Milroy lymphedema
VEGFC-related congenital primary lymphoedema
Congenital primary lymphoedema of Gordon
Hereditary lymphedema type II
Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphoedema syndrome
Constriction ring syndrome of lower limb
Meige lymphoedema
Constriction ring of upper limb with lymphoedema
PIEZO1-related generalized lymphatic dysplasia with non-immune hydrops fetalis
MLCRD (microcephaly with or without chorioretinopathy, lymphedema or intellectual disability) syndrome
Congenital malformation of lymphatic vessel of skin
Hereditary disorder of lymphatic system
Congenital lymphangiectasia
Primary adult lymphoedema
Lymphoedema of lower extremity
Foot oedema
OL-EDA-ID (anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphoedema) syndrome
Congenital lymphangiectasia with chylous reflux
HLTRS (hypotrichosis, lymphoedema, telangiectasia, renal defect) syndrome
Lymphedema, posterior choanal atresia syndrome
Distichiasis-lymphoedema syndrome
Piezo type mechanosensitive ion channel component 1-related generalized lymphatic dysplasia with non-immune hydrops fetalis
Congenital constriction band
Foot edema
PIEZO1-related lymphatic-related hydrops fetalis
Amniotic bands of upper limb
Choanal atresia
WILD syndrome
hereditary lymphoedema
Constriction ring syndrome
CELSR1-related late-onset primary lymphoedema
Edema of foot
Lymphoedema tardum
Constricting band of extremity
EPHB4-related generalised lymphatic dysplasia with atrial septal defect
Lymphedema of upper limb
GJC2-related late-onset primary lymphedema
Gap junction protein gamma 2-related late-onset primary lymphedema
Lymphoedema, posterior choanal atresia syndrome
Warts, immunodeficiency, lymphedema, anogenital dysplasia syndrome
Megakaryocytic thrombocytopenia
PIEZO1-related generalised lymphatic dysplasia with systemic involvement
Warts, immunodeficiency, lymphoedema, anogenital dysplasia syndrome
PIEZO1-related generalized lymphatic dysplasia with systemic involvement
Congenital atresia of choana
PEHOL (progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like) syndrome
Lymphedema tardum
GJC2-related late-onset primary lymphoedema
Primary lymphedema tardum
Microcephalus, lymphedema, chorioretinopathy syndrome
Macrothrombocytopenia, lymphoedema, developmental delay, facial dysmorphism, camptodactyly syndrome
Nonne-Milroy lymphedema
EPHB4-related lymphatic-related hydrops fetalis
Yellow nails
Atresia of posterior nares
Hereditary lymphedema (disorder)
Constriction ring of lower limb with lymphoedema
Generalized lymphatic dysplasia of Fotiou
Piezo type mechanosensitive ion channel component 1-related generalised lymphatic dysplasia with non-immune hydrops fetalis
Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
Milroy lymphoedema
Yellow nail syndrome
Hereditary lymphedema type I
Lymphoedema tarda
Progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like syndrome
Atresia of posterior naris
Congenital cerebral arteriovenous malformation
Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
Gap junction protein gamma 2-related late-onset primary lymphoedema
Cerebral arteriovenous malformation
Congenital lymphangiectasis
Amniotic band syndrome
Adult lymphedema
Primary adult lymphedema
Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
Hereditary lymphedema and yellow nails
Congenital atresia of posterior nares
Disseminated warts, impaired cell-mediated immunity, primary lymphedema, anogenital dysplasia syndrome
Microcephalus, lymphoedema, chorioretinopathy syndrome
PEHOL (progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like) syndrome
Macrothrombocytopenia, lymphedema, developmental delay, facial dysmorphism, camptodactyly syndrome
CELSR1-related late-onset primary lymphedema
Constriction ring syndrome of upper limb
VEGFC-related congenital primary lymphedema
Reduplication of lashes
EPHB4-related generalised lymphatic dysplasia with non-immune hydrops fetalis
OL-EDA-ID (anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema) syndrome
Congenital distichiasis
EPHB4-related generalized lymphatic dysplasia with non-immune hydrops fetalis
Lymphoedema of upper limb
Takenouchi Kosaki syndrome
Cadherin EGF LAG seven-pass G-type receptor 1-related late-onset primary lymphedema
Hereditary lymphoedema type I
Congenital anomaly of cutaneous lymphatics
Constriction ring of lower limb with lymphedema
Lymphedema of lower extremity
Hereditary lymphoedema and yellow nails
HLTRS (hypotrichosis, lymphedema, telangiectasia, renal defect) syndrome
Congenital primary lymphedema of Gordon
Congenital cutaneous lymphangiectasia
Cadherin EGF LAG seven-pass G-type receptor 1-related late-onset primary lymphoedema
Meige disease
Deformity due to amniotic band
primary lymphedema
AVM - Cerebral arteriovenous malformation
Lymphoedema and cerebral arteriovenous anomaly syndrome
Lymphedema tarda
Ectopic cilia of eyelid
Hypotrichosis, lymphoedema, telangiectasia, renal defect syndrome
Congenital malformation of cutaneous lymphatics
Nonne-Milroy lymphoedema
Ephrin receptor B4-related lymphatic-related hydrops fetalis
Meige lymphedema
Distichiasis
Generalised lymphatic dysplasia of Fotiou
Pedal edema
Hereditary lymphoedema type II
Pedal oedema
Adult lymphoedema
Primary lymphoedema tardum
lymphedema primary
PEHO-like syndrome
Constriction ring of upper limb with lymphedema
Congenital lymphangiectases
Lymphedema and cerebral arteriovenous anomaly syndrome
PIEZO1-related generalised lymphatic dysplasia with non-immune hydrops fetalis
Oedema of foot
WILD (warts, immunodeficiency, lymphoedema, anogenital dysplasia) syndrome
Distichiasis-lymphedema syndrome
Accessory eyelid
MLCRD (microcephaly with or without chorioretinopathy, lymphoedema or intellectual disability) syndrome
Lymphoedema of leg
EPHB4-related generalized lymphatic dysplasia with atrial septal defect
Congenital elephantiasis
Lymphedema of leg
Disseminated warts, impaired cell-mediated immunity, primary lymphoedema, anogenital dysplasia syndrome
WILD (warts, immunodeficiency, lymphedema, anogenital dysplasia) syndrome
primary lymphoedema

Frequently Asked Questions

What is the ICD-10 code for hereditary lymphedema?

The ICD-10-CM code for hereditary lymphedema is Q82.0. The full clinical description is "Hereditary lymphedema". Q82.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q82.0 mean?

ICD-10-CM code Q82.0 represents “Hereditary lymphedema”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q82.0 a billable code?

Yes, Q82.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q82.0 in?

Q82.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q82.0?

Q82.0 has Excludes1 notes indicating codes that cannot be used together with it, including: acrodermatitis enteropathica (E83.2); congenital erythropoietic porphyria (E80.0); pilonidal cyst or sinus (L05.-); and 1 more.

What SNOMED CT codes does Q82.0 map to?

Q82.0 maps to 42 SNOMED CT concepts: 234142008, 24606006, 400158000, 765206003, 205299003, and 37 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q82.0?

Q82.0 is linked to 1 UMLS Concept Unique Identifier: C5779780. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q82.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary lymphedema affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q82.0?

Q82.0 maps to the ICD-11 code: BD93.0 (Primary lymphoedema).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.