AutoICD API

D76.3

Billable

Other histiocytosis syndromes

Other histiocytosis syndromes

Status

Billable / Specific

Block

D70-D77

Parent Code

D76

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Reticulohistiocytoma (giant-cell)
  • Sinus histiocytosis with massive lymphadenopathy
  • Xanthogranuloma

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
D76.1

Hemophagocytic lymphohistiocytosis

BillableD76.2

Hemophagocytic syndrome, infection-associated

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

3C0ZDiseases of the blood or blood-forming organs, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(166)

SNOMED CT

UMLS

Clinical Terms

  • rosai dorfman disease
  • Syndrome, Destombes-Rosai-Dorfman
  • Polyostotic sclerosing histiocytosis
  • Retroperitoneal xanthogranuloma
  • Sinus Histiocytoses
  • SHML
  • JXG - Juvenile xanthogranuloma
  • Destombes-Rosai-Dorfman Disease
  • Juvenile xanthogranuloma
  • Reactive Xanthogranuloma
  • SLC29A3 spectrum disorder
  • Xanthoma multiplex
  • Sinus Histiocytosis with Massive Lymphadenopathy
  • Rosai-Dorfman-Destombes disease
  • Histiocytosis class IIa
  • Chronic histiocytosis
  • Histiocytoses, Sinus
  • Solitary eruptive xanthogranuloma
  • Multiple eruptive juvenile xanthogranuloma
  • Papular histiocytosis of head
  • Rosai-Dorfman syndrome
  • Erdheim-Chester disease
  • Histiocytic syndrome
  • Rosai-Dorfman disease
  • Non-Langerhans cell histiocytic dermatosis
  • Giant cell histiocytoma
  • Hereditary progressive mucinous histiocytosis
  • Histiocytosis-lymphadenopathy plus syndrome
  • Sea-blue histiocyte syndrome
  • Solitary reticulohistiocytoma
  • Xanthogranuloma (disorder)
  • Panniculitis secondary to histiocytic disorder
  • RDD
  • histiocytosis sinus
  • Undetermined cell histiocytosis
  • Nevoxanthoendothelioma
  • Subcutaneous xanthogranulomatosis
  • Naevoxanthoendothelioma
  • Histiocytosis, Sinus
  • Erdheim-Chester syndrome
  • Multiple eruptive xanthoma in infancy
  • Necrobiotic xanthogranuloma with paraproteinemia
  • Destombes Rosai Dorfman Syndrome
  • ROSAI DORFMAN DIS
  • Xanthogranuloma (morphologic abnormality)
  • Destombes-Rosai-Dorfman Syndrome
  • Progressive nodular histiocytosis
  • Xanthogranuloma
  • Rosai-Dorfman disease (disorder)
  • Necrobiotic xanthogranuloma
  • Necrobiotic xanthogranuloma with paraproteinaemia
  • H syndrome
  • Mucinous histiocytosis of the colon
  • Disease, Rosai-Dorfman
  • Congenital xanthoma tuberosum
  • sinus histiocytosis
  • disease rosai-dorfman
  • SEX - Solitary eruptive xanthogranuloma
  • Xanthoma naeviforme
  • Juvenile xanthoma
  • Malakoplakia (involving skin)
  • Reticulohistiocytic granuloma
  • Periodontitis due to histiocytosis syndrome
  • Xanthogranuloma of choroid plexus
  • RDD - Rosai-Dorfman disease
  • Benign cephalic histiocytosis
  • Histiocytosis
  • Juvenile giant cell granuloma
  • Sea-blue histiocytosis
  • Rosai-Dorfman disease (morphologic abnormality)
  • Reticulohistiocytoma (giant-cell)
  • Dermal dendritic cell histiocytosis
  • Malakoplakia
  • Juvenile xanthogranuloma of iris
  • Xanthoma neviforme
  • Cutaneous reticulohistiocytosis
  • Juvenile xanthogranuloma of skin
Frequently Asked Questions
What is the ICD-10 code for other histiocytosis syndromes?

The ICD-10-CM code for other histiocytosis syndromes is D76.3. The full clinical description is "Other histiocytosis syndromes". D76.3 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D76.3 mean?

ICD-10-CM code D76.3 represents “Other histiocytosis syndromes”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D76.3 a billable code?

Yes, D76.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D76.3 in?

D76.3 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D76.3?

D76.3 has Excludes1 notes indicating codes that cannot be used together with it, including: (Abt-) Letterer-Siwe disease (C96.0); eosinophilic granuloma (C96.6); Hand-Schüller-Christian disease (C96.5); and 12 more.

What SNOMED CT codes does D76.3 map to?

D76.3 maps to 30 SNOMED CT concepts: 255192005, 14931000119109, 400031009, 404161006, 733205009, and 25 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D76.3?

D76.3 is linked to 4 UMLS Concept Unique Identifiers: C5848165, C0477320, C5234857, C2873826. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D76.3 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other histiocytosis syndromes affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D76.3?

D76.3 maps to the ICD-11 code: 3C0Z (Diseases of the blood or blood-forming organs, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.