Q82.3

Billable

Incontinentia pigmenti

Incontinentia pigmenti

Status

Billable / Specific

Parent Code

Q82

ICD-11 Mapping

1 equivalent

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
Q82.0

Hereditary lymphedema

BillableQ82.1

Xeroderma pigmentosum

BillableQ82.2

Congenital cutaneous mastocytosis

BillableQ82.4

Ectodermal dysplasia (anhidrotic)

BillableQ82.5

Congenital non-neoplastic nevus

BillableQ82.6

Congenital sacral dimple

BillableQ82.8

Other specified congenital malformations of skin

BillableQ82.9

Congenital malformation of skin, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LD27.00Incontinentia pigmentiequivalentPrimary
Also Known As / Clinical Terms(46)

SNOMED CT

UMLS

Clinical Terms

  • asboe-hansen disease
  • Bloch-Siemens-Sulzberger Syndrome
  • bloch-sulzberger melanoblastoma
  • nevus pigmentosus systematicus
  • Bloch-Sulzberger Syndrome
  • incontinentia pigmenti syndrome
  • Hypomelanosis of Ito
  • Syndrome, Bloch-Sulzberger
  • Bloch-Siemens syndrome
  • Incontinentia pigmenti achromians syndrome
  • Bloch Sulzberger Syndrome
  • HMI - Hypomelanosis of Ito
  • Incontinentia pigmenti achromicans of Ito
  • Incontinentia pigmenti of Bloch-Sulzberger
  • IP - Incontinentia pigmenti
  • Incontinentia pigmenti syndrome (disorder)
Frequently Asked Questions
What is the ICD-10 code for incontinentia pigmenti?

The ICD-10-CM code for incontinentia pigmenti is Q82.3. The full clinical description is "Incontinentia pigmenti". Q82.3 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q82.3 mean?

ICD-10-CM code Q82.3 represents “Incontinentia pigmenti”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q82.3 a billable code?

Yes, Q82.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q82.3 in?

Q82.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q82.3?

Q82.3 has Excludes1 notes indicating codes that cannot be used together with it, including: acrodermatitis enteropathica (E83.2); congenital erythropoietic porphyria (E80.0); pilonidal cyst or sinus (L05.-); and 1 more.

What SNOMED CT codes does Q82.3 map to?

Q82.3 maps to 2 SNOMED CT concepts: 367520004, 218358001. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q82.3?

Q82.3 is linked to 1 UMLS Concept Unique Identifier: C0021171. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q82.3 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like incontinentia pigmenti affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q82.3?

Q82.3 maps to the ICD-11 code: LD27.00 (Incontinentia pigmenti).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.