D82.8
BillableImmunodeficiency associated with oth major defects
Immunodeficiency associated with other specified major defects
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(6)
D82.0Wiskott-Aldrich syndrome
D82.1Di George's syndrome
D82.2Immunodeficiency with short-limbed stature
D82.3Immunodef fol heredit defctv response to Epstein-Barr virus
D82.4Hyperimmunoglobulin E [IgE] syndrome
D82.9Immunodeficiency associated with major defect, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(44)
SNOMED CT
- HAE - Hereditary angio-oedema82966003
- HAE - Hereditary angioedema82966003
- HANE - Hereditary angioneurotic edema82966003
- HANE - Hereditary angioneurotic oedema82966003
- Hereditary Quincke's edema82966003
- Hereditary Quincke's oedema82966003
- Hereditary angio-oedema82966003
- Hereditary angioedema82966003
- Hereditary angioneurotic edema82966003
- Hereditary angioneurotic oedema82966003
- 18-p syndrome with associated immunodeficiency234640004
- Immunodeficiency associated with 18p syndrome234640004
- Hereditary angio-oedema with normal C1 esterase inhibitor activity427167008
- Hereditary angioedema - type 3427167008
- Hereditary angioedema with normal C1 esterase inhibitor activity427167008
- Hereditary angioneurotic edema with normal C1 esterase inhibitor activity427167008
- Hereditary angioneurotic oedema with normal C1 esterase inhibitor activity427167008
- Primary immunodeficiency syndrome due to p14 deficiency718717004
- Primary immunodeficiency syndrome with short stature718717004
- Woods Black Norbury syndrome719827008
- X-linked immunoneurologic disorder719827008
UMLS
Clinical Terms
- Hereditary angioedema with normal C1 esterase inhibitor activity
- Hereditary angioneurotic edema
- Hereditary angioneurotic oedema with normal C1 esterase inhibitor activity
- HAE - Hereditary angioedema
- Hereditary angioneurotic edema with normal C1 esterase inhibitor activity
- Hereditary Quincke's edema
- Hereditary angio-oedema with normal C1 esterase inhibitor activity
- 18-p syndrome with associated immunodeficiency
- Hereditary angioedema - type 3
- Hereditary angioneurotic oedema
- HANE - Hereditary angioneurotic edema
- HAE - Hereditary angio-oedema
- Primary immunodeficiency syndrome due to p14 deficiency
- Hereditary angio-oedema
- Woods Black Norbury syndrome
- X-linked immunoneurologic disorder
- HANE - Hereditary angioneurotic oedema
- Primary immunodeficiency syndrome with short stature
- Hereditary Quincke's oedema
- Immunodeficiency associated with 18p syndrome
- Hereditary angioedema
Frequently Asked Questions
What is the ICD-10 code for immunodeficiency associated with oth major defects?
The ICD-10-CM code for immunodeficiency associated with oth major defects is D82.8. The full clinical description is "Immunodeficiency associated with other specified major defects". D82.8 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D82.8 mean?
ICD-10-CM code D82.8 represents “Immunodeficiency associated with other specified major defects”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D82.8 a billable code?
Yes, D82.8 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D82.8 in?
D82.8 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D82.8?
D82.8 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D82.8 map to?
D82.8 maps to 5 SNOMED CT concepts: 234640004, 82966003, 427167008, 718717004, 719827008. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D82.8?
D82.8 is linked to 1 UMLS Concept Unique Identifier: C0477325. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D82.8 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like immunodeficiency associated with oth major defects affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D82.8?
D82.8 maps to the ICD-11 code: 4A0Z (Primary immunodeficiencies, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.