 7, with or without oligodontia and/or hypogonadotropic hypogonadismC2676243
- Leukoencephalopathy, Hypomyelinating, with Ataxia and Delayed DentitionC2676243
- Leukoencephalopathy-ataxia-hypodontia-hypomyelinationC2676243
- Pol III disorderC4038750
- Pol III-related hypomyelinating leukodystrophiesC4038750
- Pol III-related leukodystrophyC4038750
- RNA polymerase III-related leucodystrophyC4038750
- RNA polymerase III-related leukodystrophyC4038750
- Ribonucleic acid polymerase III-related leucodystrophyC4038750
- Ribonucleic acid polymerase III-related leukodystrophyC4038750
- Ribonucleic acid polymerase III-related leukodystrophy (disorder)C4038750
Clinical Terms
- Ribonucleic acid polymerase III-related leukodystrophy
- Leukodystrophy, hypomyelinating, 7, with or without oligodontia and/or hypogonadotropic hypogonadism
- Hypomyelination, hypogonadotropic hypogonadism, hypodontia syndrome (disorder)
- RNA polymerase III-related leucodystrophy
- ADDH
- Hypomyelination, hypodontia, hypogonadotropic hypogonadism
- Pol III-related hypomyelinating leukodystrophies
- 4H leucodystrophy
- Leukodystrophy, Hypomyelinating, 7
- Pol III-related leukodystrophy
- Hypomyelinating Leukodystrophy-7
- POLR-related leucodystrophy
- Ataxia, delayed dentition, and hypomyelination
- Pol III disorder
- RNA polymerase III-related leukodystrophy
- 4H leukodystrophy
- POLR-related leukodystrophy
- HLD7
- Leukoencephalopathy, Hypomyelinating, with Ataxia and Delayed Dentition
- Leukoencephalopathy-ataxia-hypodontia-hypomyelination
- 4H LEUKODYSTROPHY 1
- 4H syndrome
- Hypomyelination, hypogonadotropic hypogonadism, hypodontia syndrome
- Leukodystrophy, Hypomyelinating, with Hypodontia and Hypogonadotropic Hypogonadism
- Ribonucleic acid polymerase III-related leukodystrophy (disorder)
- Ribonucleic acid polymerase III-related leucodystrophy
Frequently Asked Questions
What is the ICD-10 code for hypomyelination - hypogonadotropic hypogonadism - hypodontia?
The ICD-10-CM code for hypomyelination - hypogonadotropic hypogonadism - hypodontia is G11.5. The full clinical description is "Hypomyelination - hypogonadotropic hypogonadism - hypodontia". G11.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G11.5 mean?
ICD-10-CM code G11.5 represents “Hypomyelination - hypogonadotropic hypogonadism - hypodontia”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G11.5 a billable code?
Yes, G11.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G11.5 in?
G11.5 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G11.5 map to?
G11.5 maps to 2 SNOMED CT concepts: 1208933000, 721846006. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G11.5?
G11.5 is linked to 2 UMLS Concept Unique Identifiers: C2676243, C4038750. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G11.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hypomyelination - hypogonadotropic hypogonadism - hypodontia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G11.5?
There is no direct ICD-11 mapping available for G11.5 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.