AutoICD API

G90.1

Billable

Familial dysautonomia [Riley-Day]

Familial dysautonomia [Riley-Day]

Status

Billable / Specific

Block

G89-G99

Parent Code

G90

ICD-11 Mapping

1 equivalent

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(9)
G90.0

Idiopathic peripheral autonomic neuropathy

G90.2

Horner's syndrome

BillableG90.3

Multi-system degeneration of the autonomic nervous system

BillableG90.4

Autonomic dysreflexia

BillableG90.5

Complex regional pain syndrome I (CRPS I)

G90.8

Other disorders of autonomic nervous system

G90.9

Disorder of the autonomic nervous system, unspecified

BillableG90.A

Postural orthostatic tachycardia syndrome [POTS]

BillableG90.B

LMNB1-related autosomal dominant leukodystrophy

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

8C21.1Hereditary sensory and autonomic neuropathy type IIIequivalentPrimary
Also Known As / Clinical Terms(82)

SNOMED CT

UMLS

Clinical Terms

  • HSAN (Hereditary Sensory and Autonomic Neuropathy) Type III
  • HSN-III
  • Type III Hereditary Sensory Neuropathy, Dominant
  • Hereditary Sensory Neuropathy Type 3
  • HSAN Type III
  • Dysautonomia, Familial
  • DYS
  • Familial dysautonomia (disorder)
  • Peripheral motor neuropathy dysautonomia syndrome
  • HSAN 3
  • dysautonomia familial
  • HSAN3
  • NEUROPATHY, HEREDITARY SENSORY AND AUTONOMIC, TYPE III
  • Riley-Day Syndrome
  • HSAN III
  • riley day syndrome
  • Hereditary sensory and autonomic neuropathy, type III
  • Dominant Hereditary Sensory Neuropathy, Type III
  • familial autonomic nervous dysfunction
  • Hereditary sensory and autonomic neuropathy type III
  • Hereditary Sensory Neuropathy, Dominant, Type III
  • Hereditary-Sensory and Autonomic Neuropathy Type III
  • Hereditary Sensory Neuropathy, Type 3, Dominant
  • Hereditary Sensory Neuropathy, Dominant, Type 3
  • Hereditary Sensory and Autonomic Neuropathy 3
  • Lisker Garcia Ramos syndrome
  • Neuropathy, Hereditary and Autonomic, Type III
  • Familial Dysautonomia
  • Hereditary dysautonomia with motor neuropathy
  • riley days syndrome
  • Type 3 Hereditary Sensory Neuropathy, Dominant
Frequently Asked Questions
What is the ICD-10 code for familial dysautonomia [riley-day]?

The ICD-10-CM code for familial dysautonomia [riley-day] is G90.1. The full clinical description is "Familial dysautonomia [Riley-Day]". G90.1 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code G90.1 mean?

ICD-10-CM code G90.1 represents “Familial dysautonomia [Riley-Day]”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.

Is G90.1 a billable code?

Yes, G90.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is G90.1 in?

G90.1 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).

What codes cannot be used with G90.1?

G90.1 has Excludes1 notes indicating codes that cannot be used together with it, including: dysfunction of the autonomic nervous system due to alcohol (G31.2).

What SNOMED CT codes does G90.1 map to?

G90.1 maps to 2 SNOMED CT concepts: 29159009, 230557001. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for G90.1?

G90.1 is linked to 1 UMLS Concept Unique Identifier: C0013364. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does G90.1 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like familial dysautonomia [riley-day] affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of G90.1?

G90.1 maps to the ICD-11 code: 8C21.1 (Hereditary sensory and autonomic neuropathy type III).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.