E78.2
BillableMixed hyperlipidemia
Mixed hyperlipidemia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Broad- or floating-betalipoproteinemia
- Combined hyperlipidemia NOS
- Elevated cholesterol with elevated triglycerides NEC
- Fredrickson's hyperlipoproteinemia, type IIb or III
- Hyperbetalipoproteinemia with prebetalipoproteinemia
- Hypercholesteremia with endogenous hyperglyceridemia
- Hyperlipidemia, group C
- Tubo-eruptive xanthoma
- Xanthoma tuberosum
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •sphingolipidosisE75.0-E75.3
- •cerebrotendinous cholesterosis [van Bogaert-Scherer- Epstein]E75.5
- •familial combined hyperlipidemiaE78.49
Related Codes(9)
E78.0Pure hypercholesterolemia
E78.1Pure hyperglyceridemia
E78.3Hyperchylomicronemia
E78.4Other hyperlipidemia
E78.5Hyperlipidemia, unspecified
E78.6Lipoprotein deficiency
E78.7Disorders of bile acid and cholesterol metabolism
E78.8Other disorders of lipoprotein metabolism
E78.9Disorder of lipoprotein metabolism, unspecified
Related Conditions
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(272)
SNOMED CT
- Hyperlipoproteinaemia3744001
- Hyperlipoproteinemia3744001
- Xanthoma63103006
- Xanthomatosis63103006
- Endogenous hyperlipaemia129589009
- Endogenous hyperlipemia129589009
- Endogenous hyperlipidaemia129589009
- Endogenous hyperlipidemia129589009
- Mixed hypercholesterolaemia and hypertriglyceridaemia129591001
- Mixed hypercholesterolemia and hypertriglyceridemia129591001
- Diabetic xanthoma217341008
- Xanthoma diabeticorum217341008
- Xanthomatosis, familial238074007
- Primary combined hyperlipidaemia238088006
- Primary combined hyperlipidemia238088006
- Primary mixed hyperlipidaemia238088006
- Primary mixed hyperlipidemia238088006
- Secondary combined hyperlipidaemia238089003
- Secondary combined hyperlipidemia238089003
- Secondary mixed hyperlipidaemia238089003
- Secondary mixed hyperlipidemia238089003
- Eruptive xanthoma238952003
- Plane xanthoma238953008
- Tuberous xanthoma238954002
- Xanthoma tuberosum238954002
- Generalised plane xanthoma238955001
- Generalized plane xanthoma238955001
- Mixed hyperlipidaemia267434003
- Mixed hyperlipidemia267434003
- Multiple-type hyperlipidaemia267434003
- Multiple-type hyperlipidemia267434003
- Apolipoprotein E deficiency398796005
- Broad beta disease398796005
- Carbohydrate induced hyperlipaemia398796005
- Carbohydrate induced hyperlipemia398796005
- Dysbetalipoproteinaemia398796005
- Dysbetalipoproteinemia398796005
- Familial dysbetalipoproteinaemia398796005
- Familial hyperbetalipoproteinaemia and hyperprebetalipoproteinaemia398796005
- Familial hyperbetalipoproteinemia and hyperprebetalipoproteinemia398796005
- Familial hypercholesterolaemia with hyperlipaemia398796005
- Familial hypercholesterolemia with hyperlipemia398796005
- Familial type 3 hyperlipoproteinaemia398796005
- Familial type 3 hyperlipoproteinemia398796005
- Familial type III hyperlipoproteinaemia398796005
- Floating beta disease398796005
- Fredrickson type III hyperlipoproteinaemia398796005
- Fredrickson type III hyperlipoproteinemia398796005
- Primary dysbetalipoproteinaemia398796005
- Primary dysbetalipoproteinemia398796005
- Remnant hyperlipidaemia398796005
- Remnant hyperlipidemia398796005
- Remnant hyperlipoproteinaemia398796005
- Remnant hyperlipoproteinemia398796005
- Diffuse xanthoma399970005
