AutoICD API

E78.6

Billable

Lipoprotein deficiency

Lipoprotein deficiency

Status

Billable / Specific

Block

E70-E88

Parent Code

E78

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Abetalipoproteinemia
  • Depressed HDL cholesterol
  • High-density lipoprotein deficiency
  • Hypoalphalipoproteinemia
  • Hypobetalipoproteinemia (familial)
  • Lecithin cholesterol acyltransferase deficiency
  • Tangier disease

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(9)
E78.0

Pure hypercholesterolemia

E78.1

Pure hyperglyceridemia

BillableE78.2

Mixed hyperlipidemia

BillableE78.3

Hyperchylomicronemia

BillableE78.4

Other hyperlipidemia

E78.5

Hyperlipidemia, unspecified

BillableE78.7

Disorders of bile acid and cholesterol metabolism

E78.8

Other disorders of lipoprotein metabolism

E78.9

Disorder of lipoprotein metabolism, unspecified

Billable

Related Conditions

Hyperlipidemia
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

5C81.ZHypolipoproteinaemia, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(396)

SNOMED CT

UMLS

Clinical Terms

  • Acanthocytoses
  • bassen-kornzweig disease
  • Apolipoprotein B deficiency
  • BASSEN-KORNZWEIG SYNDROME
  • Familial HDL deficiency
  • High-Density Lipoprotein Deficiency, Type I
  • Complete LCAT (lecithin-cholesterol acyltransferase) deficiency
  • ABL - Abetalipoproteinemia
  • LCAT DEFICIENCY
  • diseases tangiers
  • Homozygous familial hypobetalipoproteinaemia
  • Microsomal Triglyceride Transfer Protein Deficiency
  • Acyltransferase Deficiency, Lecithin:Cholesterol
  • HIGH DENSITY LIPOPROTEIN DEFICIENCY, TYPE 1
  • Hypobetalipoproteinemia
  • Hypobetalipoproteinemia (familial)
  • Cholesterol Thesaurismoses
  • Deficiency, LCAT
  • microsomal triglyceride transfer protein deficiency disease
  • Ataxia co-occurrent and due to abetalipoproteinaemia
  • ANALPHALIPOPROTEINEMIA
  • Hypocholesterolaemia
  • norum disease
  • Decreased lipoprotein
  • Familial hypobetalipoproteinemia
  • Alpha-lecithin:cholesterol acyltransferase deficiency
  • Autonomic neuropathy due to Tangier disease
  • alpha-LCAT Deficiency
  • Familial hypoalphalipoproteinaemia
  • ABL - Abetalipoproteinaemia
  • Lecithin:Cholesterol Acyltransferase Deficiency
  • Hypocholesteremia
  • Ophthalmoplegia due to abetalipoproteinaemia
  • alpha lipoprotein deficiency
  • Ataxia with abetalipoproteinaemia
  • Deficiency, alpha-LCAT
  • BASSEN KORNZWEIG DIS
  • lecithin acyltransferase deficiency
  • alpha-Lecithin-Cholesterol Acyltransferase Deficiency
  • HIGH DENSITY LIPOPROTEIN DEFICIENCY, TANGIER TYPE
  • Lecithin Cholesterol Acyltransferase Deficiency
  • Tangier disease (disorder)
  • Tangier Disease
  • Complete LCAT deficiency
  • Homozygous familial hypobetalipoproteinemia
  • Hypolipoproteinemia
  • LECITHIN CHOLESTEROL ACYLTRANSFERASE DEFIC
  • Analphaliproteinemia
  • Familial hypolipoproteinemia
  • Hypoalphalipoproteinaemia
  • Lecithin-cholesterol acyltransferase deficiency
  • Hypocholesteraemia
  • Alpha High Density Lipoprotein Deficiency Disease
  • High density lipoprotein deficiency (disorder)
  • X-linked McLeod syndrome
  • Analphalipoproteinaemia
  • deficiency lipoprotein
  • Deficiency Disease, Betalipoprotein
  • Alphalipoproteinaemia neuropathy
  • High Density Lipoprotein Deficiency, Type I
  • Familial hypobetalipoproteinaemia
  • Inborn error of lipoprotein metabolism
  • Familial hypobetalipoproteinemia (disorder)
  • Thesaurismosis, Cholesterol
  • Familial lecithin cholesterol acyltransferase deficiency
  • MICROSOMAL TRIGLYCERIDE TRANSFER PROTEIN DEFIC
  • ACANTHOCYTOSIS
  • High density lipoprotein below reference range
  • HDL Cholesterol, Low Serum
  • TGD
  • Hypoalphalipoproteinemias
  • Lipoproteinemia, Hypo alpha
  • Familial hypoalphalipoproteinemia
  • Analphalipoproteinemias
  • Partial LCAT deficiency
  • Apo A-I variant fisheye-like syndrome
  • Ataxia with abetalipoproteinemia
  • Thesaurismoses, Cholesterol
  • ApoA-I Munster variant 3
  • Fish-eye disease
  • ABETALIPOPROTEINEMIA
  • Hypoalphalipoproteinemia (disorder)
