C96.0
BillableMultifocal and multisystemic Langerhans-cell histiocytosis
Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Histiocytosis X, multisystemic
- Letterer-Siwe disease
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
C96.2Malignant mast cell neoplasm
C96.4Sarcoma of dendritic cells (accessory cells)
C96.5Multifocal and unisystemic Langerhans-cell histiocytosis
C96.6Unifocal Langerhans-cell histiocytosis
C96.9Malig neoplm of lymphoid, hematpoetc and rel tissue, unsp
C96.AHistiocytic sarcoma
C96.ZOth malig neoplm of lymphoid, hematpoetc and related tissue
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(68)
SNOMED CT
- LSD - Letterer-Siwe disease118614007
- Langerhans cell histiocytosis, disseminated118614007
- Letterer Siwe disease118614007
- Disseminated Langerhans cell histiocytosis of lymph nodes of lower limb1332422001
- Disseminated Langerhans cell histiocytosis of lymph nodes of upper limb1332423006
- Disseminated Langerhans cell histiocytosis of lymph nodes of head1332425004
- Disseminated Langerhans cell histiocytosis of cervical lymph nodes1332426003
- Disseminated Langerhans cell histiocytosis of lymph nodes of neck1332426003
- Disseminated Langerhans cell histiocytosis of spleen1332427007
- Disseminated Langerhans cell histiocytosis of lymph nodes of multiple sites1332428002
- Disseminated Langerhans cell histiocytosis of lymph nodes of thorax1332429005
- Disseminated Langerhans cell histiocytosis of pelvic lymph nodes1332430000
- Disseminated Langerhans cell histiocytosis of abdominal lymph nodes1332431001
- Disseminated Langerhans cell histiocytosis of bone1332476001
- Hand Schüller Christian disease1332476001
UMLS
- Disease, Letterer-SiweC0023381
- HISTIOCYTOSIS X, ACUTE DISSEMINATEDC0023381
- L-S DISEASEC0023381
- LESDC0023381
- LETTERER SIWE DISC0023381
- LETTERER-SIWE DISEASEC0023381
- LSD - Letterer-Siwe diseaseC0023381
- Langerhans cell granulomatosisC0023381
- Langerhans cell histiocytosis, disseminatedC0023381
- Langerhans cell histiocytosis, disseminated (disorder)C0023381
- Langerhans cell histiocytosis, disseminated (morphologic abnormality)C0023381
- Langerhans cell histiocytosis, generalisedC0023381
- Langerhans cell histiocytosis, generalizedC0023381
- Letterer Siwe DiseaseC0023381
- Letterer Siwe diseaseC0023381
- Letterer-Siwe DiseaseC0023381
- Letterer-Siwe diseaseC0023381
- histiocytosis xC0023381
- letterer - siwe diseaseC0023381
- letterer siwe diseaseC0023381
- letterer-siwe diseaseC0023381
- Histiocytosis X, multisystemicC2861648
- Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosisC2861649
- Multifocal and multisystemic Langerhans-cell histiocytosisC2861649
Clinical Terms
- Disseminated Langerhans cell histiocytosis of bone
- Langerhans cell histiocytosis, disseminated (morphologic abnormality)
- Disseminated Langerhans cell histiocytosis of lymph nodes of neck
- Langerhans cell histiocytosis, disseminated
- LETTERER SIWE DIS
- Letterer Siwe Disease
- Hand Schüller Christian disease
- Disseminated Langerhans cell histiocytosis of lymph nodes of thorax
- LSD - Letterer-Siwe disease
- Histiocytosis X, multisystemic
- LETTERER-SIWE DISEASE
- Langerhans cell granulomatosis
- HISTIOCYTOSIS X, ACUTE DISSEMINATED
- Langerhans cell histiocytosis, generalized
- histiocytosis x
- Langerhans cell histiocytosis, generalised
- LESD
- Disseminated Langerhans cell histiocytosis of spleen
- letterer - siwe disease
- L-S DISEASE
- Disseminated Langerhans cell histiocytosis of lymph nodes of head
- Langerhans cell histiocytosis, disseminated (disorder)
- Disseminated Langerhans cell histiocytosis of lymph nodes of upper limb
- Disseminated Langerhans cell histiocytosis of abdominal lymph nodes
- Disseminated Langerhans cell histiocytosis of lymph nodes of multiple sites
- Disease, Letterer-Siwe
- Disseminated Langerhans cell histiocytosis of pelvic lymph nodes
- Disseminated Langerhans cell histiocytosis of lymph nodes of lower limb
- Disseminated Langerhans cell histiocytosis of cervical lymph nodes
Frequently Asked Questions
What is the ICD-10 code for multifocal and multisystemic langerhans-cell histiocytosis?
The ICD-10-CM code for multifocal and multisystemic langerhans-cell histiocytosis is C96.0. The full clinical description is "Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis". C96.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code C96.0 mean?
ICD-10-CM code C96.0 represents “Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis”. It is classified under Chapter 2: Neoplasms and is a billable/specific code that can be used on a claim.
Is C96.0 a billable code?
Yes, C96.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is C96.0 in?
C96.0 is in Chapter 2: Neoplasms (codes C00-D49).
What codes cannot be used with C96.0?
C96.0 has Excludes1 notes indicating codes that cannot be used together with it, including: personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79); adult pulmonary Langerhans cell histiocytosis (J84.82); multifocal and unisystemic Langerhans-cell histiocytosis (C96.5); and 1 more.
What SNOMED CT codes does C96.0 map to?
C96.0 maps to 11 SNOMED CT concepts: 1332431001, 1332476001, 1332426003, 1332425004, 1332422001, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for C96.0?
C96.0 is linked to 3 UMLS Concept Unique Identifiers: C0023381, C2861648, C2861649. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does C96.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like multifocal and multisystemic langerhans-cell histiocytosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of C96.0?
C96.0 maps to the ICD-11 code: 2B31.2Z (Langerhans cell histiocytosis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.