- Disseminated xanthosiderohistiocytosis399970005
- Xanthoma disseminatum399970005
- Tubero-eruptive xanthoma402471004
- Cutaneous xanthoma402472006
- Primary polygenic type IIb combined hyperlipidaemia402474007
- Primary polygenic type IIb combined hyperlipidemia402474007
- Xanthoma due to lymphedema402476009
- Xanthoma due to lymphoedema402476009
- Secondary xanthomatous infiltration of the skin402478005
- Xanthoma due to abnormality of lipid metabolism402724009
- Primary genetic hyperlipidaemia402785008
- Primary genetic hyperlipidemia402785008
- Primary genetic mixed hyperlipidaemia402787000
- Primary genetic mixed hyperlipidemia402787000
- Atypical xanthoma disseminatum404163009
- Diffuse normolipemic plane xanthomatosis404163009
- Diffuse plane xanthomatosis404163009
- Diffuse plane xanthoma due to hyperlipidaemia1251362006
- Diffuse plane xanthoma due to hyperlipidemia1251362006
- Palmar xanthoma1254896008
- Xanthomatosis of skin of palm1254896008
- Xanthomatosis of skin of palm of hand1254896008
- Xanthoma due to primary combined hyperlipidaemia1256073006
- Xanthoma due to primary combined hyperlipidemia1256073006
- Mixed hyperlipidaemia due to type 1 diabetes mellitus1571000119104
- Mixed hyperlipidemia due to type 1 diabetes mellitus1571000119104
- Mixed hyperlipidaemia due to type 2 diabetes mellitus701000119103
- Mixed hyperlipidaemia due to type II diabetes mellitus701000119103
- Mixed hyperlipidemia due to type 2 diabetes mellitus701000119103
- Mixed hyperlipidemia due to type II diabetes mellitus701000119103
UMLS
- APOLIPOPROTEIN B-100, FAMILIAL DEFECTIVEC1704417
- APOLIPOPROTEIN B-100, FAMILIAL LIGAND-DEFECTIVEC1704417
- Apolipoprotein B 100, Familial DefectiveC1704417
- Apolipoprotein B 100, Familial Ligand DefectiveC1704417
- Apolipoprotein B-100, Familial DefectiveC1704417
- Apolipoprotein B-100, Familial Ligand-DefectiveC1704417
- Autosomal Dominant HypercholesterolemiaC1704417
- Combined Hyperlipoproteinemia, FamilialC1704417
- Combined Hyperlipoproteinemias, FamilialC1704417
- FCHL - Familial combined hyperlipidaemiaC1704417
- FCHL - Familial combined hyperlipidemiaC1704417
- FCHL2C1704417
- FDB - Familial defective apolipoprotein B-100C1704417
- FHCL2C1704417
- Familial Combined HyperlipoproteinemiaC1704417
- Familial Combined HyperlipoproteinemiasC1704417
- Familial Hypercholesterolemia 2C1704417
- Familial defective apolipoprotein B-100C1704417
- Familial defective apolipoprotein B-100 (disorder)C1704417
- Familial hyperlipoproteinaemia type IIbC1704417
- Familial hyperlipoproteinemia type IIbC1704417
- Fredrickson Type IIb hyperlipoproteinaemiaC1704417
- Fredrickson Type IIb hyperlipoproteinemiaC1704417
- Fredrickson type IIb hyperlipoproteinaemiaC1704417
- Fredrickson type IIb hyperlipoproteinemiaC1704417
- Fredrickson's hyperlipoproteinemia, type IIb or IIIC1704417
- HYPERCHOLESTEROLEMIA, AUTOSOMAL DOMINANT, TYPE BC1704417
- HYPERCHOLESTEROLEMIA, FAMILIAL, 2C1704417
- HyperapobetalipoproteinaemiaC1704417
- HyperapobetalipoproteinemiaC1704417
- Hyperbetalipoproteinemia with prebetalipoproteinemiaC1704417
- Hypercholesterolemia, Autosomal Dominant, Type BC1704417
- Hypercholesterolemia, Familial, 2C1704417
- Hyperlipoproteinemia Type IIbC1704417
- Hyperlipoproteinemia Type IIbsC1704417
- Hyperlipoproteinemia, Familial CombinedC1704417
- Hyperlipoproteinemias, Familial CombinedC1704417
