AutoICD API

E78.1

Billable

Pure hyperglyceridemia

Pure hyperglyceridemia

Status

Billable / Specific

Block

E70-E88

Parent Code

E78

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Elevated fasting triglycerides
  • Endogenous hyperglyceridemia
  • Fredrickson's hyperlipoproteinemia, type IV
  • Hyperlipidemia, group B
  • Hyperprebetalipoproteinemia
  • Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(9)
E78.0

Pure hypercholesterolemia

E78.2

Mixed hyperlipidemia

BillableE78.3

Hyperchylomicronemia

BillableE78.4

Other hyperlipidemia

E78.5

Hyperlipidemia, unspecified

BillableE78.6

Lipoprotein deficiency

BillableE78.7

Disorders of bile acid and cholesterol metabolism

E78.8

Other disorders of lipoprotein metabolism

E78.9

Disorder of lipoprotein metabolism, unspecified

Billable

Related Conditions

Hyperlipidemia
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

5C80.1HypertriglyceridaemiaequivalentPrimary
Also Known As / Clinical Terms(166)

SNOMED CT

UMLS

Clinical Terms

  • Hyperlipoproteinemia Type IV
  • HYPERLIPOPROTEINEMIA, TYPE IV
  • Fredrickson Type IV Lipidemia
  • familial hyperlipoproteinemia type IV
  • Primary genetic hyperlipidemia
  • Elevated fasting triglycerides
  • Sporadic primary hypertriglyceridaemia
  • Type IV hyperlipidemia
  • Hyperlipemias, Carbohydrate-Inducible
  • Hyperlipidemia, group B
  • Hypertriglyceridaemia
  • Very low density lipoprotinaemia
  • Secondary hypertriglyceridemia
  • hyperlipidemia type iv
  • Hypertriglyceridemia
  • Fredrickson's hyperlipoproteinemia, type IV
  • Type IV Hyperlipoproteinemia
  • Hypertriglyceridemia, Familial
  • familial hyperprebetalipoproteinemia
  • Familial Type IV Hyperlipoproteinemia
  • Inducible Hyperlipemia, Carbohydrate
  • Hyperlipoproteinemias, Type IV
  • Familial hypertriglyceridemia
  • Xanthoma due to abnormality of lipid metabolism
  • Fredrickson type IV lipidaemia
  • Endogenous hyperlipidaemia
  • Hyperlipoproteinaemia
  • Endogenous hyperlipidemia
  • Xanthoma due to primary hypertriglyceridemia
  • Type IV lipidaemia
  • Transient infantile hypertriglyceridaemia and hepatosteatosis
  • Hyperlipoproteinemia
  • Primary hypertriglyceridemia
  • Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
  • Endogenous hyperglyceridemia
  • Hyper prebeta lipoproteinemia
  • Type IV Hyperlipoproteinemias
  • Carbohydrate Inducible Hyperlipemias
  • Type IV hyperlipoproteinaemia
  • Transient infantile hypertriglyceridaemia and fatty liver
  • Inducible Hyperlipemias, Carbohydrate
  • Sporadic primary hypertriglyceridemia
  • Carbohydrate-Inducible Hyperlipemia
  • Familial Hyperlipoproteinemia Type 4
  • Transient infantile hypertriglyceridemia and hepatosteatosis
  • Primary genetic hyperlipidaemia
  • Hyperlipemia, Carbohydrate-Inducible
  • Type IV, Hyperlipoproteinemia
  • Endogenous hyperlipemia
  • Pure hyperglyceridaemia
  • Transient infantile hypertriglyceridemia and fatty liver
  • Familial hypertriglyceridemia (disorder)
  • Very low density lipoprotinemia
  • Carbohydrate Inducible Hyperlipemia
  • Familial hypertriglyceridaemia
  • Primary hypertriglyceridaemia
  • Endogenous hyperlipidemia (disorder)
  • Pure hyperglyceridemia (disorder)
  • Fredrickson type IV hyperlipoproteinaemia
  • Hyperlipemias, Carbohydrate Inducible
  • Carbohydrate-Inducible Hyperlipemias
  • Endogenous hyperlipaemia
  • Type IV lipidemia
  • Xanthoma due to primary hypertriglyceridaemia
  • Secondary hypertriglyceridaemia
  • Fredrickson type IV hyperlipoproteinemia
  • Type IV hyperlipidaemia
  • Hyperprebetalipoproteinemia
  • Hyperlipemia, Carbohydrate Inducible
  • Fredrickson type IV hyperlipoproteinemia (disorder)
Frequently Asked Questions
What is the ICD-10 code for pure hyperglyceridemia?

The ICD-10-CM code for pure hyperglyceridemia is E78.1. The full clinical description is "Pure hyperglyceridemia". E78.1 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E78.1 mean?

ICD-10-CM code E78.1 represents “Pure hyperglyceridemia”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E78.1 a billable code?

Yes, E78.1 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E78.1 in?

E78.1 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E78.1?

E78.1 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 4 more.

What SNOMED CT codes does E78.1 map to?

E78.1 maps to 14 SNOMED CT concepts: 129589009, 34528009, 238085009, 3744001, 302870006, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E78.1?

E78.1 is linked to 2 UMLS Concept Unique Identifiers: C0020480, C2874288. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E78.1 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like pure hyperglyceridemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E78.1?

E78.1 maps to the ICD-11 code: 5C80.1 (Hypertriglyceridaemia).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.