E88.9
BillableMetabolic disorder, unspecified
Metabolic disorder, unspecified
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Use Additional Code
Additional codes that should follow this code
- codes for associated conditions
Related Codes(7)
E88.0Disorders of plasma-protein metabolism, NEC
E88.1Lipodystrophy, not elsewhere classified
E88.2Lipomatosis, not elsewhere classified
E88.3Tumor lysis syndrome
E88.4Mitochondrial metabolism disorders
E88.8Other specified metabolic disorders
E88.AWasting disease (syndrome) due to underlying condition
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(285)
SNOMED CT
- Disorder of neurometabolic regulation16279005
- Metabolic myopathy26111005
- Myopathy in metabolic diseases26111005
- Generalised metabolic disorder30390004
- Generalized metabolic disorder30390004
- Restrictive cardiomyopathy secondary to familial storage disease30884007
- Storage disease34420000
- Familial cardiomyopathy35728003
- Primary familial cardiomyopathy35728003
- Arthropathy associated with an endocrine AND/OR metabolic disorder39710007
- Arthropathy associated with endocrine and metabolic disorder39710007
- Corneal deposit associated with metabolic disorder43521007
- Nutritional myopathy44253006
- Age-related hearing loss49526009
- Presbyacusia49526009
- Presbycusis49526009
- Senile deafness49526009
- Sinus bradycardia49710005
- Metabolic bone disease50279003
- Metabolic disorder of bone50279003
- Metabolic disturbance in labor AND/OR delivery61714007
- Metabolic disturbance in labour AND/OR delivery61714007
- Defective metabolism63569001
- BIH - Benign intracranial hypertension68267002
- Benign intracranial hypertension68267002
- IIH - Idiopathic intracranial hypertension68267002
- Idiopathic intracranial hypertension68267002
- Noninfective serous meningitis68267002
- Nonne's syndrome68267002
- Otitic hydrocephalus syndrome68267002
- Pseudotumor cerebri68267002
- Pseudotumour cerebri68267002
- Localised metabolic disorder74479008
- Localized metabolic disorder74479008
- MD - Metabolic disorders75934005
- Metabolic disease75934005
- Metabolic disorder75934005
- Enzyme disorder78548001
- Enzymopathy78548001
- Amino acid deficiency82994006
- IBEM - Inborn error of metabolism86095007
- IEM - Inborn error of metabolism86095007
- Inborn error of metabolism86095007
- Abnormal metabolic requirement87133009
- Defective biosynthesis102632006
- Metabolic disorders of the kidney106000008
- Metabolic renal disease106000008
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Acute metabolic disease127339009
- Acute metabolic disorder127339009
- Inherited metabolic disorder of nervous system128190004
- Chronic metabolic disease128289001
- Chronic metabolic disorder128289001
- Metabolic presbycusis129629004
- Acute confusional state, of metabolic origin191504009
- Glaucoma in endocrine, nutritional and metabolic diseases193556009
- Cardiac glycogenosis195025008
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Familial restrictive cardiomyopathy233878008
- Intrinsic staining of tooth - metabolic disease234985000
- Metabolic ileus235836004
- Metabolic and genetic disorder affecting the liver235903001
- Abnormal metabolic state due to diabetes mellitus237620003
- Abnormal metabolic state in diabetes mellitus237620003
- Metabolic and nutritional disorders affecting skin238944001
- Metabolic complication of procedures363203000
- Seizures due to metabolic disorder371022006
- Clinical manifestation of enzyme deficiency410053003
- Aplastic anaemia associated with metabolic alteration413565006
- Aplastic anemia associated with metabolic alteration413565006
- Thrombocytopenic purpura associated with metabolic disorder417626001
- Carnitine deficiency421784001
- Acquired sensorineural hearing loss609125008
- Pericarditis due to metabolic disease703332001
- Pericarditis in metabolic disease703332001
- Neuropathy of upper limb due to metabolic disorder710349003
- Peripheral neuropathy of upper limb due to metabolic disorder710349003
- Peripheral neuropathy due to metabolic disorder710360007
- Tremor due to metabolic disorder722969006
- Dementia due to metabolic abnormality722979008
- Myelopathy due to metabolic disorder722984002
- Neonatal metabolic disorder736652002
- Interstitial lung disease due to metabolic disease737183007
- Anaemia due to metabolic disorder737220002
- Anemia due to metabolic disorder737220002
- Metabolic anaemia737220002
- Metabolic anemia737220002
- Autonomic neuropathy due to metabolic disease737241008