- Type IIb hyperlipoproteinaemiaC1704417
- Type IIb hyperlipoproteinemiaC1704417
- Broad- or floating-betalipoproteinemiaC2047520
- Mixed hyperlipidaemiaC2047520
- Mixed hyperlipidemiaC2047520
- Mixed hyperlipidemia (disorder)C2047520
- Multiple-type hyperlipidaemiaC2047520
- Multiple-type hyperlipidemiaC2047520
- Combined hyperlipidaemiaC2712907
- Combined hyperlipidemiaC2712907
- Combined hyperlipidemia NOSC2712907
- combined hyperlipidemiaC2712907
- Elevated cholesterol with elevated triglycerides NECC2712905
- Hypercholesteremia with endogenous hyperglyceridemiaC2874289
- Hyperlipidemia, group CC1399990
- Tuberous xanthomaC0302164
- Tuberous xanthoma (disorder)C0302164
- Tubo-eruptive xanthomaC0302164
- Xanthoma tuberosumC0302164
- tuberous xanthomaC0302164
- tuberous xanthomasC0302164
- xanthoma tuberosumC0302164
Clinical Terms
- Familial type 3 hyperlipoproteinaemia
- tuberous xanthomas
- Familial hyperlipoproteinaemia type IIb
- Familial type 3 hyperlipoproteinemia
- Mixed hyperlipidaemia due to type 2 diabetes mellitus
- Hyperlipidemia, group C
- Hypercholesterolemia, Familial, 2
- Primary genetic hyperlipidemia
- Xanthomatosis of skin of palm of hand
- Type IIb hyperlipoproteinemia
- Primary mixed hyperlipidaemia
- FDB - Familial defective apolipoprotein B-100
- Fredrickson type IIb hyperlipoproteinaemia
- Hypercholesterolemia, Autosomal Dominant, Type B
- Primary polygenic type IIb combined hyperlipidemia
- Apolipoprotein E deficiency
- Fredrickson type IIb hyperlipoproteinemia
- Primary mixed hyperlipidemia
- Familial defective apolipoprotein B-100 (disorder)
- Disseminated xanthosiderohistiocytosis
- FCHL - Familial combined hyperlipidemia
- Mixed hyperlipidaemia due to type 1 diabetes mellitus
- APOLIPOPROTEIN B-100, FAMILIAL LIGAND-DEFECTIVE
- Hyperapobetalipoproteinaemia
- Autosomal Dominant Hypercholesterolemia
- Diabetic xanthoma
- Combined hyperlipidemia
- Xanthoma due to lymphedema
- Familial hyperbetalipoproteinaemia and hyperprebetalipoproteinaemia
- Mixed hyperlipidemia (disorder)
- Remnant hyperlipidemia
- Secondary mixed hyperlipidaemia
- Diffuse plane xanthoma due to hyperlipidaemia
- APOLIPOPROTEIN B-100, FAMILIAL DEFECTIVE
- Xanthoma due to abnormality of lipid metabolism
- Endogenous hyperlipidaemia
- Familial type III hyperlipoproteinaemia
- Hyperlipoproteinaemia
- tuberous xanthoma
- Broad beta disease
- Endogenous hyperlipidemia
- Generalized plane xanthoma
- Diffuse normolipemic plane xanthomatosis
- Mixed hypercholesterolaemia and hypertriglyceridaemia
- Hyperlipoproteinemia
- Familial hyperlipoproteinemia type IIb
- Diffuse xanthoma
- Fredrickson type III hyperlipoproteinemia
- Tubero-eruptive xanthoma
- Xanthoma
- Diffuse plane xanthoma due to hyperlipidemia
- Carbohydrate induced hyperlipemia
- Primary combined hyperlipidaemia
- Primary genetic mixed hyperlipidemia
- Xanthomatosis of skin of palm
- Familial Combined Hyperlipoproteinemias
- Mixed hyperlipidaemia
- Remnant hyperlipidaemia
- Mixed hyperlipidaemia due to type II diabetes mellitus
- Xanthomatosis, familial
- Familial defective apolipoprotein B-100
- Remnant hyperlipoproteinaemia
- Type IIb hyperlipoproteinaemia
- Xanthoma disseminatum
- Secondary xanthomatous infiltration of the skin
- Elevated cholesterol with elevated triglycerides NEC
- Hypercholesteremia with endogenous hyperglyceridemia
