H49.81
Non-billableKearns-Sayre syndrome
Kearns-Sayre syndrome
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Progressive external ophthalmoplegia with pigmentary retinopathy
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •diabetes mellitus related eye conditions, , ,E09.3, E10.3, E11.3, E13.3
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury (trauma) of eye and orbitS05
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •syphilis related eye disorders, , ,A50.01, A50.3, A51.43, A52.71
- •nystagmus and other irregular eye movementsH55
- •internal ophthalmoplegiaH52.51
- •internuclear ophthalmoplegiaH51.2
- •progressive supranuclear ophthalmoplegiaG23.1
Code Also
A second code may be required; sequencing depends on circumstances
- , if applicable, other manifestations, such as:
- •heart blockI45.9
Child Codes (4)
Related Codes(1)
Also Known As / Clinical Terms(70)
UMLS
- CHRONIC PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA WITH MYOPATHYC0022541
- CPEO WITH MYOPATHYC0022541
- CPEO WITH RAGGED-RED FIBERSC0022541
- CPEO with MyopathiesC0022541
- CPEO with MyopathyC0022541
- CPEO with Ragged Red FibersC0022541
- Chronic Progressive External Ophthalmoplegia with MyopathyC0022541
- Cpeo With Ragged-Red FibersC0022541
- Cytopathies, Kearns-Sayre MitochondrialC0022541
- Cytopathy, Kearn-Sayre MitochondrialC0022541
- Cytopathy, Kearns-Sayre MitochondrialC0022541
- KEARNS-SAYRE SYNDROMEC0022541
- KSSC0022541
- KSS - Kearns-Sayre syndromeC0022541
- Kearn Sayre Mitochondrial CytopathyC0022541
- Kearn SyndromeC0022541
- Kearn-Sayre Mitochondrial CytopathyC0022541
- Kearns Sayre Mitochondrial CytopathyC0022541
- Kearns Sayre Shy Daroff SyndromeC0022541
- Kearns Sayre SyndromeC0022541
- Kearns SyndromeC0022541
- Kearns' SyndromeC0022541
- Kearns-Sayre Mitochondrial CytopathiesC0022541
- Kearns-Sayre Mitochondrial CytopathyC0022541
- Kearns-Sayre SyndromeC0022541
- Kearns-Sayre mitochondrial cytopathyC0022541
- Kearns-Sayre syndromeC0022541
- Kearns-Sayre syndrome (disorder)C0022541
- Kearns-Sayre-Shy-Daroff SyndromeC0022541
- Mitochondrial Cytopathies, Kearns-SayreC0022541
- Mitochondrial Cytopathy, Kearn-SayreC0022541
- Mitochondrial Cytopathy, Kearns-SayreC0022541
- Mitochondrial ocular myopathyC0022541
- Myopathies, CPEO withC0022541
- Myopathy, CPEO withC0022541
- OCULOCRANIOSOMATIC SYNDROMEC0022541
- OPHTHALMOPLEGIA, PIGMENTARY DEGENERATION OF RETINA, AND CARDIOMYOPATHYC0022541
- OPHTHALMOPLEGIA, PROGRESSIVE EXTERNAL, WITH RAGGED-RED FIBERSC0022541
- OPHTHALMOPLEGIA-PLUS SYNDROMEC0022541
- Oculocraniosomatic SyndromeC0022541
- Oculocraniosomatic SyndromesC0022541
- Oculocraniosomatic syndromeC0022541
- Ophthalmoplegia Plus SyndromeC0022541
- Ophthalmoplegia Plus SyndromesC0022541
- Ophthalmoplegia plus syndromeC0022541
- Ophthalmoplegia plus syndrome (disorder)C0022541
- Ophthalmoplegia, Pigmentary Degeneration of Retina, and CardiomyopathyC0022541
- Ophthalmoplegia, Progressive External, With Ragged-Red FibersC0022541
- Ophthalmoplegia-Plus SyndromeC0022541
- Ophthalmoplegia-Plus SyndromesC0022541
- Sayre Syndrome, KearnsC0022541
- Syndrome, KearnsC0022541
- Syndrome, Kearns SayreC0022541
- Syndrome, Kearns'C0022541
- Syndrome, Kearns-SayreC0022541
- Syndrome, Kearns-Sayre-Shy-DaroffC0022541
- Syndrome, OculocraniosomaticC0022541
- Syndrome, Ophthalmoplegia PlusC0022541
- Syndrome, Ophthalmoplegia-PlusC0022541
- Syndromes, Ophthalmoplegia-PlusC0022541
- kearn sayer syndromeC0022541
- kearn sayers syndromeC0022541
- kearn sayre syndromeC0022541
- kearns sayer syndromeC0022541
- kearns sayers syndromeC0022541
- kearns sayre syndromeC0022541
- kearns syndromeC0022541
- kearns-sayer syndromeC0022541
- kearns-sayre syndromeC0022541
- Progressive external ophthalmoplegia with pigmentary retinopathyC2881300
Frequently Asked Questions
What is the ICD-10 code for kearns-sayre syndrome?
The ICD-10-CM code for kearns-sayre syndrome is H49.81. The full clinical description is "Kearns-Sayre syndrome". H49.81 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code H49.81 mean?
ICD-10-CM code H49.81 represents “Kearns-Sayre syndrome”. It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a non-billable header code. Use a more specific child code for billing purposes.
Is H49.81 a billable code?
No, H49.81 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 4 child codes under H49.81.
What chapter is H49.81 in?
H49.81 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What are the subcategories under H49.81?
H49.81 has 4 child codes, including: H49.811 (Kearns-Sayre syndrome, right eye), H49.812 (Kearns-Sayre syndrome, left eye), H49.813 (Kearns-Sayre syndrome, bilateral), H49.819 (Kearns-Sayre syndrome, unspecified eye).
What are the UMLS CUIs for H49.81?
H49.81 is linked to 2 UMLS Concept Unique Identifiers: C0022541, C2881300. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does H49.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like kearns-sayre syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of H49.81?
There is no direct ICD-11 mapping available for H49.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.