- Navajo neurohepatopathy784346006
- Navajo neuropathy784346006
- Radiculopathy due to metabolic disorder789018001
- Cardiomyopathy due to storage disease860839005
- Infiltrative cardiomyopathy871646007
- Sinus bradycardia due to metabolic disease1142111009
- Chronic tubulointerstitial nephritis due to metabolic disease1144897006
- Disorder of nerve due to metabolic disease1153623003
- Metabolic neuropathy1153623003
- Enlargement of spleen due to storage disease1162654006
- Splenomegaly due to storage disease1162654006
- Hypopituitarism due to metabolic disease1186837006
- Corneal deposits due to metabolic disorder1217638003
- Autonomic disorder due to metabolic disorder1259056005
- Disorder of autonomic nervous system due to metabolic disorder1259056005
- Metabolic autonomic disorder1259056005
- Chorea due to metabolic disorder1259619002
- Chorea due to inborn error of metabolism1259622000
- Benign intracranial hypertension due to metabolic disease1263545007
- Arthropathy due to metabolic disorder324301000119107
- Bilateral deposit in corneas678881000119107
- Corneal deposit in bilateral eyes678881000119107
- Deposit in bilateral corneas678881000119107
- Deposit in both corneas678881000119107
- Carnitine deficiency due to inborn error of metabolism55341000119107
- Corneal deposit of bilateral eyes due to metabolic disorder678941000119106
- Deposit in cornea of bilateral eyes due to metabolic disorder678941000119106
- Deposit in cornea of both eyes due to metabolic disorder678941000119106
- Corneal deposit of left eye due to metabolic disorder678951000119108
- Deposit in cornea of left eye due to metabolic disorder678951000119108
- Corneal deposit of right eye due to metabolic disorder680981000119105
- Deposit in cornea of right eye due to metabolic disorder680981000119105
- Hereditary metabolic disease1821000146108
UMLS
- DIS METABC0025517
- Disease, MetabolicC0025517
- Diseases, MetabolicC0025517
- Generalised metabolic disorderC0025517
- Generalized metabolic disorderC0025517
- Generalized metabolic disorder (disorder)C0025517
- MD - Metabolic disordersC0025517
- METAB DISC0025517
- Metabolic DiseaseC0025517
- Metabolic DiseasesC0025517
- Metabolic DisorderC0025517
- Metabolic DisordersC0025517
- Metabolic diseaseC0025517
- Metabolic disease (disorder)C0025517
- Metabolic disorderC0025517
- Metabolic disorder NOSC0025517
- Metabolic disorder, unspecifiedC0025517
- ThesaurismosesC0025517
- ThesaurismosisC0025517
- Unspecified disorder of metabolismC0025517
- metabolic diseaseC0025517
- metabolic diseasesC0025517
- metabolic disorderC0025517
- metabolic disordersC0025517
- metabolism disorderC0025517
Clinical Terms
- Deposit in bilateral corneas
- Sinus bradycardia
- Metabolic disturbance in labor AND/OR delivery
- metabolic diseases
- Navajo neuropathy
- Inborn error of metabolism
- Peripheral neuropathy of upper limb due to metabolic disorder
- Deposit in cornea of right eye due to metabolic disorder
- Generalized metabolic disorder
- Metabolic neuropathy
- Primary familial cardiomyopathy
- Disorder of nerve due to metabolic disease
- Disorder of autonomic nervous system due to metabolic disorder
- Mucopolysaccharidosis cardiomyopathy
- Familial cardiomyopathy
- Neuropathy of upper limb due to metabolic disorder
- Chronic tubulointerstitial nephritis due to metabolic disease
- Arthropathy due to metabolic disorder
- Familial restrictive cardiomyopathy
- metabolism disorder
- metabolic disease
- Chorea due to metabolic disorder
- Neonatal metabolic disorder
- Corneal deposits due to metabolic disorder
- Carnitine deficiency
- BIH - Benign intracranial hypertension
- Infiltrative cardiomyopathy
- Pericarditis in metabolic disease
- Abnormal metabolic requirement
- Chronic metabolic disorder
- IIH - Idiopathic intracranial hypertension
- Thesaurismoses
- Myopathy in metabolic diseases
- Corneal deposit in bilateral eyes
- Age-related hearing loss
- Metabolic bone disease
- Arthropathy associated with an endocrine AND/OR metabolic disorder
- Metabolic disorder of bone
- Navajo neurohepatopathy
- MD - Metabolic disorders
- Deposit in cornea of both eyes due to metabolic disorder
- Intrinsic staining of tooth - metabolic disease
- Aplastic anemia associated with metabolic alteration
- Chronic metabolic disease
- Nutritional myopathy
- Storage disease
- Metabolic disease (disorder)
- Acute confusional state, of metabolic origin
- Idiopathic intracranial hypertension
- Peripheral neuropathy due to metabolic disorder