  • Hereditary acanthocytosis
  • Lipoproteinemias, Hypo alpha
  • Apolipoprotein A-I variant disorder
  • LCATA deficiency
  • Norum's disease
  • Familial hypobetalipoproteinaemia - heterozygous form
  • ABL
  • Hypolipoproteinemia (disorder)
  • Ataxia co-occurrent and due to abetalipoproteinemia
  • Disease, Betalipoprotein Deficiency
  • Betalipoprotein Deficiency Disease
  • Hypolipoproteinaemia
  • familial cholesteryl ester deficiency
  • Hypolipoproteinemias
  • Partial LCAT (lecithin-cholesterol acyltransferase) deficiency
  • Apo A-I Milano variant
  • Chorea acanthocytosis syndrome
  • Low density lipoprotein cholesterol below reference range
  • Bassen Kornzweig Syndrome
  • High-Density Lipoprotein Deficiency, Tangier Type
  • disease tangiers
  • Lack of fat in blood
  • Congenital betalipoprotein deficiency syndrome
  • TANGIER DIS
  • Familial lecithin cholesterol acyltransferase deficiency (disorder)
  • Depressed HDL cholesterol
  • Cholesterol Thesaurismosis
  • Familial lecithin-cholesterol acyltransferase deficiency
  • MTP DEFICIENCY
  • Hypo-beta-lipoproteinaemia
  • Hypo-beta-lipoproteinemia
  • Hypobetalipoproteinemias
  • Familial hypobetalipoproteinemia - homozygous form
  • McLeod neuroacanthocytosis syndrome
  • Lipoprotein deficiency disorder (disorder)
  • Familial hypolipoproteinaemia
  • Lipoprotein deficiency disorder
  • Betalipoprotein Deficiency Diseases
  • LCATA Deficiencies
  • High density lipoprotein deficiency
  • ApoA-I Munster variant 2
  • Ophthalmoplegia due to abetalipoproteinemia
  • alpha LCAT Deficiency
  • alpha Lipoproteinemia, Hypo
  • LCAT DEFIC
  • Diseases, Betalipoprotein Deficiency
  • Abetalipoproteinemia (disorder)
  • Hypoalphalipoproteinemia
  • Familial LCAT deficiency
  • Defective adenosine triphosphate-binding cassette transporter A1
  • FED - Fish-eye disease
  • Deficiency Diseases, Betalipoprotein
  • FLD
  • Hypo alpha Lipoproteinemia
  • Bassen Kornzweig Disease
  • LCAT (lecithin-cholesterol acyltransferase) deficiency
  • Hypo beta Lipoproteinemias
  • FHBL
  • Familial hypobetalipoproteinaemia - homozygous form
  • MICROSOMAL TRIGLYCERIDE TRANSFER PROTEIN DEFIC DIS
  • Familial high density lipoprotein deficiency
  • Abetalipoproteinaemia
  • Hypo alpha Lipoproteinemias
  • Hypo beta Lipoproteinemia
  • High-density lipoprotein deficiency
  • HYPOBETALIPOPROTEINEMIA, FAMILIAL
  • Familial hypobetalipoproteinemia - heterozygous form
  • Analphaliproteinaemia
  • Alphalipoproteinemia neuropathy
  • ALPHA LECITHIN CHOLESTEROL ACYLTRANSFERASE DEFIC
  • Apo A-I Giessen variant
  • Apo A-I Marburg variant
  • Apolipoprotein A-I deficiency
  • ApoA-I Munster variant 1
  • ALPHA LCAT DEFIC
  • Spiny prickle cells present
  • HDLDT1
  • Hypocholesterolemia
  • Familial lipoprotein deficiency
  • Lipoprotein below reference range
Frequently Asked Questions
What is the ICD-10 code for lipoprotein deficiency?

The ICD-10-CM code for lipoprotein deficiency is E78.6. The full clinical description is "Lipoprotein deficiency". E78.6 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E78.6 mean?

ICD-10-CM code E78.6 represents “Lipoprotein deficiency”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E78.6 a billable code?

Yes, E78.6 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E78.6 in?

E78.6 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E78.6?

E78.6 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.

What SNOMED CT codes does E78.6 map to?

E78.6 maps to 37 SNOMED CT concepts: 190787008, 250249008, 15346004, 238102008, 238098000, and 32 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E78.6?

E78.6 is linked to 8 UMLS Concept Unique Identifiers: C0000744, C0023195, C0039292, C2874290, C1862596, and 3 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E78.6 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like lipoprotein deficiency affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E78.6?

E78.6 maps to the ICD-11 code: 5C81.Z (Hypolipoproteinaemia, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.