D82.4
BillableHyperimmunoglobulin E [IgE] syndrome
Hyperimmunoglobulin E [IgE] syndrome
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(6)
D82.0Wiskott-Aldrich syndrome
D82.1Di George's syndrome
D82.2Immunodeficiency with short-limbed stature
D82.3Immunodef fol heredit defctv response to Epstein-Barr virus
D82.8Immunodeficiency associated with oth major defects
D82.9Immunodeficiency associated with major defect, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(35)
SNOMED CT
- HIES - hyperimmunoglobulin E syndrome191009009
- Hyper-IgE syndrome191009009
- Hyperimmunoglobulin E syndrome191009009
- CADINS disease1336113009
- CARD11-associated atopy with dominant interference of NF-kB signaling syndrome1336113009
- Caspase recruitment domain family member 11-associated atopy with dominant interference of nuclear factor kappa-B signaling syndrome1336113009
- AR-HIES (autosomal recessive hyperimmunoglobulin E syndrome) due to ZNF341 deficiency1342372000
- Autosomal recessive hyper-IgE syndrome due to ZNF341 deficiency1342372000
- Autosomal recessive hyperimmunoglobulin E syndrome due to zinc finger protein 341 deficiency1342372000
- Autosomal dominant hyper-IgE syndrome due to STAT3 deficiency1351326006
- Autosomal dominant hyperimmunoglobulin E syndrome due to signal transducer and activator of transcription 3 protein deficiency1351326006
- Buckley syndrome1351326006
- Job syndrome1351326006
UMLS
Clinical Terms
- CARD11-associated atopy with dominant interference of NF-kB signaling syndrome
- Autosomal dominant hyper-IgE syndrome due to STAT3 deficiency
- HIES - hyperimmunoglobulin E syndrome
- Hyperimmunoglobulin E syndrome (disorder)
- Autosomal dominant hyperimmunoglobulin E syndrome due to signal transducer and activator of transcription 3 protein deficiency
- Hyperimmunoglobulin E syndrome
- Autosomal recessive hyper-IgE syndrome due to ZNF341 deficiency
- Hyper IgE syndrome
- Buckley syndrome
- Autosomal recessive hyperimmunoglobulin E syndrome due to zinc finger protein 341 deficiency
- CADINS disease
- Caspase recruitment domain family member 11-associated atopy with dominant interference of nuclear factor kappa-B signaling syndrome
- AR-HIES (autosomal recessive hyperimmunoglobulin E syndrome) due to ZNF341 deficiency
- Hyper-IgE syndrome
- Job syndrome
Frequently Asked Questions
What is the ICD-10 code for hyperimmunoglobulin e [ige] syndrome?
The ICD-10-CM code for hyperimmunoglobulin e [ige] syndrome is D82.4. The full clinical description is "Hyperimmunoglobulin E [IgE] syndrome". D82.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D82.4 mean?
ICD-10-CM code D82.4 represents “Hyperimmunoglobulin E [IgE] syndrome”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D82.4 a billable code?
Yes, D82.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D82.4 in?
D82.4 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D82.4?
D82.4 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D82.4 map to?
D82.4 maps to 4 SNOMED CT concepts: 1342372000, 1351326006, 1336113009, 191009009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D82.4?
D82.4 is linked to 1 UMLS Concept Unique Identifier: C3887645. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D82.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hyperimmunoglobulin e [ige] syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D82.4?
D82.4 maps to the ICD-11 code: 4A01.34 (Hyperimmunoglobulin E syndromes).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.