- Carbohydrate induced hyperlipaemia
- Fredrickson type III hyperlipoproteinaemia
- Mixed hyperlipidemia due to type 2 diabetes mellitus
- Hyperlipoproteinemias, Familial Combined
- Diffuse plane xanthomatosis
- Familial dysbetalipoproteinaemia
- FCHL - Familial combined hyperlipidaemia
- Secondary combined hyperlipidaemia
- Xanthoma diabeticorum
- Mixed hyperlipidemia due to type II diabetes mellitus
- Secondary mixed hyperlipidemia
- Primary dysbetalipoproteinemia
- Primary polygenic type IIb combined hyperlipidaemia
- Combined hyperlipidemia NOS
- Eruptive xanthoma
- Familial hyperbetalipoproteinemia and hyperprebetalipoproteinemia
- Xanthoma due to primary combined hyperlipidemia
- Atypical xanthoma disseminatum
- Primary genetic mixed hyperlipidaemia
- Primary combined hyperlipidemia
- Xanthoma due to lymphoedema
- Primary genetic hyperlipidaemia
- Combined hyperlipidaemia
- Primary dysbetalipoproteinaemia
- Apolipoprotein B 100, Familial Ligand Defective
- FHCL2
- Endogenous hyperlipemia
- Tuberous xanthoma (disorder)
- Hyperlipoproteinemia Type IIb
- Generalised plane xanthoma
- Combined Hyperlipoproteinemias, Familial
- Dysbetalipoproteinemia
- xanthoma tuberosum
- Fredrickson's hyperlipoproteinemia, type IIb or III
- Hyperbetalipoproteinemia with prebetalipoproteinemia
- Remnant hyperlipoproteinemia
- Apolipoprotein B 100, Familial Defective
- Tubo-eruptive xanthoma
- Plane xanthoma
- Cutaneous xanthoma
- Familial hypercholesterolaemia with hyperlipaemia
- Familial hypercholesterolemia with hyperlipemia
- Hyperlipoproteinemia, Familial Combined
- Combined Hyperlipoproteinemia, Familial
- Floating beta disease
- Secondary combined hyperlipidemia
- Mixed hyperlipidemia due to type 1 diabetes mellitus
- Endogenous hyperlipaemia
- Xanthoma due to primary combined hyperlipidaemia
- FCHL2
- Xanthomatosis
- Hyperlipoproteinemia Type IIbs
- Multiple-type hyperlipidemia
- Mixed hypercholesterolemia and hypertriglyceridemia
- Familial Hypercholesterolemia 2
- Broad- or floating-betalipoproteinemia
- Familial Combined Hyperlipoproteinemia
- Multiple-type hyperlipidaemia
- Palmar xanthoma
- Hyperapobetalipoproteinemia
- Dysbetalipoproteinaemia
Frequently Asked Questions
What is the ICD-10 code for mixed hyperlipidemia?
The ICD-10-CM code for mixed hyperlipidemia is E78.2. The full clinical description is "Mixed hyperlipidemia". E78.2 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E78.2 mean?
ICD-10-CM code E78.2 represents “Mixed hyperlipidemia”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E78.2 a billable code?
Yes, E78.2 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E78.2 in?
E78.2 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E78.2?
E78.2 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E78.2 map to?
E78.2 maps to 29 SNOMED CT concepts: 398796005, 404163009, 402472006, 217341008, 1251362006, and 24 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E78.2?
E78.2 is linked to 7 UMLS Concept Unique Identifiers: C1704417, C2047520, C2712907, C2712905, C2874289, and 2 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E78.2 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like mixed hyperlipidemia affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E78.2?
E78.2 maps to the ICD-11 code: 5C80.2 (Mixed hyperlipidaemia).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.