E88.4
Non-billableMitochondrial metabolism disorders
Mitochondrial metabolism disorders
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •histiocytosis X (chronic)C96.6
- •disorders of pyruvate metabolismE74.4
- •Kearns-Sayre syndromeH49.81
- •Leber's diseaseH47.22
- •Leigh's encephalopathyG31.82
- •Mitochondrial myopathy, NECG71.3
- •Reye's syndromeG93.7
Use Additional Code
Additional codes that should follow this code
- codes for associated conditions
Child Codes (5)
Related Codes(7)
E88.0Disorders of plasma-protein metabolism, NEC
E88.1Lipodystrophy, not elsewhere classified
E88.2Lipomatosis, not elsewhere classified
E88.3Tumor lysis syndrome
E88.8Other specified metabolic disorders
E88.9Metabolic disorder, unspecified
E88.AWasting disease (syndrome) due to underlying condition
Also Known As / Clinical Terms(2)
Frequently Asked Questions
What is the ICD-10 code for mitochondrial metabolism disorders?
The ICD-10-CM code for mitochondrial metabolism disorders is E88.4. The full clinical description is "Mitochondrial metabolism disorders". E88.4 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code E88.4 mean?
ICD-10-CM code E88.4 represents “Mitochondrial metabolism disorders”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a non-billable header code. Use a more specific child code for billing purposes.
Is E88.4 a billable code?
No, E88.4 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 5 child codes under E88.4.
What chapter is E88.4 in?
E88.4 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E88.4?
E88.4 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 10 more.
What are the subcategories under E88.4?
E88.4 has 5 child codes, including: E88.40 (Mitochondrial metabolism disorder, unspecified), E88.41 (MELAS syndrome), E88.42 (MERRF syndrome), E88.43 (Disorders of mitochondrial tRNA synthetases), and 1 more.
Are additional codes required with E88.4?
Yes, when using E88.4, also report: codes for associated conditions.
What are the UMLS CUIs for E88.4?
E88.4 is linked to 1 UMLS Concept Unique Identifier: C1456275. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E88.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like mitochondrial metabolism disorders affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E88.4?
There is no direct ICD-11 mapping available for E88.4 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.