AutoICD API

D82.3

Billable

Immunodef fol heredit defctv response to Epstein-Barr virus

Immunodeficiency following hereditary defective response to Epstein-Barr virus

Status

Billable / Specific

Block

D80-D89

Parent Code

D82

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • X-linked lymphoproliferative disease

Includes

Conditions included under this code

  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(6)
D82.0

Wiskott-Aldrich syndrome

BillableD82.1

Di George's syndrome

BillableD82.2

Immunodeficiency with short-limbed stature

BillableD82.4

Hyperimmunoglobulin E [IgE] syndrome

BillableD82.8

Immunodeficiency associated with oth major defects

BillableD82.9

Immunodeficiency associated with major defect, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

4A01.22Immune dysregulation syndromes presenting primarily with lymphoproliferationequivalentPrimary
Also Known As / Clinical Terms(132)

SNOMED CT

UMLS

Clinical Terms

  • X-linked lymphoproliferative syndrome type 2
  • X-Linked Lymphoproliferative Syndrome
  • XIAP deficiency syndrome
  • Lymphoproliferative Disorders, X-Linked
  • Lymphoproliferative Disease, X Linked
  • Immunodeficiency following hereditary defective response to Epstein-Barr virus (disorder)
  • Diseases, X-Linked Lymphoproliferative
  • Familial Fatal Epstein-Barr Infection
  • Duncan's syndrome
  • X Linked Lymphoproliferative Disorder
  • X-Linked Lymphoproliferative Diseases
  • XLPS - X-linked lymphoproliferative syndrome
  • Lymphoproliferative Disease, X-Linked
  • Lymphoproliferative Syndrome, X-Linked
  • Familial Fatal Epstein Barr Infection
  • Lymphoproliferative Syndrome, X-Linked, 1
  • Purtilo Syndrome
  • XLP
  • Disorders, X-Linked Lymphoproliferative
  • Epstein Barr Virus Infection, Familial Fatal
  • X-linked lymphoproliferative disease
  • Severe susceptibility to Epstein-Barr infection
  • X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia
  • duncan syndrome
  • Immunodeficiency, X Linked Progressive Combined Variable
  • Severe susceptibility to infectious mononucleosis
  • Syndromes, Purtilo
  • X Linked Lymphoproliferative Disease
  • X-linked lymphoproliferative syndrome (disorder)
  • X-Linked Lymphoproliferative Syndromes
  • Disease, Duncan
  • Epstein Barr Virus Induced Lymphoproliferative Disease In Males
  • SH2D1A/SLAM-associated protein deficiency
  • Syndromes, X-Linked Lymphoproliferative
  • Epstein-Barr Virus-Induced Lymphoproliferative Disease In Males
  • X-linked lymphoproliferative disease due to SH2D1A deficiency
  • X-Linked Lymphoproliferative Disorders
  • duncans syndrome
  • Lymphoproliferative Syndromes, X-Linked
  • Immunodeficiency 5s
  • Disorder, X-Linked Lymphoproliferative
  • X-linked lymphoproliferative disease due to XIAP deficiency
  • Immunodeficiency 5
  • Immunodeficiency, X-Linked Progressive Combined Variable
  • X LINKED LYMPHOPROLIFERATIVE DIS
  • X Linked Lymphoproliferative Syndrome
  • Purtilo Syndromes
  • Duncan Disease
  • Disease, X-Linked Lymphoproliferative
  • X-linked lymphoproliferative syndrome type 1
  • X-Linked Lymphoproliferative Disorder
  • Syndrome, Purtilo
  • Severe susceptibility to EBV infection
  • Epstein-Barr Virus Infection, Familial Fatal
  • Syndrome, X-Linked Lymphoproliferative
  • Lymphoproliferative Diseases, X-Linked
  • Lymphoproliferative Disorder, X-Linked
Frequently Asked Questions
What is the ICD-10 code for immunodef fol heredit defctv response to epstein-barr virus?

The ICD-10-CM code for immunodef fol heredit defctv response to epstein-barr virus is D82.3. The full clinical description is "Immunodeficiency following hereditary defective response to Epstein-Barr virus". D82.3 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D82.3 mean?

ICD-10-CM code D82.3 represents “Immunodeficiency following hereditary defective response to Epstein-Barr virus”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D82.3 a billable code?

Yes, D82.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D82.3 in?

D82.3 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D82.3?

D82.3 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.

What SNOMED CT codes does D82.3 map to?

D82.3 maps to 5 SNOMED CT concepts: 77121009, 191008001, 1162828001, 711481001, 1162830004. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D82.3?

D82.3 is linked to 2 UMLS Concept Unique Identifiers: C0549463, C0451697. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D82.3 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like immunodef fol heredit defctv response to epstein-barr virus affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D82.3?

D82.3 maps to the ICD-11 code: 4A01.22 (Immune dysregulation syndromes presenting primarily with lymphoproliferation).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.