- Metabolic and genetic disorder affecting the liver
- Dementia due to metabolic abnormality
- Acute metabolic disease
- Metabolic presbycusis
- Diseases, Metabolic
- Anaemia due to metabolic disorder
- Deposit in cornea of left eye due to metabolic disorder
- Senile deafness
- Generalized metabolic disorder (disorder)
- Aplastic anaemia associated with metabolic alteration
- Nonne's syndrome
- Enzyme disorder
- Chorea due to inborn error of metabolism
- Presbyacusia
- Localized metabolic disorder
- Anemia due to metabolic disorder
- METAB DIS
- Autonomic disorder due to metabolic disorder
- Tremor due to metabolic disorder
- Enzymopathy
- Glaucoma in endocrine, nutritional and metabolic diseases
- Dilated cardiomyopathy due to metabolic disorder
- Acute metabolic disorder
- Interstitial lung disease due to metabolic disease
- Pseudotumour cerebri
- Seizures due to metabolic disorder
- Disease, Metabolic
- Noninfective serous meningitis
- Deposit in cornea of bilateral eyes due to metabolic disorder
- Splenomegaly due to storage disease
- Defective biosynthesis
- Metabolic and nutritional disorders affecting skin
- Restrictive cardiomyopathy secondary to familial storage disease
- Corneal deposit of bilateral eyes due to metabolic disorder
- Metabolic disorders of the kidney
- Cardiomyopathy due to mucopolysaccharidosis
- Autonomic neuropathy due to metabolic disease
- Cardiomyopathy due to storage disease
- Metabolic myopathy
- Abnormal metabolic state due to diabetes mellitus
- Hypopituitarism due to metabolic disease
- Thrombocytopenic purpura associated with metabolic disorder
- Inherited metabolic disorder of nervous system
- Arthropathy associated with endocrine and metabolic disorder
- Metabolic disorder NOS
- Cardiac glycogenosis
- Metabolic cardiomyopathy
- Metabolic complication of procedures
- Pseudotumor cerebri
- Unspecified disorder of metabolism
- Metabolic anaemia
- Metabolic anemia
- DIS METAB
- Bilateral deposit in corneas
- Acquired sensorineural hearing loss
- Clinical manifestation of enzyme deficiency
- metabolic disorders
- Carnitine deficiency due to inborn error of metabolism
- Deposit in both corneas
- Defective metabolism
- Otitic hydrocephalus syndrome
- Amino acid deficiency
- Corneal deposit of left eye due to metabolic disorder
- Myelopathy due to metabolic disorder
- Dilated cardiomyopathy secondary to metabolic disorder
- Presbycusis
- Corneal deposit of right eye due to metabolic disorder
- Pericarditis due to metabolic disease
- Metabolic ileus
- Localised metabolic disorder
- Metabolic disturbance in labour AND/OR delivery
- Sinus bradycardia due to metabolic disease
- Benign intracranial hypertension due to metabolic disease
- Metabolic autonomic disorder
- Benign intracranial hypertension
- Generalised metabolic disorder
- IBEM - Inborn error of metabolism
- Corneal deposit associated with metabolic disorder
- Abnormal metabolic state in diabetes mellitus
- IEM - Inborn error of metabolism
- Radiculopathy due to metabolic disorder
- Metabolic renal disease
- Disorder of neurometabolic regulation
- Enlargement of spleen due to storage disease
- Thesaurismosis
- Hereditary metabolic disease
Frequently Asked Questions
What is the ICD-10 code for metabolic disorder, unspecified?
The ICD-10-CM code for metabolic disorder, unspecified is E88.9. The full clinical description is "Metabolic disorder, unspecified". E88.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E88.9 mean?
ICD-10-CM code E88.9 represents “Metabolic disorder, unspecified”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E88.9 a billable code?
Yes, E88.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E88.9 in?
E88.9 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E88.9?
E88.9 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.
Are additional codes required with E88.9?
Yes, when using E88.9, also report: codes for associated conditions.
What SNOMED CT codes does E88.9 map to?
E88.9 maps to 76 SNOMED CT concepts: 87133009, 237620003, 609125008, 191504009, 127339009, and 71 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E88.9?
E88.9 is linked to 1 UMLS Concept Unique Identifier: C0025517. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E88.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like metabolic disorder, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E88.9?
E88.9 maps to the ICD-11 code: 5D2Z (Metabolic disorders, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.