E88.1
BillableLipodystrophy, not elsewhere classified
Lipodystrophy, not elsewhere classified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Lipodystrophy NOS
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •histiocytosis X (chronic)C96.6
- •Whipple's diseaseK90.81
Use Additional Code
Additional codes that should follow this code
- codes for associated conditions
Related Codes(7)
E88.0Disorders of plasma-protein metabolism, NEC
E88.2Lipomatosis, not elsewhere classified
E88.3Tumor lysis syndrome
E88.4Mitochondrial metabolism disorders
E88.8Other specified metabolic disorders
E88.9Metabolic disorder, unspecified
E88.AWasting disease (syndrome) due to underlying condition
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(1)
Frequently Asked Questions
What is the ICD-10 code for lipodystrophy, not elsewhere classified?
The ICD-10-CM code for lipodystrophy, not elsewhere classified is E88.1. The full clinical description is "Lipodystrophy, not elsewhere classified". E88.1 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E88.1 mean?
ICD-10-CM code E88.1 represents “Lipodystrophy, not elsewhere classified”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E88.1 a billable code?
Yes, E88.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E88.1 in?
E88.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E88.1?
E88.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 5 more.
Are additional codes required with E88.1?
Yes, when using E88.1, also report: codes for associated conditions.
What are the UMLS CUIs for E88.1?
E88.1 is linked to 1 UMLS Concept Unique Identifier: C0494360. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E88.1 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like lipodystrophy, not elsewhere classified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E88.1?
E88.1 maps to the ICD-11 code: 5D2Z (Metabolic disorders, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.